Quantification assays for total and polyglutamine-expanded huntingtin proteins von Macdonald, Douglas, Tessari, Michela A, Boogaard, Ivette, Smith, Melanie, Pulli, Kristiina, Szynol, Agnieszka, Albertus, Faywell, Lamers, Marieke B A C, Dijkstra, Sipke, Kordt, Daniel, Reindl, Wolfgang, Herrmann, Frank, McAllister, George, Fischer, David F, Munoz-Sanjuan, Ignacio

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Decreased Peak Expiratory Flow Associated with Muscle Fiber-Type Switching in Spinal and Bulbar Muscular Atrophy von Yamada, Shinichiro, Hashizume, Atsushi, Hijikata, Yasuhiro, Inagaki, Tomonori, Suzuki, Keisuke, Kondo, Naohide, Kawai, Kaori, Noda, Seiya, Nakanishi, Hirotaka, Banno, Haruhiko, Hirakawa, Akihiro, Koike, Haruki, Halievski, Katherine, Jordan, Cynthia L, Katsuno, Masahisa, Sobue, Gen

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Diabetes mellitus accelerates Aβ pathology in brain accompanied by enhanced GAβ generation in nonhuman primates von Okabayashi, Sachi, Shimozawa, Nobuhiro, Yasutomi, Yasuhiro, Yanagisawa, Katsuhiko, Kimura, Nobuyuki

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Biomarker repurposing: Therapeutic drug monitoring of serum theophylline offers a potential diagnostic biomarker of Parkinson's disease von Ohmichi, Takuma, Kasai, Takashi, Kosaka, Tadashi, Shikata, Keisuke, Tatebe, Harutsugu, Ishii, Ryotaro, Shinomoto, Makiko, Mizuno, Toshiki, Tokuda, Takahiko

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Proteins with Intrinsically Disordered Domains Are Preferentially Recruited to Polyglutamine Aggregates von Wear, Maggie P, Kryndushkin, Dmitry, O'Meally, Robert, Sonnenberg, Jason L, Cole, Robert N, Shewmaker, Frank P

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Alteration of POLDIP3 splicing associated with loss of function of TDP-43 in tissues affected with ALS von Shiga, Atsushi, Ishihara, Tomohiko, Miyashita, Akinori, Kuwabara, Misaki, Kato, Taisuke, Watanabe, Norihiro, Yamahira, Akie, Kondo, Chigusa, Yokoseki, Akio, Takahashi, Masuhiro, Kuwano, Ryozo, Kakita, Akiyoshi, Nishizawa, Masatoyo, Takahashi, Hitoshi, Onodera, Osamu

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Assessment of motor function, sensory motor gating and recognition memory in a novel BACHD transgenic rat model for huntington disease von Abada, Yah-Se K, Nguyen, Huu Phuc, Schreiber, Rudy, Ellenbroek, Bart

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Viral Vector-Based Dissection of Marmoset GFAP Promoter in Mouse and Marmoset Brains von Shinohara, Yoichiro, Konno, Ayumu, Takahashi, Nobutaka, Matsuzaki, Yasunori, Kishi, Shoji, Hirai, Hirokazu

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Intravitreal administration of HA-1077, a ROCK inhibitor, improves retinal function in a mouse model of huntington disease von Li, Mei, Yasumura, Douglas, Ma, Aye Aye K, Matthes, Michael T, Yang, Haidong, Nielson, Gregory, Huang, Yong, Szoka, Francis C, Lavail, Matthew M, Diamond, Marc I

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Reduced Levels of Proteasome Products in a Mouse Striatal Cell Model of Huntington's Disease von Dasgupta, Sayani, Fishman, Michael A, Mahallati, Hana, Castro, Leandro M, Tashima, Alexandre K, Ferro, Emer S, Fricker, Lloyd D

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Lack of correlation between the kinase activity of LRRK2 harboring kinase-modifying mutations and its phosphorylation at Ser910, 935, and Ser955 von Ito, Genta, Fujimoto, Tetta, Kamikawaji, Shogo, Kuwahara, Tomoki, Iwatsubo, Takeshi

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An efficient kinetic model for assemblies of amyloid fibrils and its application to polyglutamine aggregation von Prigent, Stéphanie, Ballesta, Annabelle, Charles, Frédérique, Lenuzza, Natacha, Gabriel, Pierre, Tine, Léon Matar, Rezaei, Human, Doumic, Marie

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Reversal learning and associative memory impairments in a BACHD rat model for Huntington disease von Abada, Yah-Se K, Nguyen, Huu Phuc, Ellenbroek, Bart, Schreiber, Rudy

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Differential effect of HDAC3 on cytoplasmic and nuclear huntingtin aggregates von Mano, Tatsuo, Suzuki, Takayoshi, Tsuji, Shoji, Iwata, Atsushi

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Oral administration of the pimelic diphenylamide HDAC inhibitor HDACi 4b is unsuitable for chronic inhibition of HDAC activity in the CNS in vivo von Beconi, Maria, Aziz, Omar, Matthews, Kim, Moumné, Lara, O'Connell, Catherine, Yates, Dawn, Clifton, Steven, Pett, Hannah, Vann, Julie, Crowley, Lynsey, Haughan, Alan F, Smith, Donna L, Woodman, Ben, Bates, Gillian P, Brookfield, Fred, Bürli, Roland W, McAllister, George, Dominguez, Celia, Munoz-Sanjuan, Ignacio, Beaumont, Vahri

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A huntingtin peptide inhibits polyQ-huntingtin associated defects von Arribat, Yoan, Bonneaud, Nathalie, Talmat-Amar, Yasmina, Layalle, Sophie, Parmentier, Marie-Laure, Maschat, Florence

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Large-scale RNA interference screening in mammalian cells identifies novel regulators of mutant huntingtin aggregation von Yamanaka, Tomoyuki, Wong, Hon Kit, Tosaki, Asako, Bauer, Peter O, Wada, Koji, Kurosawa, Masaru, Shimogori, Tomomi, Hattori, Nobutaka, Nukina, Nobuyuki

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Disulfide scrambling in superoxide dismutase 1 reduces its cytotoxic effect in cultured cells and promotes protein aggregation von Leinartaitė, Lina, Johansson, Ann-Sofi

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Internal ribosome entry segment activity of ATXN8 opposite strand RNA von Chen, I-Cheng, Lin, Hsuan-Yuan, Hsiao, Ya-Chin, Chen, Chiung-Mei, Wu, Yih-Ru, Shiau, Hsin-Chieh, Shen, Yu-Fang, Huang, Kuo-Shiu, Su, Ming-Tsan, Hsieh-Li, Hsiu-Mei, Lee-Chen, Guey-Jen

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Comparison of serum and plasma as a source of blood extracellular vesicles: Increased levels of platelet-derived particles in serum extracellular vesicle fractions alter content pr... von Zhang, Xiaoman, Takeuchi, Toshihide, Takeda, Akiko, Mochizuki, Hideki, Nagai, Yoshitaka

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