Human iPSC-Derived Neural Progenitors Are an Effective Drug Discovery Model for Neurological mtDNA Disorders von Lorenz, Carmen, Lesimple, Pierre, Bukowiecki, Raul, Zink, Annika, Inak, Gizem, Mlody, Barbara, Singh, Manvendra, Semtner, Marcus, Mah, Nancy, Auré, Karine, Leong, Megan, Zabiegalov, Oleksandr, Lyras, Ekaterini-Maria, Pfiffer, Vanessa, Fauler, Beatrix, Eichhorst, Jenny, Wiesner, Burkhard, Huebner, Norbert, Priller, Josef, Mielke, Thorsten, Meierhofer, David, Izsvák, Zsuzsanna, Meier, Jochen C., Bouillaud, Frédéric, Adjaye, James, Schuelke, Markus, Wanker, Erich E., Lombès, Anne, Prigione, Alessandro

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Organization and dynamics of human mitochondrial DNA von Legros, Frédéric, Malka, Florence, Frachon, Paule, Lombès, Anne, Rojo, Manuel

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Membrane topology and mitochondrial targeting of mitofusins, ubiquitous mammalian homologs of the transmembrane GTPase Fzo von Rojo, Manuel, Legros, Frédéric, Chateau, Danielle, Lombès, Anne

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Use of H2O2 to Cause Oxidative Stress, the Catalase Issue von Ransy, Celine, Vaz, Clement, Lombes, Anne, Bouillaud, Frederic

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Clinical, biochemical and genetic spectrum of 70 patients with ACAD9 deficiency: is riboflavin supplementation effective? von Repp, Birgit M, Mastantuono, Elisa, Alston, Charlotte L, Schiff, Manuel, Haack, Tobias B, Rötig, Agnes, Ardissone, Anna, Lombès, Anne, Catarino, Claudia B, Diodato, Daria, Schottmann, Gudrun, Poulton, Joanna, Burlina, Alberto, Jonckheere, An, Munnich, Arnold, Rolinski, Boris, Ghezzi, Daniele, Rokicki, Dariusz, Wellesley, Diana, Martinelli, Diego, Wenhong, Ding, Lamantea, Eleonora, Ostergaard, Elsebet, Pronicka, Ewa, Pierre, Germaine, Smeets, Hubert J M, Wittig, Ilka, Scurr, Ingrid, de Coo, Irenaeus F M, Moroni, Isabella, Smet, Joél, Mayr, Johannes A, Dai, Lifang, de Meirleir, Linda, Schuelke, Markus, Zeviani, Massimo, Morscher, Raphael J, McFarland, Robert, Seneca, Sara, Klopstock, Thomas, Meitinger, Thomas, Wieland, Thomas, Strom, Tim M, Herberg, Ulrike, Ahting, Uwe, Sperl, Wolfgang, Nassogne, Marie-Cecile, Ling, Han, Fang, Fang, Freisinger, Peter, Van Coster, Rudy, Strecker, Valentina, Taylor, Robert W, Häberle, Johannes, Vockley, Jerry, Prokisch, Holger, Wortmann, Saskia

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ATAD3 gene cluster deletions cause cerebellar dysfunction associated with altered mitochondrial DNA and cholesterol metabolism von Desai, Radha, Frazier, Ann E, Durigon, Romina, Patel, Harshil, Jones, Aleck W, Dalla Rosa, Ilaria, Lake, Nicole J, Compton, Alison G, Mountford, Hayley S, Tucker, Elena J, Mitchell, Alice L R, Jackson, Deborah, Sesay, Abdul, Di Re, Miriam, van den Heuvel, Lambert P, Burke, Derek, Francis, David, Lunke, Sebastian, McGillivray, George, Mandelstam, Simone, Mochel, Fanny, Keren, Boris, Jardel, Claude, Turner, Anne M, Ian Andrews, P, Smeitink, Jan, Spelbrink, Johannes N, Heales, Simon J, Kohda, Masakazu, Ohtake, Akira, Murayama, Kei, Okazaki, Yasushi, Lombès, Anne, Holt, Ian J, Thorburn, David R, Spinazzola, Antonella

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Kinetic analysis of ATP hydrolysis by complex V in four murine tissues: Towards an assay suitable for clinical diagnosis von Haraux, Francis, Lombès, Anne

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Separate fusion of outer and inner mitochondrial membranes von Malka, Florence, Guillery, Olwenn, Cifuentes-Diaz, Carmen, Guillou, Emmanuelle, Belenguer, Pascale, Lombès, Anne, Rojo, Manuel

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Functional interplay between Parkin and Drp1 in mitochondrial fission and clearance von Buhlman, Lori, Damiano, Maria, Bertolin, Giulia, Ferrando-Miguel, Rosa, Lombès, Anne, Brice, Alexis, Corti, Olga

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Expanding and Underscoring the Hepato‐Encephalopathic Phenotype of QIL1/MIC13 von Russell, Bianca E., Whaley, Kaitlin G., Bove, Kevin E., Labilloy, Anatalia, Lombardo, Rachel C., Hopkin, Robert J., Leslie, Nancy D., Prada, Carlos, Assouline, Zahra, Barcia, Giulia, Bouchereau, Juliette, Chomton, Maryline, Debray, Dominique, Dorboz, Imen, Durand, Philippe, Gaignard, Pauline, Habes, Dalila, Jardel, Claude, Labarthe, François, Lévy, Jonathan, Lombès, Anne, Mehler‐Jacob, Claire, Melki, Judith, Menvielle, Laura, Munnich, Arnold, Mussini, Charlotte, Pichard, Samia, Rio, Marlène, Rötig, Agnès, Sissaoui, Samira, Slama, Abdelhamid, Miethke, Alexander G, Schiff, Manuel

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Annonacin, a lipophilic inhibitor of mitochondrial complex I, induces nigral and striatal neurodegeneration in rats: possible relevance for atypical parkinsonism in Guadeloupe von Champy, Pierre, Höglinger, Günter U., Féger, Jean, Gleye, Christophe, Hocquemiller, Reynald, Laurens, Alain, Guérineau, Vincent, Laprévote, Olivier, Medja, Fadia, Lombès, Anne, Michel, Patrick P., Lannuzel, Annie, Hirsch, Etienne C., Ruberg, Merle

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S100A8-mediated metabolic adaptation controls HIV-1 persistence in macrophages in vivo von Real, Fernando, Zhu, Aiwei, Huang, Boxin, Belmellat, Ania, Sennepin, Alexis, Vogl, Thomas, Ransy, Céline, Revol, Marc, Arrigucci, Riccardo, Lombès, Anne, Roth, Johannes, Gennaro, Maria Laura, Bouillaud, Frédéric, Cristofari, Sarra, Bomsel, Morgane

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QIL1 mutation causes MICOS disassembly and early onset fatal mitochondrial encephalopathy with liver disease von Guarani, Virginia, Jardel, Claude, Chrétien, Dominique, Lombès, Anne, Bénit, Paule, Labasse, Clémence, Lacène, Emmanuelle, Bourillon, Agnès, Imbard, Apolline, Benoist, Jean-François, Dorboz, Imen, Gilleron, Mylène, Goetzman, Eric S, Gaignard, Pauline, Slama, Abdelhamid, Elmaleh-Bergès, Monique, Romero, Norma B, Rustin, Pierre, Ogier de Baulny, Hélène, Paulo, Joao A, Harper, J Wade, Schiff, Manuel

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Mitochondrial Retrograde Signaling Mediated by UCP2 Inhibits Cancer Cell Proliferation and Tumorigenesis von ESTEVES, Pauline, PECQUEUR, Claire, ALVES-GUERRA, Marie-Clotilde, RANSY, Céline, ESNOUS, Catherine, LENOIR, Véronique, BOUILLAUD, Frédéric, BULTEAU, Anne-Laure, LOMBES, Anne, PRIP-BUUS, Carina, RICQUIER, Daniel

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Mitochondrial fusion in human cells is efficient, requires the inner membrane potential, and is mediated by mitofusins von Legros, Frédéric, Lombès, Anne, Frachon, Paule, Rojo, Manuel

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The TOMM machinery is a molecular switch in PINK1 and PARK2/PARKIN-dependent mitochondrial clearance von Bertolin, Giulia, Ferrando-Miguel, Rosa, Jacoupy, Maxime, Traver, Sabine, Grenier, Karl, Greene, Andrew W, Dauphin, Aurélien, Waharte, François, Bayot, Aurélien, Salamero, Jean, Lombès, Anne, Bulteau, Anne-Laure, Fon, Edward A, Brice, Alexis, Corti, Olga

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Mitochondrial MDM2 Regulates Respiratory Complex I Activity Independently of p53 von Arena, Giuseppe, Cissé, Madi Yann, Pyrdziak, Samuel, Chatre, Laurent, Riscal, Romain, Fuentes, Maryse, Arnold, Jamie Jon, Kastner, Markus, Gayte, Laurie, Bertrand-Gaday, Christelle, Nay, Kevin, Angebault-Prouteau, Claire, Murray, Kerren, Chabi, Beatrice, Koechlin-Ramonatxo, Christelle, Orsetti, Béatrice, Vincent, Charles, Casas, François, Marine, Jean-Christophe, Etienne-Manneville, Sandrine, Bernex, Florence, Lombès, Anne, Cameron, Craig Eugene, Dubouchaud, Hervé, Ricchetti, Miria, Linares, Laetitia Karine, Le Cam, Laurent

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Common data elements for clinical research in mitochondrial disease: a National Institute for Neurological Disorders and Stroke project von Karaa, Amel, Rahman, Shamima, Lombès, Anne, Yu-Wai-Man, Patrick, Sheikh, Muniza K., Alai-Hansen, Sherita, Cohen, Bruce H., Dimmock, David, Emrick, Lisa, Falk, Marni J., McCormack, Shana, Mirsky, David, Moore, Tony, Parikh, Sumit, Shoffner, John, Taivassalo, Tanja, Tarnopolsky, Mark, Tein, Ingrid, Odenkirchen, Joanne C., Goldstein, Amy

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Drug-Induced Alterations of Mitochondrial DNA Homeostasis in Steatotic and Nonsteatotic HepaRG Cells von Le Guillou, Dounia, Bucher, Simon, Begriche, Karima, Hoët, Delphine, Lombès, Anne, Labbe, Gilles, Fromenty, Bernard

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Engrailed protects mouse midbrain dopaminergic neurons against mitochondrial complex I insults von Joshi, Rajiv L, Hartmann, Andreas, Prochiantz, Alain, Alvarez-Fischer, Daniel, Fuchs, Julia, Castagner, François, Stettler, Olivier, Massiani-Beaudoin, Olivia, Moya, Kenneth L, Bouillot, Colette, Oertel, Wolfgang H, Lombès, Anne, Faigle, Wolfgang

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