Misrouting of v-ATPase subunit V0a1 dysregulates lysosomal acidification in a neurodegenerative lysosomal storage disease model von Bagh, Maria B., Peng, Shiyong, Chandra, Goutam, Zhang, Zhongjian, Singh, Satya P., Pattabiraman, Nagarajan, Liu, Aiyi, Mukherjee, Anil B.

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Emerging new roles of the lysosome and neuronal ceroid lipofuscinoses von Mukherjee, Anil B, Appu, Abhilash P, Sadhukhan, Tamal, Casey, Sydney, Mondal, Avisek, Zhang, Zhongjian, Bagh, Maria B

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Neuroprotection and lifespan extension in Ppt1−/− mice by NtBuHA: therapeutic implications for INCL von Sarkar, Chinmoy, Chandra, Goutam, Peng, Shiyong, Zhang, Zhongjian, Liu, Aiyi, Mukherjee, Anil B

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ER and oxidative stresses are common mediators of apoptosis in both neurodegenerative and non-neurodegenerative lysosomal storage disorders and are alleviated by chemical chaperone... von Wei, Hui, Kim, Sung-Jo, Zhang, Zhongjian, Tsai, Pei-Chih, Wisniewski, Krystyna E., Mukherjee, Anil B.

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Oral cysteamine bitartrate and N-acetylcysteine for patients with infantile neuronal ceroid lipofuscinosis: a pilot study von Levin, Sondra W, MD, Baker, Eva H, PhD, Zein, Wadih M, MD, Zhang, Zhongjian, MD, Quezado, Zenaide M N, MD, Miao, Ning, MD, Gropman, Andrea, MD, Griffin, Kurt J, MD, Bianconi, Simona, MD, Chandra, Goutam, PhD, Khan, Omar I, MD, Caruso, Rafael C, MD, Liu, Aiyi, PhD, Mukherjee, Anil B, Dr

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The blood-brain barrier is disrupted in a mouse model of infantile neuronal ceroid lipofuscinosis: amelioration by resveratrol von SAHA, Arjun, SARKAR, Chinmoy, SINGH, Satya P, ZHONGJIAN ZHANG, MUNASINGHE, Jeeva, SHIYONG PENG, CHANDRA, Goutam, KONG, Eryan, MUKHERJEE, Anil B

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Allergic Asthma: Influence of Genetic and Environmental Factors von Mukherjee, Anil B., Zhang, Zhongjian

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Lack of an Endogenous Anti-inflammatory Protein in Mice Enhances Colonization of B16F10 Melanoma Cells in the Lungs von Saha, Arjun, Lee, Yi-Ching, Zhang, Zhongjian, Chandra, Goutam, Su, Shao-Bo, Mukherjee, Anil B.

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Dynamic Palmitoylation Links Cytosol-Membrane Shuttling of Acyl-protein Thioesterase-1 and Acyl-protein Thioesterase-2 with That of Proto-oncogene H-Ras Product and Growth-associat... von Kong, Eryan, Peng, Shiyong, Chandra, Goutam, Sarkar, Chinmoy, Zhang, Zhongjian, Bagh, Maria B., Mukherjee, Anil B.

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In a mouse model of INCL reduced S‐palmitoylation of cytosolic thioesterase APT1 contributes to microglia proliferation and neuroinflammation von Sadhukhan, Tamal, Bagh, Maria B., Appu, Abhilash P., Mondal, Avisek, Zhang, Wei, Liu, Aiyi, Mukherjee, Anil B.

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Disruption of lysosomal nutrient sensing scaffold contributes to pathogenesis of a fatal neurodegenerative lysosomal storage disease von Bagh, Maria B., Appu, Abhilash P., Sadhukhan, Tamal, Mondal, Avisek, Plavelil, Nisha, Raghavankutty, Mahadevan, Supran, Ajayan M., Sadhukhan, Sriparna, Liu, Aiyi, Mukherjee, Anil B.

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Disruption of lysosomal nutrient sensing scaffold hyperactivates mTORC1 contributing to pathogenesis of a fatal neurodegenerative disease von Bagh, Maria B, Appu, Abhilash P, Sadhukhan, Tamal, Mondal, Avisek, Plavelil, Nisha, Raghavankutty, Mahadevan, Supran, Ajayan M, Sadhukhan, Sriparna, Liu, Aiyi, Mukherjee, Anil B

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Uteroglobin represses allergen-induced inflammatory response by blocking PGD2 receptor-mediated functions von Mandal, Asim K, Zhang, Zhongjian, Ray, Rabindranath, Choi, Moonsuk S, Chowdhury, Bhabadeb, Pattabiraman, Nagarajan, Mukherjee, Anil B

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Stop codon read-through with PTC124 induces palmitoyl-protein thioesterase-1 activity, reduces thioester load and suppresses apoptosis in cultured cells from INCL patients von Sarkar, Chinmoy, Zhang, Zhongjian, Mukherjee, Anil B.

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In a model of Batten disease, palmitoyl protein thioesterase-1 deficiency is associated with brown adipose tissue and thermoregulation abnormalities von Khaibullina, Alfia, Kenyon, Nicholas, Guptill, Virginia, Quezado, Martha M, Wang, Li, Koziol, Deloris, Wesley, Robert, Moya, Pablo R, Zhang, Zhongjian, Saha, Arjun, Mukherjee, Anil B, Quezado, Zenaide M N

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Uteroglobin: A Steroid-Inducible Immunomodulatory Protein That Founded the Secretoglobin Superfamily von Mukherjee, Anil B, Zhang, Zhongjian, Chilton, Beverly S

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Cln1‐mutations suppress Rab7‐RILP interaction and impair autophagy contributing to neuropathology in a mouse model of infantile neuronal ceroid lipofuscinosis von Sarkar, Chinmoy, Sadhukhan, Tamal, Bagh, Maria B., Appu, Abhilash P., Chandra, Goutam, Mondal, Avisek, Saha, Arjun, Mukherjee, Anil B.

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RAGE signaling contributes to neuroinflammation in infantile neuronal ceroid lipofuscinosis von Saha, Arjun, Kim, Sung-Jo, Zhang, Zhongjian, Lee, Yi-Ching, Sarkar, Chinmoy, Tsai, Pei-Chih, Mukherjee, Anil B.

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Cln3‐mutations underlying juvenile neuronal ceroid lipofuscinosis cause significantly reduced levels of Palmitoyl‐protein thioesterases‐1 (Ppt1)‐protein and Ppt1‐enzyme activity in... von Appu, Abhilash P., Bagh, Maria B., Sadhukhan, Tamal, Mondal, Avisek, Casey, Sydney, Mukherjee, Anil B.

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Ablation of microRNA-155 and neuroinflammation in a mouse model of CLN1-disease von Sadhukhan, Tamal, Bagh, Maria B., Sadhukhan, Sriparna, Appu, Abhilash P., Mondal, Avisek, Iben, James, Li, Tianwei, Coon, Steven L., Mukherjee, Anil B.

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