Human mitochondrial ribosomes can switch their structural RNA composition von Rorbach, Joanna, Gao, Fei, Powell, Christopher A., D’Souza, Aaron, Lightowlers, Robert N., Minczuk, Michal, Chrzanowska-Lightowlers, Zofia M.

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The human RNA-binding protein RBFA promotes the maturation of the mitochondrial ribosome von Rozanska, Agata, Richter-Dennerlein, Ricarda, Rorbach, Joanna, Gao, Fei, Lewis, Richard J, Chrzanowska-Lightowlers, Zofia M, Lightowlers, Robert N

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SLIRP stabilizes LRPPRC via an RRM-PPR protein interface von Spåhr, Henrik, Rozanska, Agata, Li, Xinping, Atanassov, Ilian, Lightowlers, Robert N, Chrzanowska-Lightowlers, Zofia M A, Rackham, Oliver, Larsson, Nils-Göran

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A human mitochondrial poly(A) polymerase mutation reveals the complexities of post-transcriptional mitochondrial gene expression von Wilson, William C, Hornig-Do, Hue-Tran, Bruni, Francesco, Chang, Jeong Ho, Jourdain, Alexis A, Martinou, Jean-Claude, Falkenberg, Maria, Spåhr, Henrik, Larsson, Nils-Göran, Lewis, Richard J, Hewitt, Lorraine, Baslé, Arnaud, Cross, Harold E, Tong, Liang, Lebel, Robert R, Crosby, Andrew H, Chrzanowska-Lightowlers, Zofia M A, Lightowlers, Robert N

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Transmission of mitochondrial DNA disorders: possibilities for the future von Brown, DT, Herbert, M, Lamb, VK, Chinnery, PF, Taylor, RW, Lightowlers, RN, Craven, L, Cree, L, Gardner, JL, Turnbull, DM

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What causes mitochondrial DNA deletions in human cells? von Krishnan, Kim J, Reeve, Amy K, Samuels, David C, Chinnery, Patrick F, Blackwood, John K, Taylor, Robert W, Wanrooij, Sjoerd, Spelbrink, Johannes N, Lightowlers, Robert N, Turnbull, Doug M

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Reanalysis and revision of the Cambridge reference sequence for human mitochondrial DNA von Turnbull, Douglass M, Andrews, Richard M, Kubacka, Iwona, Chinnery, Patrick F, Lightowlers, Robert N, Howell, Neil

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Nuclear DNA-encoded tRNAs targeted into mitochondria can rescue a mitochondrial DNA mutation associated with the MERRF syndrome in cultured human cells von Kolesnikova, Olga A., Entelis, Nina S., Jacquin-Becker, Clarisse, Goltzene, Francine, Chrzanowska-Lightowlers, Zofia M., Lightowlers, Robert N., Martin, Robert P., Tarassov, Ivan

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Investigation of a pathogenic mtDNA microdeletion reveals a translation-dependent deadenylation decay pathway in human mitochondria von Temperley, Richard J., Seneca, Sara H., Tonska, Katarzyna, Bartnik, Ewa, Bindoff, Laurence A., Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M.A.

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Natural competence of mammalian mitochondria allows the molecular investigation of mitochondrial gene expression von Koulintchenko, Milana, Temperley, Richard J., Mason, Penelope A., Dietrich, André, Lightowlers, Robert N.

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Mismatch repair activity in mammalian mitochondria von Mason, Penelope A., Matheson, Elizabeth C., Hall, Andrew G., Lightowlers, Robert N.

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Serum-deprivation stimulates cap-binding by PARN at the expense of eIF4E, consistent with the observed decrease in mRNA stability von Seal, Ruth, Temperley, Richard, Wilusz, Jeffrey, Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M. A.

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The inheritance of mitochondrial DNA heteroplasmy: random drift, selection or both? von Chinnery, Patrick F, Thorburn, David R, Samuels, David C, White, Sarah L, Dahl, Hans-Heinrik M, Turnbull, Doug M, Lightowlers, Robert N, Howell, Neil

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Molecular pathology of MELAS and MERRF the relationship between mutation load and clinical phenotypes von CHINNERY, P. F, HOWELL, N, LIGHTOWLERS, R. N, TURNBULL, D. M

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Mammalian mitochondrial genetics: heredity, heteroplasmy and disease von Lightowlers, Robert N., Chinnery, Patrick F., Turnbull, Douglass M., Howell, Neil

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Multiple neonatal deaths due to a homoplasmic mitochondrial DNA mutation von Turnbull, Douglass M, McFarland, Robert, Clark, Kim M, Morris, Andrew A.M, Taylor, Robert W, Macphail, Sheila, Lightowlers, Robert N

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Messenger RNA stability in mitochondria: different means to an end von Gagliardi, Dominique, Stepien, Piotr P, Temperley, Richard J, Lightowlers, Robert N, Chrzanowska-Lightowlers, Zofia M.A

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Targeting peptide nucleic acid (PNA) oligomers to mitochondria within cells by conjugation to lipophilic cations: implications for mitochondrial DNA replication, expression and dis... von Muratovska, A, Lightowlers, R N, Taylor, R W, Turnbull, D M, Smith, R A, Wilce, J A, Martin, S W, Murphy, M P

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Role of mitochondrial DNA mutations in human aging: Implications for the central nervous system and muscle von Brierley, Elizabeth J., Johnson, Margaret A., Lightowlers, Robert N., James, Oliver F. W., Turnbull, Douglass M.

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Selective inhibition of mutant human mitochondrial DNA replication in vitro by peptide nucleic acids von Taylor, Robert W, Chinnery, Patrick F, Turnbull, Douglass M, Lightowlers, Robert N

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