Modulating mtDNA heteroplasmy by mitochondria-targeted restriction endonucleases in a 'differential multiple cleavage-site' model von BACMAN, S. R, WILLIAMS, S. L, HERNANDEZ, D, MORAES, C. T

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Mitochondrial DNA depletion: Mutations in thymidine kinase gene with myopathy and SMA von MANCUSO, M, SALVIATI, L, GARCIA-ALVAREZ, M, MONZON, L, NAINI, A. B, HIRANO, M, BONILLA, E, TARATUTO, A. L, DIMAURO, S, VU, T. H, SACCONI, S, OTAEGUI, D, CAMANO, P, MARINA, A, BACMAN, S, MORAES, C. T, CARLO, J. R, GARCIA, M

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Pathophysiology and fate of hepatocytes in a mouse model of mitochondrial hepatopathies von Diaz, F, Garcia, S, Hernandez, D, Regev, A, Rebelo, A, Oca-Cossio, J, Moraes, C T

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The striatum is highly susceptible to mitochondrial oxidative phosphorylation dysfunctions von Pickrell, Alicia M, Fukui, Hirokazu, Wang, Xiao, Pinto, Milena, Moraes, Carlos T

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MELAS: Clinical features, biochemistry, and molecular genetics von Ciafaloni, E., Ricci, E., Shanske, S., Moraes, C. T., Silvestri, G., Hirano, M., Simonetti, S., Angelini, C., Donati, M. A., Garcia, C., Martinuzzi, A., Mosewich, R., Servidei, S., Zammarchi, E., Bonilla, E., DeVivo, D. C., Rowland, L. P., Schon, E. A., DiMauro, S.

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Distribution of wild-type and common deletion forms of mtDNA in normal and respiration-deficient muscle fibers from patients with mitochondrial myopathy von Sciacco, Monica, Bonilla, Eduardo, Schon, Eric A., DiMauro, Salvatore, Moraes, Carlos T.

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Respiratory Complex III Is Required to Maintain Complex I in Mammalian Mitochondria von Acı́n-Pérez, Rebeca, Bayona-Bafaluy, Marı́a Pilar, Fernández-Silva, Patricio, Moreno-Loshuertos, Raquel, Pérez-Martos, Acisclo, Bruno, Claudio, Moraes, Carlos T, Enrı́quez, José A

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Reactive oxygen species and mitochondrial diseases von Kirkinezos, Ilias G., Moraes, Carlos T.

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Titrating the Effects of Mitochondrial Complex I Impairment in the Cell Physiology von Barrientos, A, Moraes, C T

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mtDNA depletion with variable tissue expression : a novel genetic abnormality in mitochondrial diseases von MORAES, C. T, SHANSKE, S, TRITSCHLER, H.-J, APRILLE, J. R, ANDREETTA, F, BONILLA, E, SCHON, E. A, DIMAURO, S

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Manipulating mitochondrial DNA heteroplasmy by a mitochondrially targeted restriction endonuclease von Srivastava, S, Moraes, C T

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A disease-associated G5703A mutation in human mitochondrial DNA causes a conformational change and a marked decrease in steady-state levels of mitochondrial tRNA(Asn) von Hao, H, Moraes, C T

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Suppression of a mitochondrial tRNA gene mutation phenotype associated with changes in the nuclear background von HUILING HAO, MORRISON, L. E, MORAES, C. T

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Limitations of Allotopic Expression of Mitochondrial Genes in Mammalian Cells von Oca-Cossio, Jose, Kenyon, Lesley, Hao, Huiling, Moraes, Carlos T

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Simultaneous Transfer of Mitochondrial DNA and Single Chromosomes in Somatic Cells: A Novel Approach for the Study of Defects in Nuclear-Mitochondrial Communication von Barrientos, Antoni, Moraes, Carlos T.

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A new mutation associated with MELAS is located in a mitochondrial DNA polypeptide-coding gene von Manfredi, G., Schon, E.A., Moraes, C.T., Bonilla, E., Berry, G.T., Sladky, J.T., Dimauro, S.

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Expanding the Functional Human Mitochondrial DNA Database by the Establishment of Primate Xenomitochondrial Cybrids von Kenyon, Lesley, Moraes, Carlos T.

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Extremely high levels of mutant mtDNAs co-localize with cytochrome c oxidase-negative ragged-red fibers in patients harboring a point mutation at nt 3243 von PETRUZZELLA, V, MORAES, C. T, SANO, M. C, BONILLA, E, DIMAURO, S, SCHON, E. A

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The mitochondrial impairment, oxidative stress and neurodegeneration connection: reality or just an attractive hypothesis? von Fukui, Hirokazu, Moraes, Carlos T

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Functional Constraints of Nuclear-Mitochondrial DNA Interactions in Xenomitochondrial Rodent Cell Lines von Dey, R, Barrientos, A, Moraes, C T

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