Friedreich's ataxia reveals a mechanism for coordinate regulation of oxidative metabolism via feedback inhibition of the SIRT3 deacetylase von WAGNER, Gregory R, PRIDE, P. Melanie, BABBEY, Clifford M, PAYNE, R. Mark

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Progressive mitochondrial protein lysine acetylation and heart failure in a model of Friedreich's ataxia cardiomyopathy von Stram, Amanda R, Wagner, Gregory R, Fogler, Brian D, Pride, P Melanie, Hirschey, Matthew D, Payne, R Mark

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A TAT―Frataxin fusion protein increases lifespan and cardiac function in a conditional Friedreich's ataxia mouse model von VYAS, Piyush M, TOMAMICHEL, Wendy J, MELANIE PRIDE, P, BABBEY, Clifford M, QIUJUAN WANG, MERCIER, Jennifer, MARTIN, Elizabeth M, MARK PANE, R

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A Barth Syndrome Patient-Derived D75H Point Mutation in TAFAZZIN Drives Progressive Cardiomyopathy in Mice von Snider, Paige L, Sierra Potchanant, Elizabeth A, Sun, Zejin, Edwards, Donna M, Chan, Ka-Kui, Matias, Catalina, Awata, Junya, Sheth, Aditya, Pride, P Melanie, Payne, R Mark, Rubart, Michael, Brault, Jeffrey J, Chin, Michael T, Nalepa, Grzegorz, Conway, Simon J

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Biomarker sST2 in Adults with Transposition of the Great Arteries Palliated by Mustard Procedure: A Five-Year Follow-up von Ferguson, Haley N., Martinez, Hugo R., Pride, P. Melanie, Swan, Elizabeth A., Hurwitz, Roger A., Payne, R. Mark

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Genomic Designs of rAAVs Contribute to Pathological Changes in the Livers and Spleens of Mice von Mulcrone, Patrick L., Zhang, Junping, Pride, P. Melanie, Lam, Anh K., Frabutt, Dylan A., Ball-Kell, Susan M., Xiao, Weidong

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Cardiomyopathy of Friedreich’s Ataxia: Use of Mouse Models to Understand Human Disease and Guide Therapeutic Development von Payne, R. Mark, Pride, P. Melanie, Babbey, Clifford M.

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NAD + replacement therapy with nicotinamide riboside does not improve cardiac function in a model of mitochondrial heart disease von Stram, Amanda R., Pride, P. Melanie, Payne, R. Mark

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Reversal of Age‐related Impairment in Collateral Growth by Tempol von Coppinger, Brian, Theodorakis, Janice L, Theodorakis, Nicholas G, Pride, P Melanie, Unthank, Joseph L, Miller, Steven J

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Age‐related impairment in collateral growth is due to oxidant stress and decreased nitric oxide bioavailability von Madren, Kathryn, Bratz, Ian, Dick, Gregory, Tune, Johnathan, Bohlen, H. Glenn, Pride, P. Melanie, Bills, Randall, Zhou, Xiaosun, Unthank, Joseph, Miller, Steven J

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BIOMARKER FOR DETERMINING MITOCHONDRIAL DAMAGE IN FRIEDREICH'S ATAXIA von Payne R. Mark, Babbey Clifford M, Wagner Gregory R, Pride P. Melanie

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Biomarker for determining mitochondrial damage in friedreich's ataxia von Payne R. Mark, Babbey Clifford M, Wagner Gregory R, Pride P. Melanie

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Progressive mitochondrial protein lysine acetylation and heart failure in a model of Friedreich's ataxia cardiomyopathy von Stram, Amanda R, Wagner, Gregory R, Fogler, Brian D, Pride, P. Melanie, Hirschey, Matthew D, Payne, R. Mark

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BIOMARKER FOR DETERMINING MITOCHONDRIAL DAMAGE IN FRIEDREICH'S ATAXIA von BABBEY CLIFFORD M, WAGNER GREGORY R, PRIDE P. MELANIE, PAYNE R. MARK

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A BIOMARKER FOR DETERMINING MITOCHONDRIAL DAMAGE IN FRIEDREICH'S ATAXIA von PAYNE, RONALD MARK, BABBEY, CLIFFORD M, WAGNER, GREGORY R, PRIDE, P. MELANIE

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Germline Chd8 haploinsufficiency alters brain development in mouse von Gompers, Andrea L, Su-Feher, Linda, Ellegood, Jacob, Copping, Nycole A, Riyadh, M Asrafuzzaman, Stradleigh, Tyler W, Pride, Michael C, Schaffler, Melanie D, Wade, A Ayanna, Catta-Preta, Rinaldo, Zdilar, Iva, Louis, Shreya, Kaushik, Gaurav, Mannion, Brandon J, Plajzer-Frick, Ingrid, Afzal, Veena, Visel, Axel, Pennacchio, Len A, Dickel, Diane E, Lerch, Jason P, Crawley, Jacqueline N, Zarbalis, Konstantinos S, Silverman, Jill L, Nord, Alex S

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Germline Chd8 haploinsufficiency alters brain development in mouse von Gompers, Andrea L, Su-Feher, Linda, Ellegood, Jacob, Copping, Nycole A, Riyadh, M Asrafuzzaman, Stradleigh, Tyler W, Pride, Michael C, Schaffler, Melanie D, Wade, A Ayanna, Catta-Preta, Rinaldo, Zdilar, Iva, Louis, Shreya, Kaushik, Gaurav, Mannion, Brandon J, Plajzer-Frick, Ingrid, Afzal, Veena, Visel, Axel, Pennacchio, Len A, Dickel, Diane E, Lerch, Jason P, Crawley, Jacqueline N, Zarbalis, Konstantinos S, Silverman, Jill L, Nord, Alex S

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