Glycosphingolipid Changes in Plasma in Parkinson's Disease Independent of Glucosylceramide Levels von Vruchte, Danielle, Sturchio, Andrea, Priestman, David A., Tsitsi, Panagiota, Hertz, Ellen, Andréasson, Mattias, Markaki, Ioanna, Wallom, Kerri‐Lee, Platt, Frances, Svenningsson, Per

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Infantile-onset symptomatic epilepsy syndrome caused by a homozygous loss-of-function mutation of GM3 synthase von Crosby, Andrew H, Simpson, Michael A, Cross, Harold, Proukakis, Christos, Priestman, David A, Neville, David C A, Reinkensmeier, Gabriele, Wang, Heng, Wiznitzer, Max, Gurtz, Kay, Verganelaki, Argyro, Pryde, Anna, Patton, Michael A, Dwek, Raymond A, Butters, Terry D, Platt, Frances M

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Analysis of fluorescently labeled glycosphingolipid-derived oligosaccharides following ceramide glycanase digestion and anthranilic acid labeling von Neville, David C.A, Coquard, Virginie, Priestman, David A, te Vruchte, Danielle J.M, Sillence, Daniel J, Dwek, Raymond A, Platt, Frances M, Butters, Terry D

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Increased glycosphingolipid levels in serum and aortae of apolipoprotein E gene knockout mice von Garner, Brett, Priestman, David A, Stocker, Roland, Harvey, David J, Butters, Terry D, Platt, Frances M

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Inhibition of substrate synthesis as a strategy for glycolipid lysosomal storage disease therapy von Platt, F. M., Jeyakumar, M., Andersson, U., Priestman, D. A., Dwek, R. A., Butters, T. D., Cox, T. M., Lachmann, R. H., Hollak, C., Aerts, J. M. F. G., Van Weely, S., Hrebícek, M., Moyses, C., Gow, I., Elstein, D., Zimran, A.

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Mechanisms modifying glucose oxidation in diabetes mellitus von Randle, P J, Priestman, D A, Mistry, S, Halsall, A

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Ionization and fragmentation of neutral and acidic glycosphingolipids with a Q-TOF mass spectrometer fitted with a MALDI ion source von Hunnam, Victoria, Harvey, David J., Priestman, David A., Bateman, Robert H., Bordoli, Robert S., Tyldesley, Richard

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Glucose fatty acid interactions and the regulation of glucose disposal von Randle, Philip J., Priestman, David A., Mistry, Sharad C., Halsall, Antony

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Web Radio: Radio Production for Internet Streaming von Priestman, Chris

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Studies of the long-term regulation of hepatic pyruvate dehydrogenase kinase von Sugden, M C, Fryer, L G, Orfali, K A, Priestman, D A, Donald, E, Holness, M J

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Fasting and decreased B cell sensitivity: important role for fatty acid-induced inhibition of PDH activity von Zhou, Y. P, Priestman, D. A, Randle, P. J, Grill, V. E

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Imino sugar therapy for type 1 Gaucher disease von Priestman, D A, Platt, F M, Dwek, R A, Butters, T D

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An iPSC model of hereditary sensory neuropathy-1 reveals L-serine-responsive deficits in neuronal ganglioside composition and axoglial interactions von Clark, AJ, Kugathasan, U, Baskozos, G, Priestman, DA, Fugger, N, Lone, MA, Othman, A, Chu, KH, Blesneac, I, Wilson, ER, Laurà, M, Kalmar, B, Greensmith, L, Hornemann, T, Platt, FM, Reilly, MM, Bennett, DL

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Different mechanisms underlie the long-term regulation of pyruvate dehydrogenase kinase (PDHK) by tri-iodothyronine in heart and liver von Priestman, David A, Donald, Elaine, Holness, Mark J, Sugden, Mary C

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Systemic AAV9 gene therapy using the synapsin I promoter rescues a mouse model of neuronopathic Gaucher disease but with limited cross-correction potential to astrocytes von Massaro, G, Hughes, MP, Whaler, SM, Wallom, K-L, Priestman, DA, Platt, FM, Waddington, SN, Rahim, AA

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Pyruvate inhibition of pyruvate dehydrogenase kinase: Effects of progressive starvation and hyperthyroidism in vivo, and of dibutyryl cyclic AMP and fatty acids in cultured cardiac... von Priestman, David A., Orfali, Karen A., Sugden, Mary C.

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Impact of Protein Restriction on the Regulation of Cardiac Carnitine Palmitoyltransferase by Malonyl-CoA von Holness, Mark J, Priestman, David A, Sugden, Mary C

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Hyperthyroidism Facilitates Cardiac Fatty Acid Oxidation Through Altered Regulation of Cardiac Carnitine Palmitoyltransferase: Studies in Vivo and with Cardiac Myocytes von Sugden, M. C., Priestman, D. A., Orfali, K. A., Holness, M. J.

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Molecular Mechanisms Underlying the Long-term Impact of Dietary Fat to Increase Cardiac Pyruvate Dehydrogenase Kinase: Regulation by Insulin, Cyclic AMP and Pyruvate von Sugden, Mary C., Orfali, Karen A., Fryer, Lee G.D., Holness, Mark J., Priestman, David A.

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Moderate protein restriction during pregnancy modifies the regulation of triacylglycerol turnover and leads to dysregulation of insulin’s anti-lipolytic action von Holness, M.J, Fryer, L.G.D, Priestman, D.A, Sugden, M.C

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