The role of pyocyanin in Pseudomonas aeruginosa infection von Lau, Gee W., Hassett, Daniel J., Ran, Huimin, Kong, Fansheng

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Combination of acid β-glucosidase mutation and Saposin C deficiency in mice reveals Gba1 mutation dependent and tissue-specific disease phenotype von Liou, Benjamin, Zhang, Wujuan, Fannin, Venette, Quinn, Brian, Ran, Huimin, Xu, Kui, Setchell, Kenneth D. R., Witte, David, Grabowski, Gregory A., Sun, Ying

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Neuronopathic Gaucher disease in the mouse: viable combined selective saposin C deficiency and mutant glucocerebrosidase (V394L) mice with glucosylsphingosine and glucosylceramide... von Sun, Ying, Liou, Benjamin, Ran, Huimin, Skelton, Matthew R., Williams, Michael T., Vorhees, Charles V., Kitatani, Kazuyuki, Hannun, Yusuf A., Witte, David P., Xu, You-Hai, Grabowski, Gregory A.

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Pseudomonas aeruginosa Pyocyanin Is Critical for Lung Infection in Mice von Lau, Gee W, Ran, Huimin, Kong, Fansheng, Hassett, Daniel J, Mavrodi, Dimitri

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Properties of neurons derived from induced pluripotent stem cells of Gaucher disease type 2 patient fibroblasts: potential role in neuropathology von Sun, Ying, Florer, Jane, Mayhew, Christopher N, Jia, Zhanfeng, Zhao, Zhiying, Xu, Kui, Ran, Huimin, Liou, Benjamin, Zhang, Wujuan, Setchell, Kenneth D R, Gu, Jianguo, Grabowski, Gregory A

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Isofagomine in vivo effects in a neuronopathic Gaucher disease mouse von Sun, Ying, Ran, Huimin, Liou, Benjamin, Quinn, Brian, Zamzow, Matt, Zhang, Wujuan, Bielawski, Jacek, Kitatani, Kazuyuki, Setchell, Kenneth D R, Hannun, Yusuf A, Grabowski, Gregory A

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Human Targets of Pseudomonas aeruginosa Pyocyanin von Ran, Huimin, Hassett, Daniel J., Lau, Gee W.

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Specific saposin C deficiency: CNS impairment and acid β-glucosidase effects in the mouse von Sun, Ying, Ran, Huimin, Zamzow, Matt, Kitatani, Kazuyuki, Skelton, Matthew R., Williams, Michael T., Vorhees, Charles V., Witte, David P., Hannun, Yusuf A., Grabowski, Gregory A.

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Combined saposin C and D deficiencies in mice lead to a neuronopathic phenotype, glucosylceramide and α-hydroxy ceramide accumulation, and altered prosaposin trafficking von Sun, Ying, Witte, David P., Zamzow, Matt, Ran, Huimin, Quinn, Brian, Matsuda, Junko, Grabowski, Gregory A.

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In vivo and ex vivo evaluation of L-type calcium channel blockers on acid beta-glucosidase in Gaucher disease mouse models von Sun, Ying, Liou, Benjamin, Quinn, Brian, Ran, Huimin, Xu, You-Hai, Grabowski, Gregory A

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Neurological deficits and glycosphingolipid accumulation in saposin B deficient mice von Sun, Ying, Witte, David P., Ran, Huimin, Zamzow, Matt, Barnes, Sonya, Cheng, Hua, Han, Xianlin, Williams, Michael T., Skelton, Matthew R., Vorhees, Charles V., Grabowski, Gregory A.

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Temporal gene expression profiling reveals CEBPD as a candidate regulator of brain disease in prosaposin deficient mice von Sun, Ying, Jia, Li, Williams, Michael T, Zamzow, Matt, Ran, Huimin, Quinn, Brian, Aronow, Bruce J, Vorhees, Charles V, Witte, David P, Grabowski, Gregory A

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Pseudomonas aeruginosa pyocyanin inactivates lung epithelial vaculoar ATPase‐dependent cystic fibrosis transmembrane conductance regulator expression and localization von Kong, Fansheng, Young, Lisa, Chen, Yi, Ran, Huimin, Meyers, Melanie, Joseph, Patricia, Cho, You‐Hee, Hassett, Daniel J., Lau, Gee W.

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Reversal of advanced disease in lysosomal acid lipase deficient mice: A model for lysosomal acid lipase deficiency disease von Sun, Ying, Xu, You-Hai, Du, Hong, Quinn, Brian, Liou, Benjamin, Stanton, Lori, Inskeep, Venette, Ran, Huimin, Jakubowitz, Phillip, Grilliot, Nicholas, Grabowski, Gregory A.

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A Method on a Rapid Generation of Exquisite Textures of Building's Roof Towards Planning von Liu, Quanhai, Deng, Fei, Li, Lou, Ran, Huiming

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Tissue-specific effects of saposin A and saposin B on glycosphingolipid degradation in mutant mice von Sun, Ying, Zamzow, Matt, Ran, Huimin, Zhang, Wujuan, Quinn, Brian, Barnes, Sonya, Witte, David P, Setchell, Kenneth D R, Williams, Michael T, Vorhees, Charles V, Grabowski, Gregory A

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In Vivo and Ex Vivo Evaluation of L-Type Calcium Channel Blockers on Acid [beta]-Glucosidase in Gaucher Disease Mouse Models von Sun, Ying, Liou, Benjamin, Quinn, Brian, Ran, Huimin, Xu, You-Hai, Grabowski, Gregory A

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Pseudomonas aeruginosa pyocyanin inactivates lung epithelial vacuolar ATPase-dependent cystic fibrosis transmembrane conductance regulator expression and localization von Kong, Fansheng, Young, Lisa, Chen, Yi, Ran, Huimin, Meyers, Melanie, Joseph, Patricia, Cho, You-Hee, Hassett, Daniel J, Lau, Gee W

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Specific saposin C deficiency: CNS impairment and acid b-glucosidase effects in the mouse von Sun, Ying, Ran, Huimin, Zamzow, Matt, Kitatani, Kazuyuki, Skelton, Matthew R, Williams, Michael T, Vorhees, Charles V, Witte, David P, Hannun, Yusuf A, Grabowski, Gregory A

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137. In vivo evaluation of small molecule therapy on Gaucher disease mouse models von Sun, Ying, Liou, Benjamin, Brandewie, Jaclyn, Ran, Huimin, Quinn, Brian, Kitatani, Kazuyuki, Hannun, Yusuf, Grabowski, Gregory

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