Tissue-Specific Loss of DARS2 Activates Stress Responses Independently of Respiratory Chain Deficiency in the Heart von Dogan, Sukru Anil, Pujol, Claire, Maiti, Priyanka, Kukat, Alexandra, Wang, Shuaiyu, Hermans, Steffen, Senft, Katharina, Wibom, Rolf, Rugarli, Elena I., Trifunovic, Aleksandra

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Mitochondrial quality control: a matter of life and death for neurons von Rugarli, Elena I, Langer, Thomas

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The uncorroded-part fallacy von Rugarli, Paolo

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Loss of prohibitin membrane scaffolds impairs mitochondrial architecture and leads to tau hyperphosphorylation and neurodegeneration von Merkwirth, Carsten, Martinelli, Paola, Korwitz, Anne, Morbin, Michela, Brönneke, Hella S, Jordan, Sabine D, Rugarli, Elena I, Langer, Thomas

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Spastin binds to lipid droplets and affects lipid metabolism von Papadopoulos, Chrisovalantis, Orso, Genny, Mancuso, Giuseppe, Herholz, Marija, Gumeni, Sentiljana, Tadepalle, Nimesha, Jüngst, Christian, Tzschichholz, Anne, Schauss, Astrid, Höning, Stefan, Trifunovic, Aleksandra, Daga, Andrea, Rugarli, Elena I

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DNAJC19, a Mitochondrial Cochaperone Associated with Cardiomyopathy, Forms a Complex with Prohibitins to Regulate Cardiolipin Remodeling von Richter-Dennerlein, Ricarda, Korwitz, Anne, Haag, Mathias, Tatsuta, Takashi, Dargazanli, Sascha, Baker, Michael, Decker, Thorsten, Lamkemeyer, Tobias, Rugarli, Elena I., Langer, Thomas

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Lipid Droplets in the Pathogenesis of Hereditary Spastic Paraplegia von Tadepalle, Nimesha, Rugarli, Elena I.

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Regulation of mitochondrial proteostasis by the proton gradient von Patron, Maria, Tarasenko, Daryna, Nolte, Hendrik, Kroczek, Lara, Ghosh, Mausumi, Ohba, Yohsuke, Lasarzewski, Yvonne, Ahmadi, Zeinab Alsadat, Cabrera‐Orefice, Alfredo, Eyiama, Akinori, Kellermann, Tim, Rugarli, Elena I, Brandt, Ulrich, Meinecke, Michael, Langer, Thomas

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The m-AAA Protease Associated with Neurodegeneration Limits MCU Activity in Mitochondria von König, Tim, Tröder, Simon E., Bakka, Kavya, Korwitz, Anne, Richter-Dennerlein, Ricarda, Lampe, Philipp A., Patron, Maria, Mühlmeister, Mareike, Guerrero-Castillo, Sergio, Brandt, Ulrich, Decker, Thorsten, Lauria, Ines, Paggio, Angela, Rizzuto, Rosario, Rugarli, Elena I., De Stefani, Diego, Langer, Thomas

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Astrocyte‐specific deletion of the mitochondrial m‐AAA protease reveals glial contribution to neurodegeneration von Murru, Sara, Hess, Simon, Barth, Esther, Almajan, Eva R., Schatton, Désirée, Hermans, Steffen, Brodesser, Susanne, Langer, Thomas, Kloppenburg, Peter, Rugarli, Elena I.

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The class 3 PI3K coordinates autophagy and mitochondrial lipid catabolism by controlling nuclear receptor PPARα von Iershov, Anton, Nemazanyy, Ivan, Alkhoury, Chantal, Girard, Muriel, Barth, Esther, Cagnard, Nicolas, Montagner, Alexandra, Chretien, Dominique, Rugarli, Elena I., Guillou, Herve, Pende, Mario, Panasyuk, Ganna

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Regulation of OPA1 processing and mitochondrial fusion by m-AAA protease isoenzymes and OMA1 von Ehses, Sarah, Raschke, Ines, Mancuso, Giuseppe, Bernacchia, Andrea, Geimer, Stefan, Tondera, Daniel, Martinou, Jean-Claude, Westermann, Benedikt, Rugarli, Elena I, Langer, Thomas

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CLUH granules coordinate translation of mitochondrial proteins with mTORC1 signaling and mitophagy von Pla‐Martín, David, Schatton, Désirée, Wiederstein, Janica L, Marx, Marie‐Charlotte, Khiati, Salim, Krüger, Marcus, Rugarli, Elena I

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Whole-exome sequencing identifies homozygous AFG3L2 mutations in a spastic ataxia-neuropathy syndrome linked to mitochondrial m-AAA proteases von Pierson, Tyler Mark, Adams, David, Bonn, Florian, Martinelli, Paola, Cherukuri, Praveen F, Teer, Jamie K, Hansen, Nancy F, Cruz, Pedro, Mullikin For The Nisc Comparative Sequencing Program, James C, Blakesley, Robert W, Golas, Gretchen, Kwan, Justin, Sandler, Anthony, Fuentes Fajardo, Karin, Markello, Thomas, Tifft, Cynthia, Blackstone, Craig, Rugarli, Elena I, Langer, Thomas, Gahl, William A, Toro, Camilo

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Loss of OMA1 delays neurodegeneration by preventing stress-induced OPA1 processing in mitochondria von Korwitz, Anne, Merkwirth, Carsten, Richter-Dennerlein, Ricarda, Tröder, Simon E, Sprenger, Hans-Georg, Quirós, Pedro M, López-Otín, Carlos, Rugarli, Elena I, Langer, Thomas

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CLUH regulates mitochondrial biogenesis by binding mRNAs of nuclear-encoded mitochondrial proteins von Gao, Jie, Schatton, Désirée, Martinelli, Paola, Hansen, Henriette, Pla-Martin, David, Barth, Esther, Becker, Christian, Altmueller, Janine, Frommolt, Peter, Sardiello, Marco, Rugarli, Elena I

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The m-AAA Protease Defective in Hereditary Spastic Paraplegia Controls Ribosome Assembly in Mitochondria von Nolden, Mark, Ehses, Sarah, Koppen, Mirko, Bernacchia, Andrea, Rugarli, Elena I., Langer, Thomas

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The i-AAA protease YME1L and OMA1 cleave OPA1 to balance mitochondrial fusion and fission von Anand, Ruchika, Wai, Timothy, Baker, Michael J, Kladt, Nikolay, Schauss, Astrid C, Rugarli, Elena, Langer, Thomas

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Emerging roles of mitochondrial proteases in neurodegeneration von Martinelli, Paola, Rugarli, Elena I.

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SARM1 deletion delays cerebellar but not spinal cord degeneration in an enhanced mouse model of SPG7 deficiency von Montoro-Gámez, Carolina, Nolte, Hendrik, Molinié, Thibaut, Evangelista, Giovanna, Tröder, Simon E, Barth, Esther, Popovic, Milica, Trifunovic, Aleksandra, Zevnik, Branko, Langer, Thomas, Rugarli, Elena I

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