IRE1 Signaling Affects Cell Fate During the Unfolded Protein Response von Lin, Jonathan H, Li, Han, Yasumura, Douglas, Cohen, Hannah R, Zhang, Chao, Panning, Barbara, Shokat, Kevan M, LaVail, Matthew M, Walter, Peter

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Treatment of retinitis pigmentosa due to MERTK mutations by ocular subretinal injection of adeno-associated virus gene vector: results of a phase I trial von Ghazi, Nicola G., Abboud, Emad B., Nowilaty, Sawsan R., Alkuraya, Hisham, Alhommadi, Abdulrahman, Cai, Huimin, Hou, Rui, Deng, Wen-Tao, Boye, Sanford L., Almaghamsi, Abdulrahman, Al Saikhan, Fahad, Al-Dhibi, Hassan, Birch, David, Chung, Christopher, Colak, Dilek, LaVail, Matthew M., Vollrath, Douglas, Erger, Kirsten, Wang, Wenqiu, Conlon, Thomas, Zhang, Kang, Hauswirth, William, Alkuraya, Fowzan S.

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mTOR-mediated dedifferentiation of the retinal pigment epithelium initiates photoreceptor degeneration in mice von Zhao, Chen, Yasumura, Douglas, Li, Xiyan, Matthes, Michael, Lloyd, Marcia, Nielsen, Gregory, Ahern, Kelly, Snyder, Michael, Bok, Dean, Dunaief, Joshua L, LaVail, Matthew M, Vollrath, Douglas

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Robust Endoplasmic Reticulum-Associated Degradation of Rhodopsin Precedes Retinal Degeneration von Chiang, Wei-Chieh, Kroeger, Heike, Sakami, Sanae, Messah, Carissa, Yasumura, Douglas, Matthes, Michael T., Coppinger, Judith A., Palczewski, Krzysztof, LaVail, Matthew M., Lin, Jonathan H.

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Restoration of visual function in P23H rhodopsin transgenic rats by gene delivery of BiP/Grp78 von Gorbatyuk, Marina. S., Knox, Tessa, LaVail, Matthew M., Gorbatyuk, Oleg S., Noorwez, Syed M., Hauswirth, William W., Lin, Jonathan H., Muzyczka, Nicholas, Lewin, Alfred S., Berns, Kenneth I.

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Genotypic and phenotypic characterization of P23H line 1 rat model von Orhan, Elise, Dalkara, Deniz, Neuillé, Marion, Lechauve, Christophe, Michiels, Christelle, Picaud, Serge, Léveillard, Thierry, Sahel, José-Alain, Naash, Muna I, Lavail, Matthew M, Zeitz, Christina, Audo, Isabelle

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Tyro3 Modulates Mertk-Associated Retinal Degeneration von Vollrath, Douglas, Yasumura, Douglas, Benchorin, Gillie, Matthes, Michael T, Feng, Wei, Nguyen, Natalie M, Sedano, Cecilia D, Calton, Melissa A, LaVail, Matthew M

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Sphingolipid profile alters in retinal dystrophic P23H-1 rats and systemic FTY720 can delay retinal degeneration[S] von Stiles, Megan, Qi, Hui, Sun, Eleanor, Tan, Jeremy, Porter, Hunter, Allegood, Jeremy, Chalfant, Charles E., Yasumura, Douglas, Matthes, Michael T., LaVail, Matthew M., Mandal, Nawajes A.

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Timing and topography of cell genesis in the rat retina von Rapaport, David H., Wong, Lily L., Wood, Eric D., Yasumura, Douglas, LaVail, Matthew M.

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CNTF induces regeneration of cone outer segments in a rat model of retinal degeneration von Li, Yiwen, Tao, Weng, Luo, Lingyu, Huang, Deqiang, Kauper, Konrad, Stabila, Paul, Lavail, Matthew M, Laties, Alan M, Wen, Rong

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Intravitreal administration of HA-1077, a ROCK inhibitor, improves retinal function in a mouse model of huntington disease von Li, Mei, Yasumura, Douglas, Ma, Aye Aye K, Matthes, Michael T, Yang, Haidong, Nielson, Gregory, Huang, Yong, Szoka, Francis C, Lavail, Matthew M, Diamond, Marc I

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Retinal remodeling triggered by photoreceptor degenerations von Jones, Bryan W., Watt, Carl B., Frederick, Jeanne M., Baehr, Wolfgang, Chen, Ching-Kang, Levine, Edward M., Milam, Ann H., Lavail, Matthew M., Marc, Robert E.

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ER stress in retinal degeneration in S334ter Rho rats von Shinde, Vishal M, Sizova, Olga S, Lin, Jonathan H, LaVail, Matthew M, Gorbatyuk, Marina S

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The relationship of photoreceptor degeneration to retinal vascular development and loss in mutant rhodopsin transgenic and RCS rats von Pennesi, Mark E., Nishikawa, Shimpei, Matthes, Michael T., Yasumura, Douglas, LaVail, Matthew M.

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Stanniocalcin-1 Rescued Photoreceptor Degeneration in Two Rat Models of Inherited Retinal Degeneration von Roddy, Gavin W, Rosa Jr, Robert H, Youn Oh, Joo, Ylostalo, Joni H, Bartosh, Thomas J, Choi, Hosoon, Lee, Ryang Hwa, Yasumura, Douglas, Ahern, Kelly, Nielsen, Gregory, Matthes, Michael T, LaVail, Matthew M, Prockop, Darwin J

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Mertk Triggers Uptake of Photoreceptor Outer Segments during Phagocytosis by Cultured Retinal Pigment Epithelial Cells von Feng, Wei, Yasumura, Douglas, Matthes, Michael T., LaVail, Matthew M., Vollrath, Douglas

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Discordant anatomical, electrophysiological, and visual behavioral profiles of retinal degeneration in rat models of retinal degenerative disease von McGill, Trevor J, Prusky, Glen T, Douglas, Robert M, Yasumura, Douglas, Matthes, Michael T, Lowe, Robert J, Duncan, Jacque L, Yang, Haidong, Ahern, Kelly, Daniello, Kate M, Silver, Byron, LaVail, Matthew M

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Glutamatergic neurotransmission from melanopsin retinal ganglion cells is required for neonatal photoaversion but not adult pupillary light reflex von Delwig, Anton, Majumdar, Sriparna, Ahern, Kelly, LaVail, Matthew M, Edwards, Robert, Hnasko, Thomas S, Copenhagen, David R

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Translational and posttranslational regulation of XIAP by eIF2α and ATF4 promotes ER stress-induced cell death during the unfolded protein response von Hiramatsu, Nobuhiko, Messah, Carissa, Han, Jaeseok, LaVail, Matthew M, Kaufman, Randal J, Lin, Jonathan H

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Molecular and Cellular Alterations Induced by Sustained Expression of Ciliary Neurotrophic Factor in a Mouse Model of Retinitis Pigmentosa von Rhee, Kun Do, Ruiz, Alberto, Duncan, Jacque L, Hauswirth, William W, LaVail, Matthew M, Bok, Dean, Yang, Xian-Jie

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