Fibroadipogenic progenitors are responsible for muscle loss in limb girdle muscular dystrophy 2B von Hogarth, Marshall W., Defour, Aurelia, Lazarski, Christopher, Gallardo, Eduard, Diaz Manera, Jordi, Partridge, Terence A., Nagaraju, Kanneboyina, Jaiswal, Jyoti K.

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Risk factors and disease mechanisms in myositis von Miller, Frederick W., Lamb, Janine A., Schmidt, Jens, Nagaraju, Kanneboyina

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Behavioral and locomotor measurements using an open field activity monitoring system for skeletal muscle diseases von Tatem, Kathleen S, Quinn, James L, Phadke, Aditi, Yu, Qing, Gordish-Dressman, Heather, Nagaraju, Kanneboyina

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Towards developing standard operating procedures for pre-clinical testing in the mdx mouse model of Duchenne muscular dystrophy von Grounds, Miranda D, Radley, Hannah G, Lynch, Gordon S, Nagaraju, Kanneboyina, De Luca, Annamaria

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Asynchronous remodeling is a driver of failed regeneration in Duchenne muscular dystrophy von Dadgar, Sherry, Wang, Zuyi, Johnston, Helen, Kesari, Akanchha, Nagaraju, Kanneboyina, Chen, Yi-Wen, Hill, D Ashley, Partridge, Terence A, Giri, Mamta, Freishtat, Robert J, Nazarian, Javad, Xuan, Jianhua, Wang, Yue, Hoffman, Eric P

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Bodywide skipping of exons 45–55 in dystrophic mdx52 mice by systemic antisense delivery von Aoki, Yoshitsugu, Yokota, Toshifumi, Nagata, Tetsuya, Nakamura, Akinori, Tanihata, Jun, Saito, Takashi, Duguez, Stephanie M. R, Nagaraju, Kanneboyina, Hoffman, Eric P, Partridge, Terence, Takeda, Shin'ichi

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Secreted acid sphingomyelinase as a potential gene therapy for limb girdle muscular dystrophy 2B von Bittel, Daniel C, Sreetama, Sen Chandra, Chandra, Goutam, Ziegler, Robin, Nagaraju, Kanneboyina, Van der Meulen, Jack H, Jaiswal, Jyoti K

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Muscle Weakness in Myositis: MicroRNA‐Mediated Dystrophin Reduction in a Myositis Mouse Model and Human Muscle Biopsies von Kinder, Travis B., Heier, Christopher R., Tully, Christopher B., Van der Muelen, Jack H., Hoffman, Eric P., Nagaraju, Kanneboyina, Fiorillo, Alyson A.

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Endoplasmic Reticulum Stress in Skeletal Muscle Homeostasis and Disease von Rayavarapu, Sree, Coley, William, Nagaraju, Kanneboyina

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Discovery of serum protein biomarkers in the mdx mouse model and cross-species comparison to Duchenne muscular dystrophy patients von Hathout, Yetrib, Marathi, Ramya L, Rayavarapu, Sree, Zhang, Aiping, Brown, Kristy J, Seol, Haeri, Gordish-Dressman, Heather, Cirak, Sebahattin, Bello, Luca, Nagaraju, Kanneboyina, Partridge, Terry, Hoffman, Eric P, Takeda, Shin'ichi, Mah, Jean K, Henricson, Erik, McDonald, Craig

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Quantitative Antisense Screening and Optimization for Exon 51 Skipping in Duchenne Muscular Dystrophy von Echigoya, Yusuke, Lim, Kenji Rowel Q., Trieu, Nhu, Bao, Bo, Miskew Nichols, Bailey, Vila, Maria Candida, Novak, James S., Hara, Yuko, Lee, Joshua, Touznik, Aleksander, Mamchaoui, Kamel, Aoki, Yoshitsugu, Takeda, Shin’ichi, Nagaraju, Kanneboyina, Mouly, Vincent, Maruyama, Rika, Duddy, William, Yokota, Toshifumi

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Biomarker-focused multi-drug combination therapy and repurposing trial in mdx mice von Ziemba, Michael, Barkhouse, Molly, Uaesoontrachoon, Kitipong, Giri, Mamta, Hathout, Yetrib, Dang, Utkarsh J, Gordish-Dressman, Heather, Nagaraju, Kanneboyina, Hoffman, Eric P

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A mouse model of inherited choline kinase β-deficiency presents with specific cardiac abnormalities and a predisposition to arrhythmia von Tavasoli, Mahtab, Feridooni, Tiam, Feridooni, Hirad, Sokolenko, Stanislav, Mishra, Abhishek, Lefsay, Abir, Srinivassane, Sadish, Reid, Sarah Anne, Rowsell, Joyce, Praest, Molly, MacKinnon, Alexandra, Mammoliti, Melissa, Maloney, Ashley Alyssa, Moraca, Marina, Uaesoontrachoon, Kitipong, Nagaraju, Kanneboyina, Hoffman, Eric P., Pasumarthi, Kishore B.S., McMaster, Christopher R.

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Mechanism of action and therapeutic route for a muscular dystrophy caused by a genetic defect in lipid metabolism von Tavasoli, Mahtab, Lahire, Sarah, Sokolenko, Stanislav, Novorolsky, Robyn, Reid, Sarah Anne, Lefsay, Abir, Otley, Meredith O. C., Uaesoontrachoon, Kitipong, Rowsell, Joyce, Srinivassane, Sadish, Praest, Molly, MacKinnon, Alexandra, Mammoliti, Melissa Stella, Maloney, Ashley Alyssa, Moraca, Marina, Pedro Fernandez-Murray, J., McKenna, Meagan, Sinal, Christopher J., Nagaraju, Kanneboyina, Robertson, George S., Hoffman, Eric P., McMaster, Christopher R.

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Myoblasts and macrophages are required for therapeutic morpholino antisense oligonucleotide delivery to dystrophic muscle von Novak, James S., Hogarth, Marshall W., Boehler, Jessica F., Nearing, Marie, Vila, Maria C., Heredia, Raul, Fiorillo, Alyson A., Zhang, Aiping, Hathout, Yetrib, Hoffman, Eric P., Jaiswal, Jyoti K., Nagaraju, Kanneboyina, Cirak, Sebahattin, Partridge, Terence A.

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Effective rescue of dystrophin improves cardiac function in dystrophin-deficient mice by a modified morpholino oligomer von Wu, Bo, Moulton, Hong M, Iversen, Patrick L, Jiang, Jiangang, Li, Juan, Li, Jianbin, Spurney, Christopher F, Sali, Arpana, Guerron, Alfredo D, Nagaraju, Kanneboyina, Doran, Timothy, Lu, Peijuan, Xiao, Xiao, Lu, Qi Long

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Identification of Disease Specific Pathways Using in Vivo SILAC Proteomics in Dystrophin Deficient mdx Mouse von Rayavarapu, Sree, Coley, William, Cakir, Erdinc, Jahnke, Vanessa, Takeda, Shin'ichi, Aoki, Yoshitsugu, Grodish-Dressman, Heather, Jaiswal, Jyoti K., Hoffman, Eric P., Brown, Kristy J., Hathout, Yetrib, Nagaraju, Kanneboyina

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Enhanced autoantigen expression in regenerating muscle cells in idiopathic inflammatory myopathy von Casciola-Rosen, Livia, Nagaraju, Kanneboyina, Plotz, Paul, Wang, Kondi, Levine, Stuart, Gabrielson, Edward, Corse, Andrea, Rosen, Antony

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Suppression of autophagy permits successful enzyme replacement therapy in a lysosomal storage disorder-murine Pompe disease von Raben, Nina, Schreiner, Cynthia, Baum, Rebecca, Takikita, Shoichi, Xu, Sengen, Xie, Tao, Myerowitz, Rachel, Komatsu, Masaaki, Van Der Meulen, Jack H., Nagaraju, Kanneboyina, Ralston, Evelyn, Plotz, Paul H.

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Muscular dystrophy in the mdx mouse is a severe myopathy compounded by hypotrophy, hypertrophy and hyperplasia von Duddy, William, Duguez, Stephanie, Johnston, Helen, Cohen, Tatiana V, Phadke, Aditi, Gordish-Dressman, Heather, Nagaraju, Kanneboyina, Gnocchi, Viola, Low, SiewHui, Partridge, Terence

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