The process of mammalian mitochondrial protein synthesis von Mai, Nicole, Chrzanowska-Lightowlers, Zofia M. A., Lightowlers, Robert N.

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Defective mitochondrial protease LonP1 can cause classical mitochondrial disease von Peter, Bradley, Waddington, Christie L, Oláhová, Monika, Sommerville, Ewen W, Hopton, Sila, Pyle, Angela, Champion, Michael, Ohlson, Monica, Siibak, Triinu, Chrzanowska-Lightowlers, Zofia M A, Taylor, Robert W, Falkenberg, Maria, Lightowlers, Robert N

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Human mitochondrial nucleases von Bruni, Francesco, Lightowlers, Robert N., Chrzanowska‐Lightowlers, Zofia M.

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Mitochondrial transplantation—a possible therapeutic for mitochondrial dysfunction?: Mitochondrial transfer is a potential cure for many diseases but proof of efficacy and safety i... von Lightowlers, Robert N, Chrzanowska‐Lightowlers, Zofia MA, Russell, Oliver M

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Human ERAL1 is a mitochondrial RNA chaperone involved in the assembly of the 28S small mitochondrial ribosomal subunit von Dennerlein, Sven, Rozanska, Agata, Wydro, Mateusz, Chrzanowska-Lightowlers, Zofia M A, Lightowlers, Robert N

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Messenger RNA delivery to mitoribosomes – hints from a bacterial toxin von Bruni, Francesco, Proctor‐Kent, Yasmin, Lightowlers, Robert N., Chrzanowska‐Lightowlers, Zofia M.

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GRSF1 Regulates RNA Processing in Mitochondrial RNA Granules von Jourdain, Alexis A., Koppen, Mirko, Wydro, Mateusz, Rodley, Chris D., Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M., Martinou, Jean-Claude

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Mitochondrial RNA maturation von Chrzanowska-Lightowlers, Zofia M, Lightowlers, Robert N

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The human RNA-binding protein RBFA promotes the maturation of the mitochondrial ribosome von Rozanska, Agata, Richter-Dennerlein, Ricarda, Rorbach, Joanna, Gao, Fei, Lewis, Richard J, Chrzanowska-Lightowlers, Zofia M, Lightowlers, Robert N

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High-resolution imaging reveals compartmentalization of mitochondrial protein synthesis in cultured human cells von Zorkau, Matthew, Albus, Christin A., Berlinguer-Palmini, Rolando, Chrzanowska-Lightowlers, Zofia M. A., Lightowlers, Robert N.

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Mitochondrial protein synthesis: Figuring the fundamentals, complexities and complications, of mammalian mitochondrial translation von Lightowlers, Robert N., Rozanska, Agata, Chrzanowska-Lightowlers, Zofia M.

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The Pseudouridine Synthase RPUSD4 Is an Essential Component of Mitochondrial RNA Granules von Zaganelli, Sofia, Rebelo-Guiomar, Pedro, Maundrell, Kinsey, Rozanska, Agata, Pierredon, Sandra, Powell, Christopher A., Jourdain, Alexis A., Hulo, Nicolas, Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M., Minczuk, Michal, Martinou, Jean-Claude

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REXO2 is an oligoribonuclease active in human mitochondria von Bruni, Francesco, Gramegna, Pasqua, Oliveira, Jorge M A, Lightowlers, Robert N, Chrzanowska-Lightowlers, Zofia M A

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SLIRP stabilizes LRPPRC via an RRM-PPR protein interface von Spåhr, Henrik, Rozanska, Agata, Li, Xinping, Atanassov, Ilian, Lightowlers, Robert N, Chrzanowska-Lightowlers, Zofia M A, Rackham, Oliver, Larsson, Nils-Göran

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Rescuing stalled mammalian mitoribosomes - what can we learn from bacteria? von Ayyub, Shreya Ahana, Gao, Fei, Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M.

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Hungry Codons Promote Frameshifting in Human Mitochondrial Ribosomes von Temperley, Richard, Richter, Ricarda, Dennerlein, Sven, Lightowlers, Robert N, Chrzanowska-Lightowlers, Zofia M

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A human mitochondrial poly(A) polymerase mutation reveals the complexities of post-transcriptional mitochondrial gene expression von Wilson, William C, Hornig-Do, Hue-Tran, Bruni, Francesco, Chang, Jeong Ho, Jourdain, Alexis A, Martinou, Jean-Claude, Falkenberg, Maria, Spåhr, Henrik, Larsson, Nils-Göran, Lewis, Richard J, Hewitt, Lorraine, Baslé, Arnaud, Cross, Harold E, Tong, Liang, Lebel, Robert R, Crosby, Andrew H, Chrzanowska-Lightowlers, Zofia M A, Lightowlers, Robert N

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Human mitochondrial ribosomes can switch their structural RNA composition von Rorbach, Joanna, Gao, Fei, Powell, Christopher A., D’Souza, Aaron, Lightowlers, Robert N., Minczuk, Michal, Chrzanowska-Lightowlers, Zofia M.

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A functional peptidyl-tRNA hydrolase, ICT1, has been recruited into the human mitochondrial ribosome von Richter, Ricarda, Rorbach, Joanna, Pajak, Aleksandra, Smith, Paul M, Wessels, Hans J, Huynen, Martijn A, Smeitink, Jan A, Lightowlers, Robert N, Chrzanowska-Lightowlers, Zofia M

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Defective Mitochondrial mRNA Maturation Is Associated with Spastic Ataxia von Crosby, Andrew H., Patel, Heema, Chioza, Barry A., Proukakis, Christos, Gurtz, Kay, Patton, Michael A., Sharifi, Reza, Harlalka, Gaurav, Simpson, Michael A., Dick, Katherine, Reed, Johanna A., Al-Memar, Ali, Chrzanowska-Lightowlers, Zofia M.A., Cross, Harold E., Lightowlers, Robert N.

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