TIA1 Mutations in Amyotrophic Lateral Sclerosis and Frontotemporal Dementia Promote Phase Separation and Alter Stress Granule Dynamics von Mackenzie, Ian R., Nicholson, Alexandra M., Sarkar, Mohona, Messing, James, Purice, Maria D., Pottier, Cyril, Annu, Kavya, Baker, Matt, Perkerson, Ralph B., Kurti, Aishe, Matchett, Billie J., Mittag, Tanja, Temirov, Jamshid, Hsiung, Ging-Yuek R., Krieger, Charles, Murray, Melissa E., Kato, Masato, Fryer, John D., Petrucelli, Leonard, Zinman, Lorne, Weintraub, Sandra, Mesulam, Marsel, Keith, Julia, Zivkovic, Sasha A., Hirsch-Reinshagen, Veronica, Roos, Raymond P., Züchner, Stephan, Graff-Radford, Neill R., Petersen, Ronald C., Caselli, Richard J., Wszolek, Zbigniew K., Finger, Elizabeth, Lippa, Carol, Lacomis, David, Stewart, Heather, Dickson, Dennis W., Kim, Hong Joo, Rogaeva, Ekaterina, Bigio, Eileen, Boylan, Kevin B., Taylor, J. Paul, Rademakers, Rosa

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Machine learning predicts translation initiation sites in neurologic diseases with nucleotide repeat expansions von Gleason, Alec C, Ghadge, Ghanashyam, Chen, Jin, Sonobe, Yoshifumi, Roos, Raymond P

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Translation of dipeptide repeat proteins from the C9ORF72 expanded repeat is associated with cellular stress von Sonobe, Yoshifumi, Ghadge, Ghanashyam, Masaki, Katsuhisa, Sendoel, Ataman, Fuchs, Elaine, Roos, Raymond P.

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Guanabenz, which enhances the unfolded protein response, ameliorates mutant SOD1-induced amyotrophic lateral sclerosis von Wang, Lijun, Popko, Brian, Tixier, Emily, Roos, Raymond P

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TDP-43 proteinopathy in Theiler's murine encephalomyelitis virus infection von Masaki, Katsuhisa, Sonobe, Yoshifumi, Ghadge, Ghanashyam, Pytel, Peter, Roos, Raymond P

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Apical dendrite degeneration, a novel cellular pathology for Betz cells in ALS von Genç, Barış, Jara, Javier H., Lagrimas, Amiko K. B., Pytel, Peter, Roos, Raymond P., Mesulam, M. Marsel, Geula, Changiz, Bigio, Eileen H., Özdinler, P. Hande

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Single chain variable fragment antibodies directed against SOD1 ameliorate disease in mutant SOD1 transgenic mice von Ghadge, Ghanashyam D., Kay, Brian K., Drigotas, Claire, Roos, Raymond P.

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A C. elegans model of C9orf72-associated ALS/FTD uncovers a conserved role for eIF2D in RAN translation von Sonobe, Yoshifumi, Aburas, Jihad, Krishnan, Gopinath, Fleming, Andrew C., Ghadge, Ghanashyam, Islam, Priota, Warren, Eleanor C., Gu, Yuanzheng, Kankel, Mark W., Brown, André E. X., Kiskinis, Evangelos, Gendron, Tania F., Gao, Fen-Biao, Roos, Raymond P., Kratsios, Paschalis

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Knockdown of GADD34 in neonatal mutant SOD1 mice ameliorates ALS von Ghadge, Ghanashyam D., Sonobe, Yoshifumi, Camarena, Adrian, Drigotas, Claire, Rigo, Frank, Ling, Karen K., Roos, Raymond P.

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Translation of dipeptide repeat proteins in C9ORF72 ALS/FTD through unique and redundant AUG initiation codons von Sonobe, Yoshifumi, Lee, Soojin, Krishnan, Gopinath, Gu, Yuanzheng, Kwon, Deborah Y, Gao, Fen-Biao, Roos, Raymond P, Kratsios, Paschalis

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The effect of mutant SOD1 dismutase activity on non-cell autonomous degeneration in familial amyotrophic lateral sclerosis von Wang, Lijun, Sharma, Kamal, Grisotti, Gabriella, Roos, Raymond P

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Evidence for an early innate immune response in the motor cortex of ALS von Jara, Javier H, Genç, Barış, Stanford, Macdonell J, Pytel, Peter, Roos, Raymond P, Weintraub, Sandra, Mesulam, M Marsel, Bigio, Eileen H, Miller, Richard J, Özdinler, P Hande

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Poloxamer 188 decreases membrane toxicity of mutant SOD1 and ameliorates pathology observed in SOD1 mouse model for ALS von Riehm, Jacob J., Wang, Lijun, Ghadge, Ghanashyam, Teng, Michael, Correa, Ana M., Marks, Jeremy D., Roos, Raymond P., Allen, Michael J.

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Zika Virus—A Public Health Emergency of International Concern von Roos, Raymond P

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Restricted expression of mutant SOD1 in spinal motor neurons and interneurons induces motor neuron pathology von Wang, Lijun, Sharma, Kamal, Deng, Han-Xiang, Siddique, Teepu, Grisotti, Gabriella, Liu, Erdong, Roos, Raymond P

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An enhanced integrated stress response ameliorates mutant SOD1-induced ALS von Wang, Lijun, Popko, Brian, Roos, Raymond P.

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Selective knockdown of mutant SOD1 in Schwann cells ameliorates disease in G85R mutant SOD1 transgenic mice von Wang, Lijun, Pytel, Peter, Feltri, M. Laura, Wrabetz, Lawrence, Roos, Raymond P

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Kozak Similarity Score Algorithm Identifies Alternative Translation Initiation Codons Implicated in Cancers von Gleason, Alec C., Ghadge, Ghanashyam, Sonobe, Yoshifumi, Roos, Raymond P.

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Different Strains of Theiler's Murine Encephalomyelitis Virus Antagonize Different Sites in the Type I Interferon Pathway von Stavrou, Spyridon, Feng, Zongdi, Lemon, Stanley M, Roos, Raymond P

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Apoptotic and Antiapoptotic Activity of L Protein of Theiler's Murine Encephalomyelitis Virus von STAVROU, Spyridon, GHADGE, Ghanashyam, ROOS, Raymond P

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