Every CFTR variant counts – Target-capture based next-generation-sequencing for molecular diagnosis in the German CF Registry von Ahting, Simone, Nährlich, Lutz, Held, Inka, Henn, Constance, Krill, Angelika, Landwehr, Kerstin, Meister, Jochen, Nährig, Susanne, Nolde, Anna, Remke, Katharina, Ruppel, Renate, Sauer-Heilborn, Annette, Schebek, Martin, Schopper, Gudrun, Schulte-Hubbert, Bernhard, Schwarz, Carsten, Smaczny, Christina, Wege, Sabine, Hentschel, Julia

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COVID-19 vaccine prioritisation for people with cystic fibrosis von Carr, Siobhán B, Cosgriff, Rebecca, Harutyunyan, Satenik, Middleton, Peter G, Ruseckaite, Rasa, Ahern, Susannah, Daneau, Géraldine, Filho, Luiz Vicente R F da Silva, Stephenson, Anne L, Cheng, Stephanie Y, Melo, Joel, Corvol, Harriet, Burgel, Pierre-Régis, Nährlich, Lutz, McKone, Edward, Colombo, Carla, Salvatore, Marco, Padoan, Rita, Abdrakhmanov, Olzhas, Gulmans, Vincent, Byrnes, Catherine A, Amelina, Elena, Kondratyeva, Elena, Zhekayte, Elena, Kashirskaya, Nataliya, Zampoli, Marco, Pastor-Vivero, M Dolores, Mondejar-Lopez, Pedro, de Monestrol, Isabelle, Jung, Andeas, McClenaghan, Elliot, Brownlee, Keith, Rizvi, Samar, Goss, Christopher H, Elbert, Alexander, Faro, Albert, Gutierrez, Hector, Marshall, Bruce C

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Randomized controlled phase 2 trial of hydroxychloroquine in childhood interstitial lung disease von Griese, Matthias, Kappler, Matthias, Stehling, Florian, Schulze, Johannes, Baden, Winfried, Koerner-Rettberg, Cordula, Carlens, Julia, Prenzel, Freerk, Nährlich, Lutz, Thalmeier, Andreas, Sebah, Daniela, Kronfeld, Kai, Rock, Hans, Ruckes, Christian, Wetzke, Martin, Seidl, Elias, Schwerk, Nicolaus

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Genotype-epigenotype-phenotype correlations in females with frontometaphyseal dysplasia von Zenker, Martin, Nährlich, Lutz, Sticht, Heinrich, Reis, André, Horn, Denise

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Dynamics of abdominal symptoms during the start of a new therapy with elexacaftor/tezacaftor/ivacaftor using the novel CFAbd-day2day questionnaire von Mainz, Jochen G., Barucha, Anton, Huang, Pu, Bechinger, Lilith, Duckstein, Franziska, Polte, Louise, Sadrieh, Pauline, Nährlich, Lutz, Eickmeier, Olaf, Van Dullemen, Suzanne, Eschenhagen, Patience, Schwarz, Carsten, Lüth, Stefan, Zagoya, Carlos, Graepler-Mainka, Ute

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Vergleich von Diagnosedaten nach der Einführung des Mukoviszidosescreenings bei Neugeborenen in Deutschland von Nährlich, Lutz, Brockow, Inken

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Molecular Epidemiology of Mycobacterium abscessus Isolates Recovered from German Cystic Fibrosis Patients von Wetzstein, Nils, Diricks, Margo, Kohl, Thomas A., Wichelhaus, Thomas A., Andres, Sönke, Paulowski, Laura, Schwarz, Carsten, Lewin, Astrid, Kehrmann, Jan, Kahl, Barbara C., Dichtl, Karl, Hügel, Christian, Eickmeier, Olaf, Smaczny, Christina, Schmidt, Annika, Zimmermann, Stefan, Nährlich, Lutz, Hafkemeyer, Sylvia, Niemann, Stefan, Maurer, Florian P., Hogardt, Michael

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Vergleich von Diagnosedaten nach der Einführung des Mukoviszidosescreenings bei Neugeborenen in Deutschland von Nährlich, Lutz, Brockow, Inken

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Long-Term Inhaled Dry Powder Mannitol in Cystic Fibrosis: An International Randomized Study von AITKEN, Moira L, BELLON, Gabriel, ZUCKERMAN, Jonathan B, CHARLTON, Brett, DE BOECK, Kris, FLUME, Patrick A, FOX, Howard G, GELLER, David E, HAARMAN, Eric G, HEBESTREIT, Helge U, LAPEY, Allen, MANJULA SCHOU, I

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Therapy of CF-Patients with Amitriptyline and Placebo - a Randomised, Double-Blind, Placebo-Controlled Phase IIb Multicenter, Cohort-Study von Nährlich, Lutz, Mainz, Jochen G., Adams, Constantin, Engel, Corinna, Herrmann, Gloria, Icheva, Vanya, Lauer, Josefine, Deppisch, Caroline, Wirth, Andreas, Unger, Katy, Graepler-Mainka, Ute, Hector, Andreas, Heyder, Susanne, Stern, Martin, Döring, Gerd, Gulbins, Erich, Riethmüller, Joachim

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Altered protease and antiprotease balance during a COPD exacerbation contributes to mucus obstruction von Chillappagari, Shashi, Preuss, Jenni, Licht, Sebastian, Müller, Christian, Mahavadi, Poornima, Sarode, Gaurav, Vogelmeier, Claus, Guenther, Andreas, Nahrlich, Lutz, Rubin, Bruce K, Henke, Markus O

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Comparison of diagnostic data after introduction of cystic fibrosis screening in newborns in Germany von Nährlich, Lutz, Brockow, Inken

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TIMP-1/-2 and transient elastography allow non invasive diagnosis of cystic fibrosis associated liver disease von Rath, Timo, Menendez, Katrin Menendez, Kügler, Marion, Hage, Lisa, Wenzel, Christian, Schulz, Richard, Graf, Jürgen, Nährlich, Lutz, Roeb, Elke, Roderfeld, Martin

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Impact of the A (H1N1) pandemic influenza (season 2009–2010) on patients with cystic fibrosis von Viviani, Laura, Assael, Baroukh M, Kerem, Eitan

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Preventive Inhalation of Hypertonic Saline in Infants with Cystic Fibrosis (PRESIS). A Randomized, Double-Blind, Controlled Study von Stahl, Mirjam, Wielpütz, Mark O, Ricklefs, Isabell, Dopfer, Christian, Barth, Sandra, Schlegtendal, Anne, Graeber, Simon Y, Sommerburg, Olaf, Diekmann, Gesa, Hüsing, Johannes, Koerner-Rettberg, Cordula, Nährlich, Lutz, Dittrich, Anna-Maria, Kopp, Matthias V, Mall, Marcus A

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Lung transplantation for end-stage cystic fibrosis before and after the availability of elexacaftor-tezacaftor-ivacaftor, Germany, 2012-2021 von Ringshausen, Felix C, Sauer-Heilborn, Annette, Büttner, Tina, Dittrich, Anna-Maria, Schwerk, Nicolaus, Ius, Fabio, Nährlich, Lutz, Welte, Tobias, Greer, Mark

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A multinational report to characterise SARS-CoV-2 infection in people with cystic fibrosis von Cosgriff, Rebecca, Ahern, Susannah, Bell, Scott C., Brownlee, Keith, Burgel, Pierre-Régis, Byrnes, Cass, Corvol, Harriet, Cheng, Stephanie Y., Elbert, Alexander, Faro, Albert, Goss, Christopher H., Gulmans, Vincent, Marshall, Bruce C., McKone, Edward, Middleton, Peter G., Ruseckaite, Rasa, Stephenson, Anne L., Carr, Siobhán B, Reid, David, Wark, Peter, Daneau, Géraldine, Boussaud, Véronique, Brinchault, Graziella, Coirier-Duet, Emmanuelle, Dubus, Jean-Christophe, Grenet, Dominique, Miranda, Sandra de, Beaumont, Laurence, Kanaan, Reem, Lauraens, Muriel, Martin, Clémence, Mittaine, Marie, Prévotat, Anne, Reynaud-Gaubert, Martine, Sermet-Gaudelus, Isabelle, Tatopoulos, Aurelie, Nährlich, Lutz, Plant, Barry, Gunaratnam, Cedric, Jackson, Abaigeal, Groot, Karin M. de Winter-de, Luijk, Bart, Wesseling, Geertjan, Allenby, Mark, Duckers, Jamie, Gunn, Elaine, Jones, Andrew, Ketchell, Robert Ian, Madge, Susan L., Maitra, Anirban, Mujtaba, Ghulam, Rodgers, Helen, Shafi, Nadia, Simmonds, Nicholas, Southern, Kevin, Watson, Danie, Rizvi, Samar, Seguin, Julie, Garbarz, Janet, Rosamilia, Kristen, Berdella, Maria, Nick, Jerry A., Belkin, Richard, Gilmore, Diana, McBennett, Kim, Padoan, Rita, Salvatore, Marco

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Multicentre standardisation of chest MRI as radiation-free outcome measure of lung disease in young children with cystic fibrosis von Wielpütz, Mark O., von Stackelberg, Oyunbileg, Stahl, Mirjam, Jobst, Bertram J., Eichinger, Monika, Puderbach, Michael U., Nährlich, Lutz, Barth, Sandra, Schneider, Christian, Kopp, Matthias V., Ricklefs, Isabell, Buchholz, Michael, Tümmler, Burkhard, Dopfer, Christian, Vogel-Claussen, Jens, Kauczor, Hans-Ulrich, Mall, Marcus A.

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Increased frequency of the restless legs syndrome in adults with cystic fibrosis von Jurisch, Peter, Gall, Henning, Richter, Manuel Jonas, Seeger, Werner, Nährlich, Lutz, Völkel, Sebastian, Hirche, Tim Oliver, Schulz, Richard

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Persistent tachypnea of infancy: Follow up at school age von Seidl, Elias, Carlens, Julia, Schwerk, Nicolaus, Wetzke, Martin, Marczak, Honorata, Lange, Joanna, Krenke, Katarzyna, Mayell, Sarah J., Escribano, Amparo, Seidenberg, Jürgen, Ahrens, Frank, Hebestreit, Helge, Nährlich, Lutz, Sismanlar, Tugba, Aslan, Ayse T., Snijders, Deborah, Ullmann, Nicola, Kappler, Matthias, Griese, Matthias

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