N-butyldeoxynojirimycin causes weight loss as a result of appetite suppression in lean and obese mice von Priestman, D.A, van der Spoel, A.C, Butters, T.D, Dwek, R.A, Platt, F.M

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Severe endothelial dysfunction in the aorta of a mouse model of Fabry disease; partial prevention by N‐butyldeoxynojirimycin treatment von Heare, T., Alp, N. J., Priestman, D. A., Kulkarni, A. B., Qasba, P., Butters, T. D., Dwek, R. A., Clarke, K., Channon, K. M., Platt, F. M.

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Inhibition of substrate synthesis as a strategy for glycolipid lysosomal storage disease therapy von Platt, F. M., Jeyakumar, M., Andersson, U., Priestman, D. A., Dwek, R. A., Butters, T. D., Cox, T. M., Lachmann, R. H., Hollak, C., Aerts, J. M. F. G., Van Weely, S., Hrebícek, M., Moyses, C., Gow, I., Elstein, D., Zimran, A.

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Mechanisms modifying glucose oxidation in diabetes mellitus von Randle, P J, Priestman, D A, Mistry, S, Halsall, A

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Fasting and decreased B cell sensitivity: important role for fatty acid-induced inhibition of PDH activity von Zhou, Y. P, Priestman, D. A, Randle, P. J, Grill, V. E

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Imino sugar therapy for type 1 Gaucher disease von Priestman, D A, Platt, F M, Dwek, R A, Butters, T D

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Role of protein synthesis and of fatty acid metabolism in the longer-term regulation of pyruvate dehydrogenase kinase von PRIESTMAN, D. A, MISTRY, S. C, HALSALL, A, RANDLE, P. J

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Hyperthyroidism Facilitates Cardiac Fatty Acid Oxidation Through Altered Regulation of Cardiac Carnitine Palmitoyltransferase: Studies in Vivo and with Cardiac Myocytes von Sugden, M. C., Priestman, D. A., Orfali, K. A., Holness, M. J.

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Ionization and fragmentation of neutral and acidic glycosphingolipids with a Q-TOF mass spectrometer fitted with a MALDI ion source von Hunnam, Victoria, Harvey, David J., Priestman, David A., Bateman, Robert H., Bordoli, Robert S., Tyldesley, Richard

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Glycosphingolipid Changes in Plasma in Parkinson's Disease Independent of Glucosylceramide Levels von Vruchte, Danielle, Sturchio, Andrea, Priestman, David A., Tsitsi, Panagiota, Hertz, Ellen, Andréasson, Mattias, Markaki, Ioanna, Wallom, Kerri‐Lee, Platt, Frances, Svenningsson, Per

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Moderate protein restriction during pregnancy modifies the regulation of triacylglycerol turnover and leads to dysregulation of insulin’s anti-lipolytic action von Holness, M.J, Fryer, L.G.D, Priestman, D.A, Sugden, M.C

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Glucose fatty acid interactions and the regulation of glucose disposal von Randle, Philip J., Priestman, David A., Mistry, Sharad C., Halsall, Antony

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Pretranslational regulation of pyruvate dehydrogenase complex subunits in white adipose tissue during the suckling-weaning transition in the rat von Maury, J, Kerbey, A.L, Priestman, D.A, Patel, M.S, Girard, J, Ferre, P

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Evidence that rat liver pyruvate dehydrogenase kinase activator protein is a pyruvate dehydrogenase kinase von MISTRY, S. C, PRIESTMAN, D. A, KERBEY, A. L, RANDLE, P. J

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Purification and partial characterization of rat liver pyruvate dehydrogenase kinase activator protein (free pyruvate dehydrogenase kinase) von Priestman, David A., Mistry, Sharad C., Kerbey, Alan L., Randle, Philip J.

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Presence in human cells and tissues of two prolidases and their alteration in prolidase deficiency von Butterworth, J., Priestman, D. A.

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Infantile-onset symptomatic epilepsy syndrome caused by a homozygous loss-of-function mutation of GM3 synthase von Crosby, Andrew H, Simpson, Michael A, Cross, Harold, Proukakis, Christos, Priestman, David A, Neville, David C A, Reinkensmeier, Gabriele, Wang, Heng, Wiznitzer, Max, Gurtz, Kay, Verganelaki, Argyro, Pryde, Anna, Patton, Michael A, Dwek, Raymond A, Butters, Terry D, Platt, Frances M

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Prolinase and non-specific dipeptidase of human kidney von Priestman, D A, Butterworth, J

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Studies of the long-term regulation of hepatic pyruvate dehydrogenase kinase von Sugden, M C, Fryer, L G, Orfali, K A, Priestman, D A, Donald, E, Holness, M J

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Analysis of fluorescently labeled glycosphingolipid-derived oligosaccharides following ceramide glycanase digestion and anthranilic acid labeling von Neville, David C.A, Coquard, Virginie, Priestman, David A, te Vruchte, Danielle J.M, Sillence, Daniel J, Dwek, Raymond A, Platt, Frances M, Butters, Terry D

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