MG132‐induced progerin clearance is mediated by autophagy activation and splicing regulation von Harhouri, Karim, Navarro, Claire, Depetris, Danielle, Mattei, Marie‐Geneviève, Nissan, Xavier, Cau, Pierre, De Sandre‐Giovannoli, Annachiara, Lévy, Nicolas

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Vulnerability of progeroid smooth muscle cells to biomechanical forces is mediated by MMP13 von Pitrez, Patricia R., Estronca, Luís, Monteiro, Luís Miguel, Colell, Guillem, Vazão, Helena, Santinha, Deolinda, Harhouri, Karim, Thornton, Daniel, Navarro, Claire, Egesipe, Anne-Laure, Carvalho, Tânia, Dos Santos, Rodrigo L., Lévy, Nicolas, Smith, James C., de Magalhães, João Pedro, Ori, Alessandro, Bernardo, Andreia, De Sandre-Giovannoli, Annachiara, Nissan, Xavier, Rosell, Anna, Ferreira, Lino

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Combined treatment with statins and aminobisphosphonates extends longevity in a mouse model of human premature aging von Varela, Ignacio, Osorio, Fernando G, Cobo, Juan, Suárez, María F, Freije, José M P, López-Otín, Carlos, Pereira, Sandrine, Cadiñanos, Juan, Ugalde, Alejandro P, de Carlos, Félix, Navarro, Claire L, Foray, Nicolas, Cau, Pierre, Lévy, Nicolas

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Molecular bases of progeroid syndromes von Navarro, Claire L., Cau, Pierre, Lévy, Nicolas

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Nuclear matrix, nuclear envelope and premature aging syndromes in a translational research perspective von Cau, Pierre, Navarro, Claire, Harhouri, Karim, Roll, Patrice, Sigaudy, Sabine, Kaspi, Elise, Perrin, Sophie, De Sandre-Giovannoli, Annachiara, Lévy, Nicolas

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Random walk with restart on multiplex and heterogeneous biological networks von Valdeolivas, Alberto, Tichit, Laurent, Navarro, Claire L., Perrin, Sophie, Odelin, Gaelle, Lévy, Nicolas, Cau, Pierre, Remy, Élisabeth, Baudot, Anaïs

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A recurrent homozygous LMNA missense variant p.Thr528Met causes atypical progeroid syndrome characterized by mandibuloacral dysostosis, severe muscular dystrophy, and skeletal defo... von Saadi, Abdelkrim, Navarro, Claire, Ozalp, Ozge, Lourenco, Charles Marques, Fayek, Racha, Da Silva, Nathalie, Chaouch, Athmane, Benahmed, Meryem, Kubisch, Christian, Munnich, Arnold, Lévy, Nicolas, Roll, Patrice, Pacha, Lamia Ali, Chaouch, Malika, Lessel, Davor, De Sandre‐Giovannoli, Annachiara

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Unique Preservation of Neural Cells in Hutchinson- Gilford Progeria Syndrome Is Due to the Expression of the Neural-Specific miR-9 MicroRNA von Nissan, Xavier, Blondel, Sophie, Navarro, Claire, Maury, Yves, Denis, Cécile, Girard, Mathilde, Martinat, Cécile, De Sandre-Giovannoli, Annachiara, Levy, Nicolas, Peschanski, Marc

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Heterozygous expression of Cre recombinase in podocytes has no impact on the anti‐glomerular basement membrane glomerulonephritis model in C57BL/6J mice von Mousseaux, Cyril, Migeon, Tiffany, Frère, Perrine, Verpont, Marie Christine, Lutete, Elisabeth, Navarro, Claire, Louedec, Liliane, Hadchouel, Juliette

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Antisense-Based Progerin Downregulation in HGPS-Like Patients' Cells von Harhouri, Karim, Navarro, Claire, Baquerre, Camille, Da Silva, Nathalie, Bartoli, Catherine, Casey, Frank, Mawuse, Guedenon Koffi, Doubaj, Yassamine, Lévy, Nicolas, De Sandre-Giovannoli, Annachiara

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New ZMPSTE24 (FACE1) mutations in patients affected with restrictive dermopathy or related progeroid syndromes and mutation update von Navarro, Claire Laure, Esteves-Vieira, Vera, Courrier, Sébastien, Boyer, Amandine, Duong Nguyen, Thuy, Huong, Le Thi Thanh, Meinke, Peter, Schröder, Winnie, Cormier-Daire, Valérie, Sznajer, Yves, Amor, David J, Lagerstedt, Kristina, Biervliet, Martine, van den Akker, Peter C, Cau, Pierre, Roll, Patrice, Lévy, Nicolas, Badens, Catherine, Wehnert, Manfred, De Sandre-Giovannoli, Annachiara

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Truncated prelamin A expression in HGPS-like patients: a transcriptional study von Barthélémy, Florian, Navarro, Claire, Fayek, Racha, Da Silva, Nathalie, Roll, Patrice, Sigaudy, Sabine, Oshima, Junko, Bonne, Gisèle, Papadopoulou-Legbelou, Kyriaki, Evangeliou, Athanasios E, Spilioti, Martha, Lemerrer, Martine, Wevers, Ron A, Morava, Eva, Robaglia-Schlupp, Andrée, Lévy, Nicolas, Bartoli, Marc, De Sandre-Giovannoli, Annachiara

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A conserved splicing mechanism of the LMNA gene controls premature aging von Lopez-Mejia, Isabel C., Vautrot, Valentin, De Toledo, Marion, Behm-Ansmant, Isabelle, Bourgeois, Cyril F., Navarro, Claire L., Osorio, Fernando G., Freije, José M. P., Stévenin, James, De Sandre-Giovannoli, Annachiara, Lopez-Otin, Carlos, Lévy, Nicolas, Branlant, Christiane, Tazi, Jamal

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An inherited LMNA gene mutation in atypical Progeria syndrome von Doubaj, Yassamine, De Sandre‐Giovannoli, Annachiara, Vera, Esteves‐Vieira, Navarro, Claire Laure, Elalaoui, Siham Chafai, Tajir, Mariam, Lévy, Nicolas, Sefiani, Abdelaziz

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A New Lamin A Mutation Associated with Acrogeria Syndrome von Hadj-Rabia, Smail, Mashiah, Jacob, Roll, Patrice, Boyer, Amandine, Bourgeois, Patrice, Van Kien, Philippe Khau, Lévy, Nicolas, De Sandre-Giovannoli, Annachiara, Bodemer, Christine, Navarro, Claire

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Type B mandibuloacral dysplasia with congenital myopathy due to homozygous ZMPSTE24 missense mutation von Yaou, Rabah Ben, Navarro, Claire, Quijano-Roy, Susana, Bertrand, Anne T, Massart, Catherine, De Sandre-Giovannoli, Annachiara, Cadiñanos, Juan, Mamchaoui, Kamel, Butler-Browne, Gillian, Estournet, Brigitte, Richard, Pascale, Barois, Annie, Lévy, Nicolas, Bonne, Gisèle

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Prelamin A processing and functional effects in restrictive dermopathy von Columbaro, Marta, Mattioli, Elisabetta, Schena, Elisa, Capanni, Cristina, Cenni, Vittoria, Levy, Nicolas, Navarro, Claire L., Del Coco, Rosalba, Squarzoni, Stefano, Camozzi, Daria, Hutchison, Chris J., Wehnert, Manfred, Lattanzi, Giovanna

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Carbapenemase-Producing Enterobacteriaceae and Nonfermentative Bacteria, the Philippines, 2013-2016 von Velasco, John Mark, Valderama, Maria Theresa, Peacock, Trent, Warawadee, Nirdnoy, Nogrado, Kathyleen, Navarro, Fatima Claire, Chua, Jr, Domingo, Apichai, Srijan, Sirigade, Ruekit, Macareo, Louis R, Swierczewski, Brett

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Lamin A and ZMPSTE24 (FACE-1) defects cause nuclear disorganization and identify restrictive dermopathy as a lethal neonatal laminopathy von Navarro, Claire L., De Sandre-Giovannoli, Annachiara, Bernard, Rafaëlle, Boccaccio, Irène, Boyer, Amandine, Geneviève, David, Hadj-Rabia, Smail, Gaudy-Marqueste, Caroline, Smitt, Henk Sillevis, Vabres, Pierre, Faivre, Laurence, Verloes, Alain, Van Essen, Ton, Flori, Elisabeth, Hennekam, Raoul, Beemer, Frits A., Laurent, Nicole, Le Merrer, Martine, Cau, Pierre, Lévy, Nicolas

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HGPS and related premature aging disorders: From genomic identification to the first therapeutic approaches von Pereira, Sandrine, Bourgeois, Patrice, Navarro, Claire, Esteves-Vieira, Vera, Cau, Pierre, De Sandre-Giovannoli, Annachiara, Lévy, Nicolas

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