A Human-Mouse Chimeric Model of Obliterative Bronchiolitis after Lung Transplantation von Xue, Jianmin, Zhu, Xuehai, George, M. Patricia, Myerburg, Michael M, Stoner, Michael W, Pilewski, Joseph W, Duncan, Steven R

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Egr-1 regulates autophagy in cigarette smoke-induced chronic obstructive pulmonary disease von Chen, Zhi-Hua, Kim, Hong Pyo, Sciurba, Frank C, Lee, Seon-Jin, Feghali-Bostwick, Carol, Stolz, Donna B, Dhir, Rajiv, Landreneau, Rodney J, Schuchert, Mathew J, Yousem, Samuel A, Nakahira, Kiichi, Pilewski, Joseph M, Lee, Janet S, Zhang, Yingze, Ryter, Stefan W, Choi, Augustine M K

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Effect of VX-770 in Persons with Cystic Fibrosis and the G551D-CFTR Mutation von Accurso, Frank J, Rowe, Steven M, Clancy, J.P, Boyle, Michael P, Dunitz, Jordan M, Durie, Peter R, Sagel, Scott D, Hornick, Douglas B, Konstan, Michael W, Donaldson, Scott H, Moss, Richard B, Pilewski, Joseph M, Rubenstein, Ronald C, Uluer, Ahmet Z, Aitken, Moira L, Freedman, Steven D, Rose, Lynn M, Mayer-Hamblett, Nicole, Dong, Qunming, Zha, Jiuhong, Stone, Anne J, Olson, Eric R, Ordoñez, Claudia L, Campbell, Preston W, Ashlock, Melissa A, Ramsey, Bonnie W

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Prospective Evaluation of Coronavirus Disease 2019 (COVID-19) Vaccine Responses Across a Broad Spectrum of Immunocompromising Conditions: the COVID-19 Vaccination in the Immunocomp... von Haidar, Ghady, Agha, Mounzer, Bilderback, Andrew, Lukanski, Amy, Linstrum, Kelsey, Troyan, Rachel, Rothenberger, Scott, McMahon, Deborah K, Crandall, Melissa D, Sobolewksi, Michele D, Nathan Enick, P, Jacobs, Jana L, Collins, Kevin, Klamar-Blain, Cynthia, Macatangay, Bernard J C, Parikh, Urvi M, Heaps, Amy, Coughenour, Lindsay, Schwartz, Marc B, Dueker, Jeffrey M, Silveira, Fernanda P, Keebler, Mary E, Humar, Abhinav, Luketich, James D, Morrell, Matthew R, Pilewski, Joseph M, McDyer, John F, Pappu, Bhanu, Ferris, Robert L, Marks, Stanley M, Mahon, John, Mulvey, Katie, Hariharan, Sundaram, Updike, Glenn M, Brock, Lorraine, Edwards, Robert, Beigi, Richard H, Kip, Paula L, Wells, Alan, Minnier, Tami, Angus, Derek C, Mellors, John W

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Reduced histone deacetylase 7 activity restores function to misfolded CFTR in cystic fibrosis von Balch, William E, Hutt, Darren M, Herman, David, Rodrigues, Ana P C, Noel, Sabrina, Pilewski, Joseph M, Matteson, Jeanne, Hoch, Ben, Kellner, Wendy, Kelly, Jeffery W, Schmidt, Andre, Thomas, Philip J, Matsumura, Yoshihiro, Skach, William R, Gentzsch, Martina, Riordan, John R, Sorscher, Eric J, Okiyoneda, Tsukasa, Yates, John R, Lukacs, Gergely L, Frizzell, Raymond A, Manning, Gerard, Gottesfeld, Joel M

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Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation von Clancy, J P, Rowe, Steven M, Accurso, Frank J, Aitken, Moira L, Amin, Raouf S, Ashlock, Melissa A, Ballmann, Manfred, Boyle, Michael P, Bronsveld, Inez, Campbell, Preston W, De Boeck, Kris, Donaldson, Scott H, Dorkin, Henry L, Dunitz, Jordan M, Durie, Peter R, Jain, Manu, Leonard, Anissa, McCoy, Karen S, Moss, Richard B, Pilewski, Joseph M, Rosenbluth, Daniel B, Rubenstein, Ronald C, Schechter, Michael S, Botfield, Martyn, Ordoñez, Claudia L, Spencer-Green, George T, Vernillet, Laurent, Wisseh, Steve, Yen, Karl, Konstan, Michael W

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Autoantibodies in Patients with Chronic Obstructive Pulmonary Disease von Feghali-Bostwick, Carol A, Gadgil, Aneal S, Otterbein, Leo E, Pilewski, Joseph M, Stoner, Michael W, Csizmadia, Eva, Zhang, Yingze, Sciurba, Frank C, Duncan, Steven R

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Routine deep vein thrombosis screening after lung transplantation: Incidence and risk factors von Jorge, Ahmed, Sanchez, Pablo G., Hayanga, J.W. Awori, Pilewski, Joseph M., Morrell, Mathew, Tuft, Marie, Ryan, John, D'Cunha, Jonathan

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A physiologically-motivated compartment-based model of the effect of inhaled hypertonic saline on mucociliary clearance and liquid transport in cystic fibrosis von Markovetz, Matthew R, Corcoran, Timothy E, Locke, Landon W, Myerburg, Michael M, Pilewski, Joseph M, Parker, Robert S

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Comprehensive Gene Expression Profiles Reveal Pathways Related to the Pathogenesis of Chronic Obstructive Pulmonary Disease von Ning, Wen, Li, Chao-Jun, Kaminski, Naftali, Feghali-Bostwick, Carol A., Alber, Sean M., Di, Yuanpu P., Otterbein, Sherrie L., Song, Ruiping, Hayashi, Shizu, Zhou, Zhihong, Pinsky, David J., Watkins, Simon C., Pilewski, Joseph M., Sciurba, Frank C., Peters, David G., Hogg, James C., Augustine M. K. Choi, Vogelstein, Bert

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VX-659–Tezacaftor–Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles von Davies, Jane C, Moskowitz, Samuel M, Brown, Cynthia, Horsley, Alexander, Mall, Marcus A, McKone, Edward F, Plant, Barry J, Prais, Dario, Ramsey, Bonnie W, Taylor-Cousar, Jennifer L, Tullis, Elizabeth, Uluer, Ahmet, McKee, Charlotte M, Robertson, Sarah, Shilling, Rebecca A, Simard, Christopher, Van Goor, Fredrick, Waltz, David, Xuan, Fengjuan, Young, Tim, Rowe, Steven M

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Cellular and Humoral Autoreactivity in Idiopathic Pulmonary Fibrosis von Feghali-Bostwick, Carol A, Tsai, Christopher G, Valentine, Vincent G, Kantrow, Stephen, Stoner, Michael W, Pilewski, Joseph M, Gadgil, Aneal, George, M. Patricia, Gibson, Kevin F, Choi, Augustine M. K, Kaminski, Naftali, Zhang, Yingze, Duncan, Steven R

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Safety and early treatment effects of the CXCR2 antagonist SB-656933 in patients with cystic fibrosis von Moss, Richard B, Mistry, Sunil J, Konstan, Michael W, Pilewski, Joseph M, Kerem, Eitan, Tal-Singer, Ruth, Lazaar, Aili L

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Advancing the pipeline of cystic fibrosis clinical trials: a new roadmap with a global trial network perspective von Mayer-Hamblett, Nicole, Clancy, John Paul, Jain, Raksha, Donaldson, Scott H, Fajac, Isabelle, Goss, Christopher H, Polineni, Deepika, Ratjen, Felix, Quon, Bradley S, Zemanick, Edith T, Bell, Scott C, Davies, Jane C, Jain, Manu, Konstan, Michael W, Kerper, Natanya R, LaRosa, Tré, Mall, Marcus A, McKone, Edward, Pearson, Kelsie, Pilewski, Joseph M, Quittell, Lynne, Rayment, Jonathan H, Rowe, Steven M, Taylor-Cousar, Jennifer L, Retsch-Bogart, George, Downey, Damian G

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Overnight delivery of hypertonic saline by nasal cannula aerosol for cystic fibrosis von Corcoran, Timothy E., Godovchik, Joseph E., Donn, Karl H., Busick, David R., Goralski, Jennifer, Locke, Landon W., Markovetz, Matthew R., Myerburg, Michael M., Muthukrishnan, Ashok, Weber, Lawrence, Lacy, Ryan T., Pilewski, Joseph M.

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Clinical mechanism of the cystic fibrosis transmembrane conductance regulator potentiator ivacaftor in G551D-mediated cystic fibrosis von Rowe, Steven M, Heltshe, Sonya L, Gonska, Tanja, Donaldson, Scott H, Borowitz, Drucy, Gelfond, Daniel, Sagel, Scott D, Khan, Umer, Mayer-Hamblett, Nicole, Van Dalfsen, Jill M, Joseloff, Elizabeth, Ramsey, Bonnie W

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A CFTR Potentiator in Patients with Cystic Fibrosis and the G551D Mutation von Ramsey, Bonnie W, Davies, Jane, McElvaney, N. Gerard, Tullis, Elizabeth, Bell, Scott C, Dřevínek, Pavel, Griese, Matthias, McKone, Edward F, Wainwright, Claire E, Konstan, Michael W, Moss, Richard, Ratjen, Felix, Sermet-Gaudelus, Isabelle, Rowe, Steven M, Dong, Qunming, Rodriguez, Sally, Yen, Karl, Ordoñez, Claudia, Elborn, J. Stuart

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Ataluren for the treatment of nonsense-mutation cystic fibrosis: a randomised, double-blind, placebo-controlled phase 3 trial von Kerem, Eitan, MD, Konstan, Michael W, Dr, De Boeck, Kris, MD, Accurso, Frank J, MD, Sermet-Gaudelus, Isabelle, MD, Wilschanski, Michael, MD, Elborn, J Stuart, MD, Melotti, Paola, MD, Bronsveld, Inez, MD, Fajac, Isabelle, MD, Malfroot, Anne, MD, Rosenbluth, Daniel B, MD, Walker, Patricia A, MD, McColley, Susanna A, MD, Knoop, Christiane, MD, Quattrucci, Serena, MD, Rietschel, Ernst, MD, Zeitlin, Pamela L, MD, Barth, Jay, MD, Elfring, Gary L, MS, Welch, Ellen M, PhD, Branstrom, Arthur, PhD, Spiegel, Robert J, MD, Peltz, Stuart W, PhD, Ajayi, Temitayo, MD, Rowe, Steven M, MD

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Effect of ivacaftor on mucociliary clearance and clinical outcomes in cystic fibrosis patients with G551D-CFTR von Donaldson, Scott H, Laube, Beth L, Corcoran, Timothy E, Bhambhvani, Pradeep, Zeman, Kirby, Ceppe, Agathe, Zeitlin, Pamela L, Mogayzel, Jr, Peter J, Boyle, Michael, Locke, Landon W, Myerburg, Michael M, Pilewski, Joseph M, Flanagan, Brian, Rowe, Steven M, Bennett, William D

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Pseudomonas infection and mucociliary and absorptive clearance in the cystic fibrosis lung von Locke, Landon W, Myerburg, Michael M, Weiner, Daniel J, Markovetz, Matthew R, Parker, Robert S, Muthukrishnan, Ashok, Weber, Lawrence, Czachowski, Michael R, Lacy, Ryan T, Pilewski, Joseph M, Corcoran, Timothy E

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