The S/T-Rich Motif in the DNAJB6 Chaperone Delays Polyglutamine Aggregation and the Onset of Disease in a Mouse Model von Kakkar, Vaishali, Månsson, Cecilia, de Mattos, Eduardo P., Bergink, Steven, van der Zwaag, Marianne, van Waarde, Maria A.W.H., Kloosterhuis, Niels J., Melki, Ronald, van Cruchten, Remco T.P., Al-Karadaghi, Salam, Arosio, Paolo, Dobson, Christopher M., Knowles, Tuomas P.J., Bates, Gillian P., van Deursen, Jan M., Linse, Sara, van de Sluis, Bart, Emanuelsson, Cecilia, Kampinga, Harm H.

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CAG Repeat Size Influences the Progression Rate of Spinocerebellar Ataxia Type 3 von Leotti, Vanessa B., Vries, Jeroen J., Oliveira, Camila M., Mattos, Eduardo P., Te Meerman, Gerard J., Brunt, Ewout R., Kampinga, Harm H., Jardim, Laura B., Verbeek, Dineke S.

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DNAJB6, a Key Factor in Neuronal Sensitivity to Amyloidogenesis von Thiruvalluvan, Arun, de Mattos, Eduardo P., Brunsting, Jeanette F., Bakels, Rob, Serlidaki, Despina, Barazzuol, Lara, Conforti, Paola, Fatima, Azra, Koyuncu, Seda, Cattaneo, Elena, Vilchez, David, Bergink, Steven, Boddeke, Erik H.W.G., Copray, Sjef, Kampinga, Harm H.

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Protein Quality Control Pathways at the Crossroad of Synucleinopathies von De Mattos, Eduardo P., Wentink, Anne, Nussbaum-Krammer, Carmen, Hansen, Christian, Bergink, Steven, Melki, Ronald, Kampinga, Harm H.

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Identification of a premature stop codon mutation in the PHGDH gene in severe Neu-Laxova syndrome-evidence for phenotypic variability von Mattos, Eduardo P., Silva, André Anjos da, Magalhães, José Antônio A, Leite, Júlio César L., Leistner-Segal, Sandra, Gus-Kessler, Rejane, Perez, Juliano Adams, Vedolin, Leonardo M., Torreblanca-Zanca, Albertina, Lapunzina, Pablo, Ruiz-Perez, Victor L., Sanseverino, Maria Teresa V.

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Clinical and molecular characterization of a Brazilian cohort of campomelic dysplasia patients, and identification of seven new SOX9 mutations von Mattos, Eduardo P, Sanseverino, Maria Teresa V, Magalhães, José Antônio A, Leite, Júlio César L, Félix, Temis Maria, Todeschini, Luiz Alberto, Cavalcanti, Denise P, Schüler-Faccini, Lavinia

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Chaperones in Polyglutamine Aggregation: Beyond the Q-Stretch von Kuiper, E F E, de Mattos, Eduardo P, Jardim, Laura B, Kampinga, Harm H, Bergink, Steven

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Ophthalmological and Neurologic Manifestations in Pre-clinical and Clinical Phases of Spinocerebellar Ataxia Type 7 von Azevedo, Pietro B., Rocha, Anastácia G., Keim, Leda M. N., Lavinsky, Daniel, Furtado, Gabriel V., de Mattos, Eduardo P., Vargas, Fernando R., Leotti, Vanessa B., Saraiva-Pereira, Maria-Luiza, Jardim, Laura B.

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Clinical and Molecular Characterization of Osteogenesis Imperfecta Type V von Brizola, Evelise, Mattos, Eduardo P., Ferrari, Jessica, Freire, Patricia O.A., Germer, Raquel, Llerena Jr, Juan C., Félix, Têmis M.

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Misoprostol: A retrospective analysis of consultations to a Brazilian Teratology Information Service von Hoffmeister, Mariana C., Lopes, Flávia V., Sanseverino, Paula B., Mattos, Eduardo P., Ferrão, Maurício F., Franciosi, Betina P., Metzdorf, Luiza, Metzdorf, Marcela, Crestani, Paulo V., Silva, André A., Vianna, Fernanda S.L., Azevedo, Ligia M.R., Sanseverino, Maria Teresa V., Schüler-Faccini, Lavinia

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Atelosteogenesis Type 2/Diastrophic Dysplasia Phenotypic Spectrum: From Prenatal to Preimplantation Genetic Diagnosis von Mattos, Eduardo P., Magalhaes, Jose Antonio A., Mittaz-Crettol, Laureane, Azambuja, Ricardo, Okada, Lilian, Cavalcanti, Denise P., Cuzzi, Juliana, Badalotti, Mariangela, Petracco, Rafaella, Petracco, Alvaro, Schuler-Faccini, Lavinia, Sanseverino, Maria Teresa V.

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On the relative importance of CSR ecological strategies and integrative traits to explain species dominance at local scales von Rosado, Bruno H. P., de Mattos, Eduardo A.

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Multidimensional ecological analyses demonstrate how interactions between functional traits shape fitness and life history strategies von Pistón, Nuria, Bello, Francesco, Dias, André T. C., Götzenberger, Lars, Rosado, Bruno H. P., Mattos, Eduardo A., Salguero‐Gómez, Roberto, Carmona, Carlos P., Cornelissen, Hans

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Eltonian shortfall due to the Grinnellian view: functional ecology between the mismatch of niche concepts von Rosado, Bruno H. P., Figueiredo, Marcos S. L., de Mattos, Eduardo A., Grelle, Carlos E. V.

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Inhalation of the prodrug PI3K inhibitor CL27c improves lung function in asthma and fibrosis von Campa, Carlo C., Silva, Rangel L., Margaria, Jean P., Pirali, Tracey, Mattos, Matheus S., Kraemer, Lucas R., Reis, Diego C., Grosa, Giorgio, Copperi, Francesca, Dalmarco, Eduardo M., Lima-Júnior, Roberto C. P., Aprile, Silvio, Sala, Valentina, Dal Bello, Federica, Prado, Douglas Silva, Alves-Filho, Jose Carlos, Medana, Claudio, Cassali, Geovanni D., Tron, Gian Cesare, Teixeira, Mauro M., Ciraolo, Elisa, Russo, Remo C., Hirsch, Emilio

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Metal bioaccumulation, oxidative stress and antioxidant responses in oysters Crassostrea gasar transplanted to an estuary in southern Brazil von Ferreira, Clarissa P., Lima, Daína, Paiva, Raphaella, Vilke, Juliano M., Mattos, Jacó J., Almeida, Eduardo A., Grott, Suelen C., Alves, Thiago C., Corrêa, Jacyara N., Jorge, Marianna B., Uczay, Mariana, Vogel, Carla I.G., Gomes, Carlos H.A.M., Bainy, Afonso C.D., Lüchmann, Karim H.

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Alternative plant designs: consequences for community assembly and ecosystem functioning von Dias, André Tavares Corrêa, Rosado, Bruno H P, De Bello, Francesco, Pistón, Nuria, De Mattos, Eduardo A

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Exposure to phenanthrene and depuration: Changes on gene transcription, enzymatic activity and lipid peroxidation in gill of scallops Nodipecten nodosus von Piazza, Rômi S., Trevisan, Rafael, Flores-Nunes, Fabrício, Toledo-Silva, Guilherme, Wendt, Nestor, Mattos, Jacó J., Lima, Daína, Taniguchi, Satie, Sasaki, Silvio Tarou, Mello, Álvaro C.P., Zacchi, Flávia L., Serrano, Miguel A.S., Gomes, Carlos H.A.M., Bícego, Márcia C., Almeida, Eduardo A.de, Bainy, Afonso C.D.

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Emerging and legacy contaminants on the Brazilian southern coast (Santa Catarina): A multi-biomarker approach in oysters Crassostrea gasar (Adanson, 1757) von Bastolla, Camila L.V., Guerreiro, Fernando C., Saldaña-Serrano, Miguel, Gomes, Carlos H.A.M., Lima, Daína, Rutkoski, Camila F., Mattos, Jacó J., Dias, Vera Helena V., Righetti, Bárbara P.H., Ferreira, Clarissa P., Martim, Julia, Alves, Thiago C., Melo, Claudio M.R., Marques, Maria R.F., Lüchmann, Karim H., Almeida, Eduardo A., Bainy, Afonso C.D.

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A phase 2 study of first‐line nivolumab in patients with locally advanced or metastatic cutaneous squamous‐cell carcinoma von Munhoz, Rodrigo R., Nader‐Marta, Guilherme, Camargo, Veridiana P., Queiroz, Marcello M., Cury‐Martins, Jade, Ricci, Hermínia, Mattos, Marcela R., Menezes, Thiago A. F., Machado, Guilherme U. C., Bertolli, Eduardo, Barros, Milton, Souza, Carina E., Franke, Fábio, Ferreira, Fabio O., Feher, Olavo, Castro, Gilberto

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