Severe Pulmonary Fibrosis as the First Manifestation of Interferonopathy ( TMEM173 Mutation) von Picard, Cécile, MD, Thouvenin, Guillaume, MD, Kannengiesser, Caroline, MD, PhD, Dubus, Jean-Christophe, MD, PhD, Jeremiah, Nadia, PhD, Rieux-Laucat, Frédéric, PhD, Crestani, Bruno, MD, PhD, Belot, Alexandre, MD, PhD, Thivolet-Béjui, Françoise, MD, PhD, Secq, Véronique, MD, PhD, Ménard, Christelle, Reynaud-Gaubert, Martine, MD, PhD, Reix, Philippe, MD, PhD

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The day after. Rethinking the Cystic Fibrosis model of care and structure of the CF team in the era of triple combination therapy von Reix, Philippe

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Impact of Coexistence Phenotype Between Staphylococcus aureus and Pseudomonas aeruginosa Isolates on Clinical Outcomes Among Cystic Fibrosis Patients von Briaud, Paul, Bastien, Sylvère, Camus, Laura, Boyadjian, Marie, Reix, Philippe, Mainguy, Catherine, Vandenesch, François, Doléans-Jordheim, Anne, Moreau, Karen

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Optimized approach for the identification of highly efficient correctors of nonsense mutations in human diseases von Benhabiles, Hana, Gonzalez-Hilarion, Sara, Amand, Séverine, Bailly, Christine, Prévotat, Anne, Reix, Philippe, Hubert, Dominique, Adriaenssens, Eric, Rebuffat, Sylvie, Tulasne, David, Lejeune, Fabrice

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Viral respiratory tract infections in young children with cystic fibrosis: a prospective full-year seasonal study von Eymery, Mathilde, Morfin, Florence, Doleans-Jordheim, Anne, Perceval, Marie, Ohlmann, Camille, Mainguy, Catherine, Reix, Philippe

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Editorial: New insights into caring for pediatric patients with cystic fibrosis von Bui, Stephanie, Delhaes, Laurence, Dournes, Gael, Reix, Philippe, Fayon, Michael John

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Lumacaftor/ivacaftor initiation in two liver transplantation patients under tacrolimus and antifungal azoles von Chouchane, Ikrame, Stremler‐Lebel, Nathalie, Reix, Philippe

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Pulmonary hemosiderosis in children with Down syndrome: a national experience von Alimi, Aurelia, Taytard, Jessica, Abou Taam, Rola, Houdouin, Véronique, Forgeron, Aude, Lubrano Lavadera, Marc, Cros, Pierrick, Gibertini, Isabelle, Derelle, Jocelyne, Deschildre, Antoine, Thumerelle, Caroline, Epaud, Ralph, Reix, Philippe, Fayon, Michael, Roullaud, Sylvie, Troussier, Françoise, Renoux, Marie-Catherine, de Blic, Jacques, Leyronnas, Sophie, Thouvenin, Guillaume, Perisson, Caroline, Ravel, Aimé, Clement, Annick, Corvol, Harriet, Nathan, Nadia

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Implementation of Model-Based Dose Adjustment of Tobramycin in Adult Patients with Cystic Fibrosis von Reverchon, Jérémy, Tuloup, Vianney, Garreau, Romain, Nave, Viviane, Cohen, Sabine, Reix, Philippe, Durupt, Stéphane, Nove-Josserand, Raphaele, Durieu, Isabelle, Reynaud, Quitterie, Bourguignon, Laurent, Charles, Sandrine, Goutelle, Sylvain

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Whole pulmonary assessment 1 year after paediatric acute respiratory distress syndrome: prospective multicentre study von Nève, Véronique, Sadik, Ahmed, Petyt, Laurent, Dauger, Stéphane, Kheniche, Ahmed, Denjean, André, Léger, Pierre-Louis, Chalard, François, Boulé, Michèle, Javouhey, Etienne, Reix, Philippe, Canterino, Isabelle, Deken, Valérie, Matran, Régis, Leteurtre, Stéphane, Leclerc, Francis

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Strong incidence of Pseudomonas aeruginosa on bacterial rrs and ITS genetic structures of cystic fibrosis sputa von Pages-Monteiro, Laurence, Marti, Romain, Commun, Carine, Alliot, Nolwenn, Bardel, Claire, Meugnier, Helene, Perouse-de-Montclos, Michele, Reix, Philippe, Durieu, Isabelle, Durupt, Stephane, Vandenesch, Francois, Freney, Jean, Cournoyer, Benoit, Doleans-Jordheim, Anne

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Chest physiotherapy enhances detection of Pseudomonas aeruginosa in nonexpectorating children with cystic fibrosis von Marguet, Christophe, Houdouin, Véronique, Pin, Isabelle, Reix, Philippe, Huet, Frédéric, Mittaine, Marie, Ramel, Sophie, Wizla-Derambure, Nathalie, Abely, Michel, Dalphin, Marie-Laure, Fayon, Michael, Bihouée, Tiphaine, Le Bourgeois, Muriel, Deneuville, Eric, Corvol, Harriet, Laurans, Muriel, Couderc, Laure, Leroux, Evelyne, Lémée, Ludovic

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Efficacy and Safety of Elexacaftor/Tezacaftor/Ivacaftor in Children 6 Through 11 Years of Age with Cystic Fibrosis Heterozygous for F508del and a Minimal Function Mutation: A Phase... von Mall, Marcus A, Brugha, Rossa, Gartner, Silvia, Legg, Julian, Moeller, Alexander, Mondejar-Lopez, Pedro, Prais, Dario, Pressler, Tacjana, Ratjen, Felix, Reix, Philippe, Robinson, Paul D, Selvadurai, Hiran, Stehling, Florian, Ahluwalia, Neil, Arteaga-Solis, Emilio, Bruinsma, Bote G, Jennings, Mark, Moskowitz, Samuel M, Noel, Sabrina, Tian, Simon, Weinstock, Tanya G, Wu, Pan, Wainwright, Claire E, Davies, Jane C

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Efficacy and tolerance of intravenous methylprednisolone pulses in children with severe bronchopulmonary dysplasia requiring respiratory support von Reynaud, Josseline, Dreyfus, Lélia, Coutier, Laurianne, Butin, Marine, Godbert, Isabelle, Baudin, Florent, Horvat, Côme, Reix, Philippe

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Moving the Dial on Airway Inflammation in Response to Trikafta in Adolescents with Cystic Fibrosis von Lepissier, Agathe, Bonnel, Anne Sophie, Wizla, Nathalie, Weiss, Laurence, Mittaine, Marie, Bessaci, Katia, Kerem, Eitan, Houdouin, Véronique, Reix, Philippe, Marguet, Christophe, Sermet-Gaudelus, Isabelle

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Efficacy and safety of lumacaftor and ivacaftor in patients aged 6–11 years with cystic fibrosis homozygous for F508del-CFTR : a randomised, placebo-controlled phase 3 trial von Ratjen, Felix, Prof, Hug, Christopher, MD, Marigowda, Gautham, MD, Tian, Simon, MD, Huang, Xiaohong, PhD, Stanojevic, Sanja, PhD, Milla, Carlos E, MD, Robinson, Paul D, MBChB, Waltz, David, MD, Davies, Jane C, Prof

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Factors of late respiratory support or oxygen weaning in infants with bronchopulmonary dysplasia von Garcia-Anton, Alma, Dreyfus, Lélia, Portefaix, Aurélie, Baudin, Florent, Plaisant, Franck, Loppinet, Thomas, Reix, Philippe, Butin, Marine, Coutier, Laurianne

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Impact of prone positioning in infants with Pierre Robin sequence: a polysomnography study von Coutier, L., Guyon, A., Reix, Philippe, Franco, P.

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Population Pharmacokinetic Modeling and Dosing Simulations of Tobramycin in Pediatric Patients with Cystic Fibrosis von Praet, Antonin, Bourguignon, Laurent, Vetele, Florence, Breant, Valentine, Genestet, Charlotte, Dumitrescu, Oana, Doleans-Jordheim, Anne, Reix, Philippe, Goutelle, Sylvain

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HOMA indices as screening tests for cystic fibrosis-related diabetes von Toin, Tom, Reynaud, Quitterie, Denis, Angélique, Durieu, Isabelle, Mainguy, Catherine, Llerena, Catherine, Pin, Isabelle, Touzet, Sandrine, Reix, Philippe

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