Human Inborn Errors of Immunity: 2022 Update on the Classification from the International Union of Immunological Societies Expert Committee von Tangye, Stuart G., Al-Herz, Waleed, Bousfiha, Aziz, Cunningham-Rundles, Charlotte, Franco, Jose Luis, Holland, Steven M., Klein, Christoph, Morio, Tomohiro, Oksenhendler, Eric, Picard, Capucine, Puel, Anne, Puck, Jennifer, Seppänen, Mikko R. J., Somech, Raz, Su, Helen C., Sullivan, Kathleen E., Torgerson, Troy R., Meyts, Isabelle

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The Ever-Increasing Array of Novel Inborn Errors of Immunity: an Interim Update by the IUIS Committee von Tangye, Stuart G., Al-Herz, Waleed, Bousfiha, Aziz, Cunningham-Rundles, Charlotte, Franco, Jose Luis, Holland, Steven M, Klein, Christoph, Morio, Tomohiro, Oksenhendler, Eric, Picard, Capucine, Puel, Anne, Puck, Jennifer, Seppänen, Mikko R. J., Somech, Raz, Su, Helen C, Sullivan, Kathleen E., Torgerson, Troy R., Meyts, Isabelle

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European Society for Immunodeficiencies (ESID) and European Reference Network on Rare Primary Immunodeficiency, Autoinflammatory and Autoimmune Diseases (ERN RITA) Complement Guide... von Brodszki, Nicholas, Frazer-Abel, Ashley, Grumach, Anete S., Kirschfink, Michael, Litzman, Jiri, Perez, Elena, Seppänen, Mikko R. J., Sullivan, Kathleen E., Jolles, Stephen

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Glimpses into treating GLILD von Martelius, Timi, Seppänen, Mikko R.J.

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Editorial: Updates on the pathogenesis of common variable immunodeficiency (CVID) von Martelius, Timi, Seppänen, Mikko R J, Warnatz, Klaus

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Novel cytoskeletal mutations with immunodeficiency: Why is the raven like a writing desk? von Seppänen, Mikko R.J.

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Inflammation and Neutrophil Oxidative Burst in a Family with NFKB1 p.R157X LOF and Sterile Necrotizing Fasciitis von Santaniemi, Wenny, Åström, Pirjo, Glumoff, Virpi, Pernaa, Nora, Tallgren, Ella-Noora, Palosaari, Sanna, Nissinen, Antti, Kaustio, Meri, Kuismin, Outi, Saarela, Janna, Nurmi, Katariina, Eklund, Kari K., Seppänen, Mikko R. J., Hautala, Timo

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Primary Immunodeficiency, a Possible Cause of Neutrophilic Necrotizing Dermatosis von Kaustio, Meri, Hautala, Timo, Seppänen, Mikko R. J

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Inborn Errors of Immunity on the Island of Ireland — a Cross-Jurisdictional UKPID/ESID Registry Report von Ryan, Paul, Redenbaugh, Vyanka, McGucken, Jayne, Kindle, Gerhard, Devlin, Lisa A., Coulter, Tanya, Buckland, Matthew S., Seppänen, Mikko R. J., Conlon, Niall P., Feighery, Conleth, Edgar, J. David M.

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Human OTULIN haploinsufficiency impairs cell-intrinsic immunity to staphylococcal α-toxin von Spaan, András N, Neehus, Anna-Lena, Laplantine, Emmanuel, Staels, Frederik, Ogishi, Masato, Seeleuthner, Yoann, Rapaport, Franck, Lacey, Keenan A, Van Nieuwenhove, Erika, Chrabieh, Maya, Hum, David, Migaud, Mélanie, Izmiryan, Araksya, Lorenzo, Lazaro, Kochetkov, Tatiana, Heesterbeek, Dani A C, Bardoel, Bart W, DuMont, Ashley L, Dobbs, Kerry, Chardonnet, Solenne, Heissel, Søren, Baslan, Timour, Zhang, Peng, Yang, Rui, Bogunovic, Dusan, Wunderink, Herman F, Haas, Pieter-Jan A, Molina, Henrik, Van Buggenhout, Griet, Lyonnet, Stanislas, Notarangelo, Luigi D, Seppänen, Mikko R J, Weil, Robert, Seminario, Gisela, Gomez-Tello, Héctor, Wouters, Carine, Mesdaghi, Mehrnaz, Shahrooei, Mohammad, Bossuyt, Xavier, Sag, Erdal, Topaloglu, Rezan, Ozen, Seza, Leavis, Helen L, van Eijk, Maarten M J, Bezrodnik, Liliana, Blancas Galicia, Lizbeth, Hovnanian, Alain, Nassif, Aude, Bader-Meunier, Brigitte, Neven, Bénédicte, Meyts, Isabelle, Schrijvers, Rik, Puel, Anne, Bustamante, Jacinta, Aksentijevich, Ivona, Kastner, Daniel L, Torres, Victor J, Humblet-Baron, Stéphanie, Liston, Adrian, Abel, Laurent, Boisson, Bertrand, Casanova, Jean-Laurent

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Clinical efficacy of SARS‐CoV‐2 Omicron‐neutralizing antibodies in immunoglobulin preparations for the treatment of agammaglobulinemia in patients with primary antibody deficiency... von Karbiener, Michael, Kindle, Gerhard, Meyts, Isabelle, Seppänen, Mikko R. J., Candotti, Fabio, Kamieniak, Marta, Ilk, Reinhard, Kreil, Thomas R., Seidel, Markus G.

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Characterization of Expanded Gamma Delta T Cells from Atypical X-SCID Patient Reveals Preserved Function and IL2RG-Mediated Signaling von Tuovinen, Elina A., Pöysti, Sakari, Hamdan, Firas, Le, Kim My, Keskitalo, Salla, Turunen, Tanja, Minier, Léa, Mamia, Nanni, Heiskanen, Kaarina, Varjosalo, Markku, Cerullo, Vincenzo, Kere, Juha, Seppänen, Mikko R. J., Hänninen, Arno, Grönholm, Juha

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Rubella virus-associated granulomas controlled with allogeneic hematopoietic stem cell transplantation von Hautala, Timo, Perelygina, Ludmila, Salmenniemi, Urpu, Seppänen, Mikko R. J.

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The 2022 Update of IUIS Phenotypical Classification for Human Inborn Errors of Immunity von Bousfiha, Aziz, Moundir, Abderrahmane, Tangye, Stuart G., Picard, Capucine, Jeddane, Leïla, Al-Herz, Waleed, Rundles, Charlotte C., Franco, Jose Luis, Holland, Steven M., Klein, Christoph, Morio, Tomohiro, Oksenhendler, Eric, Puel, Anne, Puck, Jennifer, Seppänen, Mikko R. J., Somech, Raz, Su, Helen C., Sullivan, Kathleen E., Torgerson, Troy R., Meyts, Isabelle

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The GAIN Registry — a New Prospective Study for Patients with Multi-organ Autoimmunity and Autoinflammation von Staus, Paulina, Rusch, Stephan, El-Helou, Sabine, Müller, Gabriele, Krausz, Máté, Geisen, Ulf, Caballero-Oteyza, Andrés, Krüger, Renate, Bakhtiar, Shahrzad, Lee-Kirsch, Min Ae, Fasshauer, Maria, Baumann, Ulrich, Hoyer, Bimba Franziska, Farela Neves, João, Borte, Michael, Carrabba, Maria, Hauck, Fabian, Ehl, Stephan, Bader, Peter, von Bernuth, Horst, Atschekzei, Faranaz, Seppänen, Mikko R. J., Warnatz, Klaus, Nieters, Alexandra, Kindle, Gerhard, Grimbacher, Bodo

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Behçet disease (BD) and BD‐like clinical phenotypes: NF‐κB pathway in mucosal ulcerating diseases von Perazzio, Sandro F., Allenspach, Eric J., Eklund, Kari K., Varjosalo, Markku, Shinohara, Michi M., Torgerson, Troy R., Seppänen, Mikko R. J.

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Comparison of machine learning methods in the early identification of vasculitides, myositides and glomerulonephritides von Ryyppö, Rasmus, Häyrynen, Sergei, Joutsijoki, Henry, Juhola, Martti, Seppänen, Mikko R. J.

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Somatic mutations and T-cell clonality in patients with immunodeficiency von Savola, Paula, Martelius, Timi, Kankainen, Matti, Huuhtanen, Jani, Lundgren, Sofie, Koski, Yrjö, Eldfors, Samuli, Kelkka, Tiina, Keränen, Mikko A I, Ellonen, Pekka, Kovanen, Panu E, Kytölä, Soili, Saarela, Janna, Lähdesmäki, Harri, Seppänen, Mikko R J, Mustjoki, Satu

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Somatic mutations and T-cell clonality in patients with immunodeficiency von Savola, Paula, Martelius, Timi, Kankainen, Matti, Huuhtanen, Jani, Lundgren, Sofie, Koski, Yrjö, Eldfors, Samuli, Kelkka, Tiina, Keränen, Mikko A I, Ellonen, Pekka, Kovanen, Panu E, Kytölä, Soili, Saarela, Janna, Lähdesmäki, Harri, Seppänen, Mikko R J, Mustjoki, Satu

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Studying severe long COVID to understand post-infectious disorders beyond COVID-19 von Brodin, Petter, Casari, Giorgio, Townsend, Liam, O’Farrelly, Cliona, Tancevski, Ivan, Löffler-Ragg, Judith, Mogensen, Trine H., Casanova, Jean Laurent

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