Phase II studies of nebulised Arikace in CF patients with Pseudomonas aeruginosa infection von Clancy, J P, Dupont, L, Konstan, M W, Billings, J, Fustik, S, Goss, C H, Lymp, J, Minic, P, Quittner, A L, Rubenstein, R C, Young, K R, Saiman, L, Burns, J L, Govan, J R W, Ramsey, B, Gupta, R

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Long-term treatment with oral N-acetylcysteine: Affects lung function but not sputum inflammation in cystic fibrosis subjects. A phase II randomized placebo-controlled trial von Conrad, C, Lymp, J, Thompson, V, Dunn, C, Davies, Z, Chatfield, B, Nichols, D, Clancy, J, Vender, R, Egan, M.E, Quittell, L, Michelson, P, Antony, V, Spahr, J, Rubenstein, R.C, Moss, R.B, Herzenberg, L.A, Goss, C.H, Tirouvanziam, R

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A pilot clinical trial of oral sodium 4-phenylbutyrate (buphenyl) in ΔF508-homozygous cystic fibrosis patients: Partial restoration of nasal epithelial CFTR function von RUBENSTEIN, R. C, ZEITLIN, P. L

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Mutation in the Gene Responsible for Cystic Fibrosis and Predisposition to Chronic Rhinosinusitis in the General Population von Wang, XinJing, Moylan, Birgitta, Leopold, Donald A, Kim, Jean, Rubenstein, Ronald C, Togias, Alkis, Proud, David, Zeitlin, Pamela L, Cutting, Garry R

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In vitro pharmacologic restoration of CFTR-mediated chloride transport with sodium 4-phenylbutyrate in cystic fibrosis epithelial cells containing delta F508-CFTR von Rubenstein, R C, Egan, M E, Zeitlin, P L

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CFTR gene transduction in neonatal rabbits using an adeno-associated virus (AAV) vector von RUBENSTEIN, R. C, MCVEIGH, U, FLOTTE, T. R, GUGGINO, W. B, ZEITLIN, P. L

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Sodium 4-phenylbutyrate downregulates HSC70 expression by facilitating mRNA degradation von Rubenstein, Ronald C, Lyons, Bridget M

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Acute flank pain and reversible renal dysfunction associated with nonsteroidal anti-inflammatory drug use von MCINTIRE, S. C, RUBENSTEIN, R. C, GARTNER, J. C, GILBOA, N, ELLIS, D

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D25 PEDIATRIC CYSTIC FIBROSIS: Regulation Of The Erp29 Promoter By The F508del-Cftr Corrector 4-Phenylbutyrate And The E2f-1 Tanscription Factor von Alexiou, S, Suaud, L, Rubenstein, R C

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A topological data analytic approach for discovering biophysical signatures in protein dynamics von Tang, Wai Shing, da Silva, Gabriel Monteiro, Kirveslahti, Henry, Skeens, Erin, Feng, Bibo, Sudijono, Timothy, Yang, Kevin K, Mukherjee, Sayan, Rubenstein, Brenda, Crawford, Lorin

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The hydrophobic tryptic core of the beta-adrenergic receptor retains Gs regulatory activity in response to agonists and thiols von Rubenstein, RC, Wong, SK, Ross, EM

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Genistein Restores Functional Interactions between ΔF508-CFTR and ENaC in Xenopus Oocytes von Suaud, Laurence, Li, Jinqing, Jiang, Qinshi, Rubenstein, Ronald C., Kleyman, Thomas R.

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C62 PEDIATRIC CASES I: A Neonatal Presentation Of Co-Morbid Maple Syrup Urine Disease And Cystic Fibrosis von Friedman, N L, Grande, L M, Blair, J L, Yudkoff, M, Rubenstein, R C

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Genistein Improves Regulatory Interactions between G551D-Cystic Fibrosis Transmembrane Conductance Regulator and the Epithelial Sodium Channel in Xenopus Oocytes von Suaud, Laurence, Carattino, Marcelo, Kleyman, Thomas R., Rubenstein, Ronald C.

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Nocturnal saturation and glucose tolerance in children with cystic fibrosis von Suratwala, Dharmeshkumar, Chan, June S H, Kelly, Andrea, Meltzer, Lisa J, Gallagher, Paul R, Traylor, Joel, Rubenstein, Ronald C, Marcus, Carole L

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Differential Effects of Hsc70 and Hsp70 on the Intracellular Trafficking and Functional Expression of Epithelial Sodium Channels von Goldfarb, Samuel B., Kashlan, Ossama B., Watkins, Jeffrey N., Suaud, Laurence, Yan, Wusheng, Kleyman, Thomas R., Rubenstein, Ronald C.

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Risk Factors for Death of Patients with Cystic Fibrosis Awaiting Lung Transplantation von Belkin, Richard A, Henig, Noreen R, Singer, Lianne G, Chaparro, Cecilia, Rubenstein, Ronald C, Xie, Sharon X, Yee, Justin Y, Kotloff, Robert M, Lipson, David A, Bunin, Greta R

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Selectivity of the .beta.-adrenergic receptor among Gs, Gi's, and Go: assay using recombinant .alpha. subunits in reconstituted phospholipid vesicles von Rubenstein, Ronald C, Linder, Maurine E, Ross, Elliott M

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Sodium 4-phenylbutyrate downregulates Hsc70: implications for intracellular trafficking of Delta F508-CFTR von Rubenstein, Ronald C, Zeitlin, Pamela L

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A simplified cyclic adenosine monophosphate–mediated sweat rate test for quantitative measure of cystic fibrosis transmembrane regulator (CFTR) function von Callen, Amy, Diener-West, Marie, Zeitlin, Pamela L., Rubenstein, Ronald C.

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