Establishing normative data for the evaluation of cognitive performance in Huntington’s disease considering the impact of gender, age, language, and education von Mühlbäck, Alžbeta, Mana, Josef, Wallner, Michael, Frank, Wiebke, Lindenberg, Katrin S., Hoffmann, Rainer, Klempířová, Olga, Klempíř, Jiří, Landwehrmeyer, G. Bernhard, Bezdicek, Ondrej

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Fast-to-Slow Transition of Skeletal Muscle Contractile Function and Corresponding Changes in Myosin Heavy and Light Chain Formation in the R6/2 Mouse Model of Huntington's Disease von Hering, Tanja, Braubach, Peter, Landwehrmeyer, G Bernhard, Lindenberg, Katrin S, Melzer, Werner

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ALS-causing mutations differentially affect PGC-1α expression and function in the brain vs. peripheral tissues von Bayer, Hanna, Lang, Kerstin, Buck, Eva, Higelin, Julia, Barteczko, Lara, Pasquarelli, Noemi, Sprissler, Jasmin, Lucas, Tanja, Holzmann, Karlheinz, Demestre, Maria, Lindenberg, Katrin S, Danzer, Karin M, Boeckers, Tobias, Ludolph, Albert C, Dupuis, Luc, Weydt, Patrick, Witting, Anke

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General loss of proteostasis links Huntington disease to Cockayne syndrome von Wagner, Maximilian, Zhu, Gaojie, Khalid, Fatima, Phan, Tamara, Maity, Pallab, Lupu, Ludmila, Agyeman-Duah, Eric, Wiese, Sebastian, Lindenberg, Katrin S., Schön, Michael, Landwehrmeyer, G. Bernhard, Penzo, Marianna, Kochanek, Stefan, Scharffetter-Kochanek, Karin, Mulaw, Medhanie, Iben, Sebastian

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HAP40 protein levels are huntingtin-dependent and decrease in Huntington disease von Huang, Bin, Seefelder, Manuel, Buck, Eva, Engler, Tatjana, Lindenberg, Katrin S., Klein, Fabrice, Landwehrmeyer, G. Bernhard, Kochanek, Stefan

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Speech biomarkers in Huntington's disease: A cross‐sectional study in pre‐symptomatic, prodromal and early manifest stages von Kouba, Tomas, Frank, Wiebke, Tykalova, Tereza, Mühlbäck, Alzbeta, Klempíř, Jiří, Lindenberg, Katrin S., Landwehrmeyer, G. Bernhard, Rusz, Jan

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High-resolution respirometry of fine-needle muscle biopsies in pre-manifest Huntington's disease expansion mutation carriers shows normal mitochondrial respiratory function von Buck, Eva, Zügel, Martina, Schumann, Uwe, Merz, Tamara, Gumpp, Anja M, Witting, Anke, Steinacker, Jürgen M, Landwehrmeyer, G Bernhard, Weydt, Patrick, Calzia, Enrico, Lindenberg, Katrin S

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Serum Response Factor (SRF)-cofilin-actin signaling axis modulates mitochondrial dynamics von Beck, Henning, Flynn, Kevin, Lindenberg, Katrin S, Schwarz, Heinz, Bradke, Frank, Di Giovanni, Simone, Knöll, Bernd

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Two-point magnitude MRI for rapid mapping of brown adipose tissue and its application to the R6/2 mouse model of Huntington disease von Lindenberg, Katrin S, Weydt, Patrick, Müller, Hans-Peter, Bornstedt, Axel, Ludolph, Albert C, Landwehrmeyer, G Bernhard, Rottbauer, Wolfgang, Kassubek, Jan, Rasche, Volker

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Disease-modifying treatment approaches in Huntington disease : Past and future von Frank, Wiebke, Lindenberg, Katrin S, Mühlbäck, Alzbeta, Lewerenz, Jan, Landwehrmeyer, G Bernhard

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Proteases Acting on Mutant Huntingtin Generate Cleaved Products that Differentially Build Up Cytoplasmic and Nuclear Inclusions von Lunkes, Astrid, Lindenberg, Katrin S., Ben-Haı̈em, Léa, Weber, Chantal, Devys, Didier, Landwehrmeyer, G.Bernhard, Mandel, Jean-Louis, Trottier, Yvon

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A Protein Interaction Network Links GIT1, an Enhancer of Huntingtin Aggregation, to Huntington's Disease von Goehler, Heike, Lalowski, Maciej, Stelzl, Ulrich, Waelter, Stephanie, Stroedicke, Martin, Worm, Uwe, Droege, Anja, Lindenberg, Katrin S., Knoblich, Maria, Haenig, Christian, Herbst, Martin, Suopanki, Jaana, Scherzinger, Eberhard, Abraham, Claudia, Bauer, Bianca, Hasenbank, Renate, Fritzsche, Anja, Ludewig, Andreas H., Buessow, Konrad, Coleman, Sarah H., Gutekunst, Claire-Anne, Landwehrmeyer, Bernhard G., Lehrach, Hans, Wanker, Erich E.

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Altered Ca(2+) signaling in skeletal muscle fibers of the R6/2 mouse, a model of Huntington's disease von Braubach, Peter, Orynbayev, Murat, Andronache, Zoita, Hering, Tanja, Landwehrmeyer, Georg Bernhard, Lindenberg, Katrin S, Melzer, Werner

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Comparison of Sirtuin 3 Levels in ALS and Huntington's Disease-Differential Effects in Human Tissue Samples vs. Transgenic Mouse Models von Buck, Eva, Bayer, Hanna, Lindenberg, Katrin S, Hanselmann, Johannes, Pasquarelli, Noemi, Ludolph, Albert C, Weydt, Patrick, Witting, Anke

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Impairment of the ubiquitin-proteasome system by truncated cardiac myosin binding protein C mutants von SARIKAS, Antonio, CARRIER, Lucie, SCHENKE, Carolus, DOLL, Daniela, FLAVIGNY, Jeanne, LINDENBERG, Katrin S, ESCHENHAGEN, Thomas, ZOLK, Oliver

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Transgenic rat model of Huntington's disease von von Hörsten, Stephan, Schmitt, Ina, Nguyen, Huu Phuc, Holzmann, Carsten, Schmidt, Thorsten, Walther, Thomas, Bader, Michael, Pabst, Reinhard, Kobbe, Philipp, Krotova, Jana, Stiller, Detlef, Kask, Ants, Vaarmann, Annika, Rathke-Hartlieb, Silvia, Schulz, Jörg B., Grasshoff, Ute, Bauer, Ingrid, Vieira-Saecker, Ana Maria Menezes, Paul, Martin, Jones, Lesley, Lindenberg, Katrin S., Landwehrmeyer, Bernhard, Bauer, Andreas, Li, Xiao-Jiang, Riess, Olaf

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Mitochondrial impairment in patients and asymptomatic mutation carriers of Huntington's disease von Saft, Carsten, Zange, Jochen, Andrich, Jürgen, Müller, Klaus, Lindenberg, Katrin, Landwehrmeyer, Bernhard, Vorgerd, Matthias, Kraus, Peter H., Przuntek, Horst, Schöls, Ludger

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Myopathy as a first symptom of Huntington's disease in a Marathon runner von Kosinski, Christoph M., Schlangen, Christiane, Gellerich, Frank N., Gizatullina, Zemfira, Deschauer, Markus, Schiefer, Johannes, Young, Anne B., Landwehrmeyer, Georg Bernhard, Toyka, Klaus V., Sellhaus, Bernd, Lindenberg, Katrin S.

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Gene expression analysis on a single cell level in Purkinje cells of Huntington's disease transgenic mice von Euler, Philipp, Friedrich, Bernd, Ziegler, Ruhtraut, Kuhn, Alexandre, Lindenberg, Katrin S., Weiller, Cornelius, Zucker, Birgit

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Adenovirus vector-based in vitro neuronal cell model for Huntington's disease with human disease-like differential aggregation and degeneration von Dong, Xiaomin, Zong, Shan, Witting, Anke, Lindenberg, Katrin S., Kochanek, Stefan, Huang, Bin

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