Molecular characterization of methicillin-resistant Staphylococcus aureus from a fatal case of necrotizing fasciitis in an extremely low-birth-weight infant von Orii, K.O., Iwao, Y., Higuchi, W., Takano, T., Yamamoto, T.

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Effect of ‘attenuated' mutations in mucopolysaccharidosis IVA on molecular phenotypes of N-acetylgalactosamine-6-sulfate sulfatase von Montaño, A. M, Sukegawa, K, Kato, Z, Carrozzo, R, Di Natale, P, Christensen, E, Orii, K. O, Orii, T, Kondo, N, Tomatsu, S

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Mucopolysaccharidosis IVA: identification of mutations and methylation study in GALNS gene von Tomatsu, S, Nishioka, T, Montaño, A M, Gutierrez, M A, Pena, O S, Orii, K O, Sly, W S, Yamaguchi, S, Orii, T, Paschke, E, Kircher, S G, Noguchi, A

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Keratan sulphate levels in mucopolysaccharidoses and mucolipidoses von Tomatsu, S., Okamura, K., Maeda, H., Taketani, T., Castrillon, S. V., Gutierrez, M. A., Nishioka, T., Fachel, A. A., Orii, K. O., Grubb, J. H., Cooper, A., Thornley, M., Wraith, E., Barrera, L. A., Laybauer, L. S., Giugliani, R., Schwartz, I. V., Frenking, G. Schulze, Beck, M., Kircher, S. G., Paschke, E., Yamaguchi, S., Ullrich, K., Haskins, M., Isogai, K., Suzuki, Y., Orii, T., Kondo, N., Creer, M., Okuyama, T., Tanaka, A., Noguchi, A.

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Association between SEN Virus Infection and Hepatitis C in Japan von Umemura, Takeji, Alter, Harvey J., Tanaka, Eiji, Yeo, Anthony E. T., Shih, J. Wai-Kuo, Orii, Koji, Matsumoto, Akihiro, Yoshizawa, Kaname, Kiyosawa, Kendo

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Myopathic form of very-long chain acyl-CoA dehydrogenase deficiency : Evidence for temperature-sensitive mild mutations in both mutant alleles in a Japanese girl von FUKAO, Toshiyuki, WATANABE, Hiroh, ORII, Kenji E, TAKAHASHI, Yukitoshi, HIRANO, Akiko, KONDO, Tomio, YAMAGUCHI, Seiji, AOYAMA, Toshifumi, KONDO, Naomi

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Mitochondrial trifunctional protein deficiency associated with recurrent myoglobinuria in adolescence von MIYAJIMA, H, ORII, K. E, SHINDO, Y, HASHIMOTO, T, SHINKA, T, KUHARA, T, MATSUMOTO, I, SHIMIZU, H, KANEKO, E

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New wireless thermometer for RF and microwave thermal therapy using an MMIC in an Si BJT VCO type von Kotsuka, Y., Orii, K., Kojima, H., Tanaka, M.

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Mutation analysis of very-long-chain acyl-coenzyme A dehydrogenase (VLCAD) deficiency : Identification and characterization of mutant VLCAD cDNAs from four patients von SOURI, M, AOYAMA, T, ORII, K, YAMAGUCHI, S, HASHIMOTO, T

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Formation of the Enzyme Complex in Mitochondria Is Required for Function of Trifunctional β-Oxidation Protein von Orii, Kenji E., Aoyama, Toshifumi, Souri, Masayoshi, Jiang, Ling Ling, Orii, Koji O., Hayashi, Shuhei, Yamaguchi, Seiji, Kondo, Naomi, Orii, Tadao, Hashimoto, Takashi

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Succinyl-CoA:3-Ketoacid CoA Transferase (SCOT): Cloning of the Human SCOT Gene, Tertiary Structural Modeling of the Human SCOT Monomer, and Characterization of Three Pathogenic Mut... von Fukao, Toshiyuki, Mitchell, Grant A., Song, Xiang-Qian, Nakamura, Haruki, Kassovska-Bratinova, Sacha, Orii, Kenji E., Wraith, James E., Besley, Guy, Wanders, Ronald J.A., Niezen-Koning, Klary E., Berry, Gerard T., Palmieri, Michael, Kondo, Naomi

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BLM (the Causative Gene of Bloom Syndrome) Protein Translocation into the Nucleus by a Nuclear Localization Signal von Kaneko, Hideo, Orii, Koji O, Matsui, Eiko, Shimozawa, Nobuyuki, Fukao, Toshiyuki, Matsumoto, Takehisa, Shimamoto, Akira, Furuichi, Yasuhiro, Hayakawa, Seiro, Kasahara, Kimiko, Kondo, Naomi

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Molecular basis of very long chain acyl-CoA dehydrogenase deficiency in three Israeli patients: Identification of a complex mutant allele with P65L and K247Q mutations, the former... von Watanabe, Hiroh, Orii, Kenji E., Fukao, Toshiyuki, Song, Xiang-Qian, Aoyama, Toshifumi, IJlst, Lodewijk, Ruiter, Jos, Wanders, Ronald J.A., Kondo, Naomi

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Assignment of the human mitochondrial very-long-chain acyl-CoA dehydrogenase gene (LCACD) to 17p13 by in situ hybridization von AOYAMA, T, WAKUI, K, FUKUSHIMA, Y, ORII, K. O, HASHIMOTO, T

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The mouse N-acetylgalactosamine-6-sulfate sulfatase ( Galns) gene: cDNA isolation, genomic characterization, chromosomal assignment and analysis of the 5′-flanking region von Montaño, Adriana Maria, Yamagishi, Atsushi, Tomatsu, Shunji, Fukuda, Seiji, Copeland, Neal G., Orii, Kenji E., Isogai, Koji, Yamada, Naoto, Kato, Zen-Ichiro, Jenkins, Nancy A., Gilbert, Debra J., Sukegawa, Kazuko, Orii, Tadao, Kondo, Naomi

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Splenic artery aneurysm of the anomalous splenomesenteric trunk: successful treatment by transcatheter embolization using detachable coils von Sato, Motohiro, Anno, Izumi, Yamaguchi, Masayuki, Iida, Hiroyuki, Orii, Kazuo

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Development of MPS IVA mouse (Galnstm(hC79S·mC76S)slu) tolerant to human N-acetylgalactosamine-6-sulfate sulfatase von Tomatsu, Shunji, Gutierrez, Monica, Nishioka, Tatsuo, Yamada, Masamichi, Yamada, Mana, Tosaka, Yasuhiro, Grubb, Jeffrey H., Montaño, Adriana M., Vieira, Matheus B., Trandafirescu, Georgeta G., Peña, Olga M., Yamaguchi, Seiji, Orii, Koji O., Orii, Tadao, Noguchi, Akihiko, Laybauer, Leticia

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Severe sinoatrial dysfunction after esophageal surgery: a case report von Takahashi, S, Mizutani, T, Watanabe, M, Iida, H, Orii, K, Toyooka, H

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Defining the Pathway for Tat-mediated Delivery of β-Glucuronidase in Cultured Cells and MPS VII Mice von Orii, Koji O, Grubb, Jeffrey H, Vogler, Carole, Levy, Beth, Tan, Yun, Markova, Kamelia, Davidson, Beverly L, Mao, Q, Orii, Tadao, Kondo, Naomi, Sly, William S

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Molecular characterization of the mouse very-long-chain acyl-CoA dehydrogenase gene von Orii, K O, Aoyama, T, Saito-Ohara, F, Ikeuchi, T, Orii, T, Kondo, N, Hashimoto, T

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