Gain of toxic function by long-term AAV9-mediated SMN overexpression in the sensorimotor circuit von Van Alstyne, Meaghan, Tattoli, Ivan, Delestrée, Nicolas, Recinos, Yocelyn, Workman, Eileen, Shihabuddin, Lamya S., Zhang, Chaolin, Mentis, George Z., Pellizzoni, Livio

Volltext

ALS-associated mutant FUS induces selective motor neuron degeneration through toxic gain of function von Sharma, Aarti, Lyashchenko, Alexander K., Lu, Lei, Nasrabady, Sara Ebrahimi, Elmaleh, Margot, Mendelsohn, Monica, Nemes, Adriana, Tapia, Juan Carlos, Mentis, George Z., Shneider, Neil A.

Volltext

An SMN-Dependent U12 Splicing Event Essential for Motor Circuit Function von Lotti, Francesco, Imlach, Wendy L., Saieva, Luciano, Beck, Erin S., Hao, Le T., Li, Darrick K., Jiao, Wei, Mentis, George Z., Beattie, Christine E., McCabe, Brian D., Pellizzoni, Livio

Volltext

The Classical Complement Pathway Mediates Microglia-Dependent Remodeling of Spinal Motor Circuits during Development and in SMA von Vukojicic, Aleksandra, Delestrée, Nicolas, Fletcher, Emily V., Pagiazitis, John G., Sankaranarayanan, Sethu, Yednock, Ted A., Barres, Ben A., Mentis, George Z.

Volltext

Spinal Inhibitory Interneuron Diversity Delineates Variant Motor Microcircuits von Bikoff, Jay B., Gabitto, Mariano I., Rivard, Andre F., Drobac, Estelle, Machado, Timothy A., Miri, Andrew, Brenner-Morton, Susan, Famojure, Erica, Diaz, Carolyn, Alvarez, Francisco J., Mentis, George Z., Jessell, Thomas M.

Volltext

Molecular correlates of muscle spindle and Golgi tendon organ afferents von Oliver, Katherine M., Florez-Paz, Danny M., Badea, Tudor Constantin, Mentis, George Z., Menon, Vilas, de Nooij, Joriene C.

Volltext

Activity Regulates the Incidence of Heteronymous Sensory-Motor Connections von Mendelsohn, Alana I., Simon, Christian M., Abbott, L.F., Mentis, George Z., Jessell, Thomas M.

Volltext

Early Functional Impairment of Sensory-Motor Connectivity in a Mouse Model of Spinal Muscular Atrophy von Mentis, George Z., Blivis, Dvir, Liu, Wenfang, Drobac, Estelle, Crowder, Melissa E., Kong, Lingling, Alvarez, Francisco J., Sumner, Charlotte J., O'Donovan, Michael J.

Volltext

Dysregulation of Mdm2 and Mdm4 alternative splicing underlies motor neuron death in spinal muscular atrophy von Van Alstyne, Meaghan, Simon, Christian M, Sardi, S Pablo, Shihabuddin, Lamya S, Mentis, George Z, Pellizzoni, Livio

Volltext

Converging Mechanisms of p53 Activation Drive Motor Neuron Degeneration in Spinal Muscular Atrophy von Simon, Christian M., Dai, Ya, Van Alstyne, Meaghan, Koutsioumpa, Charalampia, Pagiazitis, John G., Chalif, Joshua I., Wang, Xiaojian, Rabinowitz, Joseph E., Henderson, Christopher E., Pellizzoni, Livio, Mentis, George Z.

Volltext

Stasimon Contributes to the Loss of Sensory Synapses and Motor Neuron Death in a Mouse Model of Spinal Muscular Atrophy von Simon, Christian M., Van Alstyne, Meaghan, Lotti, Francesco, Bianchetti, Elena, Tisdale, Sarah, Watterson, D. Martin, Mentis, George Z., Pellizzoni, Livio

Volltext

Catecholaminergic dysfunction drives postural and locomotor deficits in a mouse model of spinal muscular atrophy von Pagiazitis, John G., Delestrée, Nicolas, Sowoidnich, Leonie, Sivakumar, Nandhini, Simon, Christian M., Chatzisotiriou, Athanasios, Albani, Maria, Mentis, George Z.

Volltext

Preserving neuromuscular synapses in ALS by stimulating MuSK with a therapeutic agonist antibody von Cantor, Sarah, Zhang, Wei, Delestrée, Nicolas, Remédio, Leonor, Mentis, George Z, Burden, Steven J

Volltext

A Stem Cell Model of the Motor Circuit Uncouples Motor Neuron Death from Hyperexcitability Induced by SMN Deficiency von Simon, Christian M., Janas, Anna M., Lotti, Francesco, Tapia, Juan Carlos, Pellizzoni, Livio, Mentis, George Z.

Volltext

SMN Is Essential for the Biogenesis of U7 Small Nuclear Ribonucleoprotein and 3′-End Formation of Histone mRNAs von Tisdale, Sarah, Lotti, Francesco, Saieva, Luciano, Van Meerbeke, James P., Crawford, Thomas O., Sumner, Charlotte J., Mentis, George Z., Pellizzoni, Livio

Volltext

Diverging roles for Lrp4 and Wnt signaling in neuromuscular synapse development during evolution von Remédio, Leonor, Gribble, Katherine D, Lee, Jennifer K, Kim, Natalie, Hallock, Peter T, Delestrée, Nicolas, Mentis, George Z, Froemke, Robert C, Granato, Michael, Burden, Steven J

Volltext

Sumoylation regulates the assembly and activity of the SMN complex von Riboldi, Giulietta M., Faravelli, Irene, Kuwajima, Takaaki, Delestrée, Nicolas, Dermentzaki, Georgia, De Planell-Saguer, Mariangels, Rinchetti, Paola, Hao, Le Thi, Beattie, Christine C., Corti, Stefania, Przedborski, Serge, Mentis, George Z., Lotti, Francesco

Volltext

Editorial: Dysfunction and Repair of Neural Circuits for Motor Control von Tosolini, Andrew Paul, Mentis, George Z, Martin, John H

Volltext

Sensory-Derived Glutamate Regulates Presynaptic Inhibitory Terminals in Mouse Spinal Cord von Mende, Michael, Fletcher, Emily V., Belluardo, Josephine L., Pierce, Joseph P., Bommareddy, Praveen K., Weinrich, Jarret A., Kabir, Zeeba D., Schierberl, Kathryn C., Pagiazitis, John G., Mendelsohn, Alana I., Francesconi, Anna, Edwards, Robert H., Milner, Teresa A., Rajadhyaksha, Anjali M., van Roessel, Peter J., Mentis, George Z., Kaltschmidt, Julia A.

Volltext

Laser microscopy acquisition and analysis of premotor synapses in the murine spinal cord von Buettner, Jannik M., Kirmann, Toni, Mentis, George Z., Hallermann, Stefan, Simon, Christian M.

Volltext