Supercompetitor Status of Drosophila Myc Cells Requires p53 as a Fitness Sensor to Reprogram Metabolism and Promote Viability von de la Cova, Claire, Senoo-Matsuda, Nanami, Ziosi, Marcello, Wu, D. Christine, Bellosta, Paola, Quinzii, Catarina M., Johnston, Laura A.

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Coenzyme Q and mitochondrial disease von Quinzii, Catarina M., Hirano, Michio

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Aurora kinase A inhibition reverses the Warburg effect and elicits unique metabolic vulnerabilities in glioblastoma von Nguyen, Trang T. T., Shang, Enyuan, Shu, Chang, Kim, Sungsoo, Mela, Angeliki, Humala, Nelson, Mahajan, Aayushi, Yang, Hee Won, Akman, Hasan Orhan, Quinzii, Catarina M., Zhang, Guoan, Westhoff, Mike-Andrew, Karpel-Massler, Georg, Bruce, Jeffrey N., Canoll, Peter, Siegelin, Markus D.

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High-Mobility Group Box 1 Is Dispensable for Autophagy, Mitochondrial Quality Control, and Organ Function In Vivo von Huebener, Peter, Gwak, Geum-Youn, Pradere, Jean-Philippe, Quinzii, Catarina M., Friedman, Richard, Lin, Chyuan-Sheng, Trent, Chad M., Mederacke, Ingmar, Zhao, Enpeng, Dapito, Dianne H., Lin, Yuxi, Goldberg, Ira J., Czaja, Mark J., Schwabe, Robert F.

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Loss-of-function mutations in MGME1 impair mtDNA replication and cause multisystemic mitochondrial disease von Kornblum, Cornelia, Nicholls, Thomas J, Haack, Tobias B, Schöler, Susanne, Peeva, Viktoriya, Danhauser, Katharina, Hallmann, Kerstin, Zsurka, Gábor, Rorbach, Joanna, Iuso, Arcangela, Wieland, Thomas, Sciacco, Monica, Ronchi, Dario, Comi, Giacomo P, Moggio, Maurizio, Quinzii, Catarina M, DiMauro, Salvatore, Calvo, Sarah E, Mootha, Vamsi K, Klopstock, Thomas, Strom, Tim M, Meitinger, Thomas, Minczuk, Michal, Kunz, Wolfram S, Prokisch, Holger

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Targeting a Braf/Mapk pathway rescues podocyte lipid peroxidation in CoQ-deficiency kidney disease von Sidhom, Eriene-Heidi, Kim, Choah, Kost-Alimova, Maria, Ting, May Theng, Keller, Keith, Avila-Pacheco, Julian, Watts, Andrew Jb, Vernon, Katherine A, Marshall, Jamie L, Reyes-Bricio, Estefanía, Racette, Matthew, Wieder, Nicolas, Kleiner, Giulio, Grinkevich, Elizabeth J, Chen, Fei, Weins, Astrid, Clish, Clary B, Shaw, Jillian L, Quinzii, Catarina M, Greka, Anna

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Abnormalities of hydrogen sulfide and glutathione pathways in mitochondrial dysfunction von Quinzii, Catarina M, Lopez, Luis C

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Coenzyme Q10 modulates sulfide metabolism and links the mitochondrial respiratory chain to pathways associated to one carbon metabolism von González-García, Pilar, Hidalgo-Gutiérrez, Agustín, Mascaraque, Cristina, Barriocanal-Casado, Eliana, Bakkali, Mohammed, Ziosi, Marcello, Abdihankyzy, Ussipbek Botagoz, Sánchez-Hernández, Sabina, Escames, Germaine, Prokisch, Holger, Martín, Francisco, Quinzii, Catarina M, López, Luis C

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Metabolic Targets of Coenzyme Q10 in Mitochondria von Hidalgo-Gutiérrez, Agustín, González-García, Pilar, Díaz-Casado, María Elena, Barriocanal-Casado, Eliana, López-Herrador, Sergio, Quinzii, Catarina M, López, Luis C

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Treatment of CoQ(10) deficient fibroblasts with ubiquinone, CoQ analogs, and vitamin C: time- and compound-dependent effects von López, Luis C, Quinzii, Catarina M, Area, Estela, Naini, Ali, Rahman, Shamima, Schuelke, Markus, Salviati, Leonardo, Dimauro, Salvatore, Hirano, Michio

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Activation of LXRβ inhibits tumor respiration and is synthetically lethal with Bcl‐xL inhibition von Nguyen, Trang Thi Thu, Ishida, Chiaki Tsuge, Shang, Enyuan, Shu, Chang, Torrini, Consuelo, Zhang, Yiru, Bianchetti, Elena, Sanchez‐Quintero, Maria J, Kleiner, Giulio, Quinzii, Catarina M, Westhoff, Mike‐Andrew, Karpel‐Massler, Georg, Canoll, Peter, Siegelin, Markus D

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Deoxypyrimidine monophosphate bypass therapy for thymidine kinase 2 deficiency von Garone, Caterina, Garcia‐Diaz, Beatriz, Emmanuele, Valentina, Lopez, Luis C, Tadesse, Saba, Akman, Hasan O, Tanji, Kurenai, Quinzii, Catarina M, Hirano, Michio

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A Nonsense Mutation in COQ9 Causes Autosomal-Recessive Neonatal-Onset Primary Coenzyme Q10 Deficiency: A Potentially Treatable Form of Mitochondrial Disease von Duncan, Andrew J., Bitner-Glindzicz, Maria, Meunier, Brigitte, Costello, Harry, Hargreaves, Iain P., López, Luis C., Hirano, Michio, Quinzii, Catarina M., Sadowski, Michael I., Hardy, John, Singleton, Andrew, Clayton, Peter T., Rahman, Shamima

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Mechanisms and Therapeutic Effects of Benzoquinone Ring Analogs in Primary CoQ Deficiencies von Pesini, Alba, Hidalgo-Gutierrez, Agustin, Quinzii, Catarina M

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Coenzyme Q deficiency causes impairment of the sulfide oxidation pathway von Ziosi, Marcello, Di Meo, Ivano, Kleiner, Giulio, Gao, Xing‐Huang, Barca, Emanuele, Sanchez‐Quintero, Maria J, Tadesse, Saba, Jiang, Hongfeng, Qiao, Changhong, Rodenburg, Richard J, Scalais, Emmanuel, Schuelke, Markus, Willard, Belinda, Hatzoglou, Maria, Tiranti, Valeria, Quinzii, Catarina M

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The Role of Sulfide Oxidation Impairment in the Pathogenesis of Primary CoQ Deficiency von Quinzii, Catarina M, Luna-Sanchez, Marta, Ziosi, Marcello, Hidalgo-Gutierrez, Agustin, Kleiner, Giulio, Lopez, Luis C

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The clinical heterogeneity of coenzyme Q10 deficiency results from genotypic differences in the Coq9 gene von Luna‐Sánchez, Marta, Díaz‐Casado, Elena, Barca, Emanuele, Tejada, Miguel Ángel, Montilla‐García, Ángeles, Cobos, Enrique Javier, Escames, Germaine, Acuña‐Castroviejo, Dario, Quinzii, Catarina M, López, Luis Carlos

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ANO10 mutations cause ataxia and coenzyme Q10 deficiency von Balreira, Andrea, Boczonadi, Veronika, Barca, Emanuele, Pyle, Angela, Bansagi, Boglarka, Appleton, Marie, Graham, Claire, Hargreaves, Iain P., Rasic, Vedrana Milic, Lochmüller, Hanns, Griffin, Helen, Taylor, Robert W., Naini, Ali, Chinnery, Patrick F., Hirano, Michio, Quinzii, Catarina M., Horvath, Rita

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Mitochondrial dysfunction in fibroblasts of Multiple System Atrophy von Monzio Compagnoni, Giacomo, Kleiner, Giulio, Bordoni, Andreina, Fortunato, Francesco, Ronchi, Dario, Salani, Sabrina, Guida, Marianna, Corti, Corrado, Pichler, Irene, Bergamini, Christian, Fato, Romana, Pellecchia, Maria Teresa, Vallelunga, Annamaria, Del Sorbo, Francesca, Elia, Antonio, Reale, Chiara, Garavaglia, Barbara, Mora, Gabriele, Albanese, Alberto, Cogiamanian, Filippo, Ardolino, Gianluca, Bresolin, Nereo, Corti, Stefania, Comi, Giacomo P., Quinzii, Catarina M., Di Fonzo, Alessio

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CoQ10 supplementation rescues nephrotic syndrome through normalization of H2S oxidation pathway von Kleiner, Giulio, Barca, Emanuele, Ziosi, Marcello, Emmanuele, Valentina, Xu, Yimeng, Hidalgo-Gutierrez, Agustin, Qiao, Changhong, Tadesse, Saba, Area-Gomez, Estela, Lopez, Luis C., Quinzii, Catarina M.

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