WS18.4 Intestinal current measurement as outcome marker for clinical trials: the ECFS CTN certification process and central reading core facility von Scheinert, S, de Jonge, H, Bronsveld, I, Nahrlich, L, Melotti, P, van Koningsbruggen-Rietschel, S, Sermet-Gaudelus, I, Hayes, K, Derichs, N

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Real life practice of sweat testing in Europe von Cirilli, N., Southern, K.W., Buzzetti, R., Barben, J., Nährlich, L., Munck, A., Wilschanski, M., De Boeck, K., Derichs, N.

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Reply to the letter Regarding the article entitled “Standards for the care of people with CF: a timely and accurate diagnosis” von Castellani, C, Raraigh, K, Nährlich, L, Sermet-Gaudelus, I, Simmonds, NJ

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414 Demographic and clinical aspects of cystic fibrosis-related diabetes (CFRD) – a registry comparison between the European CF Society Patient Registry (ECFSPR) and the German/Aus... von Prinz, N, Zolin, A, Konrad, K, Nährlich, L, Laubner, K, Olesen, H.V, Bauer, M, Jung, A, Frischer, T, Holl, R.W

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WS11.4 Real life practice of sweat testing in Europe: results from an ECFS-wide survey von Cirilli, N, Buzzetti, R, Southern, K.W, Barben, J, Nährlich, L, Munck, A, Wilschanski, M, De Boeck, K, Derichs, N

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Mukoviszidose – wenn die Diagnose unsicher bleibt von Hammermann, J., Ballmann, M., Bend, J., Nährlich, L., Nüßlein, T., Schmidt, S., Smrekar, U., Sommerburg, O., Ellemunter, H.

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P319 Effects of elexacaftor/tezacaftor/ivacaftor (ETI) on nutrition parameters and resting energy expenditure (REE) in people with cystic fibrosis (pwCF) von Sasse, L., Simon, A., Rückes-Nilges, C., Nährlich, L.

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Monitoring of omalizumab therapy in children and adolescents von Steiß, J O, Schmidt, A, Lindemann, H, Rudloff, S, Staatz, A, Strohner, P, Becher, G, Nährlich, L, Zimmer, K P

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P277 The novel CFAbd-Score.kid reveals a significant decline in abdominal symptoms in children with cystic fibrosis aged 6-<12 years on a new therapy with elexacaftor/tezacaftor/iv... von Mainz, J.G., Zagoya, C., Bechinger, L., Duckstein, F., Barucha, A., Polte, L., Nährlich, L., Simon, A., Eickmeier, O., van Dullemen, S., Graepler-Mainka, U., Sadrieh, P.

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Genotype-epigenotype-phenotype correlations in females with frontometaphyseal dysplasia von Zenker, Martin, Nährlich, Lutz, Sticht, Heinrich, Reis, André, Horn, Denise

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P210 COACH project - screening for psychological comorbidity in adolescents with cystic fibrosis von Temming, S., Thalemann, R., Andert, M., Nährlich, L., Baumeister, H., Mall, M., Staab, D.

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WS04.04 Development and validation of the CFAbd-Score.kid, a novel gastrointestinal patient-reported outcome measure specific for children with cystic fibrosis von Sadrieh, P., Bechinger, L., Duckstein, F., Barucha, A., Nährlich, L., Simon, A., Eickmeier, O., Dullemen, S. van, Kemp, D., Mühl, B., Eschenhagen, P., Schwarz, C., Graepler-Mainka, U., Zagoya, C., Mainz, J.G.

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ePS2.08 Risk factors for cystic fibrosis arthropathy: data from the National German Cystic Fibrosis Patient Registry von Grehn, C., Dittrich, A.-M., Wosniok, J., Nährlich, L., Schwarz, C.

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International management platform for children’s interstitial lung disease (chILD-EU) von Griese, Matthias, Seidl, Elias, Hengst, Meike, Reu, Simone, Rock, Hans, Anthony, Gisela, Kiper, Nural, Emiralioğlu, Nagehan, Snijders, Deborah, Goldbeck, Lutz, Leidl, Reiner, Ley-Zaporozhan, Julia, Krüger-Stollfuss, Ingrid, Kammer, Birgit, Wesselak, Traudl, Eismann, Claudia, Schams, Andrea, Neuner, Doerthe, MacLean, Morag, Nicholson, Andrew G, Lauren, McCann, Clement, Annick, Epaud, Ralph, de Blic, Jacques, Ashworth, Michael, Aurora, Paul, Calder, Alistair, Wetzke, Martin, Kappler, Matthias, Cunningham, Steve, Schwerk, Nicolaus, Bush, Andy

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P299 Assessing dynamics of abdominal symptoms during a new therapy with elexacaftor/tezacaftor/ivacaftor using the new CFAbd-day2day© questionnaire von Mainz, J.G., Barucha, A., Huang, P., Bechinger, L., Duckstein, F., Polte, L., Nährlich, L., Eickmeier, O., van Dullemen, S., Eschenhagen, P., Sadrieh, P., Schwarz, C., Lüth, S., Zagoya, C., Graepler-Mainka, U.

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Persistent Tachypnea of Infancy. Usual and Aberrant von Rauch, Daniela, Wetzke, Martin, Reu, Simone, Wesselak, Waltraud, Schams, Andrea, Hengst, Meike, Kammer, Birgit, Ley-Zaporozhan, Julia, Kappler, Matthias, Proesmans, Marijke, Lange, Joanna, Escribano, Amparo, Kerem, Eitan, Ahrens, Frank, Brasch, Frank, Schwerk, Nicolaus, Griese, Matthias

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CF quality assurance in Germany: MUKO.dok as a specific database developed for analysis and out-patient clinic management von Schlangen, M, Bergmann, I, Fischer, R, Nährlich, L, Smaczny, C, Wenzlaff, P, Wiedemann, B, Müller, M

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Balanced translocation t(4q; 10q) in infantile spinal muscular atrophy von Hofner, G, Nährlich, L, Lauffer, H

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P083 Clinical progression of SARS-CoV-2 infection in people with cystic fibrosis: a global observational study von McClenaghan, E., Cosgriff, R., Brownlee, K., Ahern, S., Burgel, P.-R., Byrnes, C.A., Colombo, C., Corvol, H., Cheng, S.Y., Daneau, G., Elbert, A., Faro, A., Goss, C.H., Gulmans, V., Gutierrez, H., de Monestrol, I., Jung, A., Nährlich, L., Kashirskaya, N., Marshall, B.C., McKone, E., Middleton, P.G., Mondejar-Lopez, P., Pastor-Vivero, M.D., Padoan, R., Rizvi, S., Ruseckaite, R., Salvatore, M., Stephenson, A.L., da Silva Filho, L.V.R., Melo, J., Zampoli, M., Abdrakhmanov, O., Harutyunyan, S., Carr, S.B.

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Mukoviszidose – wenn die Diagnose unsicher bleibt von Hammermann, J., Ballmann, M., Bend, J., Nährlich, L., Nüßlein, T., Schmidt, S., Smrekar, U., Sommerburg, O., Ellemunter, H.

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