Similarities and differences between the immunopathogenesis of COVID-19-related pediatric multisystem inflammatory syndrome and Kawasaki disease von Esteve-Sole, Ana, Anton, Jordi, Pino-Ramirez, Rosa Maria, Sanchez-Manubens, Judith, Fumadó, Victoria, Fortuny, Claudia, Rios-Barnes, María, Sanchez-de-Toledo, Joan, Girona-Alarcón, Mónica, Mosquera, Juan Manuel, Ricart, Silvia, Launes, Cristian, de Sevilla, Mariona Fernández, Jou, Cristina, Muñoz-Almagro, Carmen, González-Roca, Eva, Vergara, Andrea, Carrillo, Jorge, Juan, Manel, Cuadras, Daniel, Noguera-Julian, Antoni, Jordan, Iolanda, Alsina, Laia

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IRF8 Mutations and Human Dendritic-Cell Immunodeficiency von Hambleton, Sophie, Salem, Sandra, Bustamante, Jacinta, Bigley, Venetia, Boisson-Dupuis, Stéphanie, Azevedo, Joana, Fortin, Anny, Haniffa, Muzlifah, Ceron-Gutierrez, Lourdes, Bacon, Chris M, Menon, Geetha, Trouillet, Céline, McDonald, David, Carey, Peter, Ginhoux, Florent, Alsina, Laia, Zumwalt, Timothy J, Kong, Xiao-Fei, Kumararatne, Dinakantha, Butler, Karina, Hubeau, Marjorie, Feinberg, Jacqueline, Al-Muhsen, Saleh, Cant, Andrew, Abel, Laurent, Chaussabel, Damien, Doffinger, Rainer, Talesnik, Eduardo, Grumach, Anete, Duarte, Alberto, Abarca, Katia, Moraes-Vasconcelos, Dewton, Burk, David, Berghuis, Albert, Geissmann, Frédéric, Collin, Matthew, Casanova, Jean-Laurent, Gros, Philippe

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Evaluating the Genetics of Common Variable Immunodeficiency: Monogenetic Model and Beyond von de Valles-Ibáñez, Guillem, Esteve-Solé, Ana, Piquer, Mònica, González-Navarro, E Azucena, Hernandez-Rodriguez, Jessica, Laayouni, Hafid, González-Roca, Eva, Plaza-Martin, Ana María, Deyà-Martínez, Ángela, Martín-Nalda, Andrea, Martínez-Gallo, Mónica, García-Prat, Marina, Del Pino-Molina, Lucía, Cuscó, Ivón, Codina-Solà, Marta, Batlle-Masó, Laura, Solís-Moruno, Manuel, Marquès-Bonet, Tomàs, Bosch, Elena, López-Granados, Eduardo, Aróstegui, Juan Ignacio, Soler-Palacín, Pere, Colobran, Roger, Yagüe, Jordi, Alsina, Laia, Juan, Manel, Casals, Ferran

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Severe Autoinflammatory Manifestations and Antibody Deficiency Due to Novel Hypermorphic PLCG2 Mutations von Martín-Nalda, Andrea, Fortuny, Claudia, Rey, Lourdes, Bunney, Tom D., Alsina, Laia, Esteve-Solé, Ana, Bull, Daniel, Anton, Maria Carmen, Basagaña, María, Casals, Ferran, Deyá, Angela, García-Prat, Marina, Gimeno, Ramon, Juan, Manel, Martinez-Banaclocha, Helios, Martinez-Garcia, Juan J, Mensa-Vilaró, Anna, Rabionet, Raquel, Martin-Begue, Nieves, Rudilla, Francesc, Yagüe, Jordi, Estivill, Xavier, García-Patos, Vicente, Pujol, Ramon M., Soler-Palacín, Pere, Katan, Matilda, Pelegrín, Pablo, Colobran, Roger, Vicente, Asun, Arostegui, Juan I.

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Treg in inborn errors of immunity: gaps, knowns and future perspectives von Kennedy-Batalla, Rebeca, Acevedo, Daniel, Luo, Yiyi, Esteve-Solé, Ana, Vlagea, Alexandru, Correa-Rocha, Rafael, Seoane-Reula, Ma Elena, Alsina, Laia

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Immunomodulation in Sepsis: The Role of Endotoxin Removal by Polymyxin B-Immobilized Cartridge von Esteban, Elisabeth, Ferrer, Ricard, Alsina, Laia, Artigas, Antonio

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B Regulatory Cells: Players in Pregnancy and Early Life von Esteve-Solé, Ana, Luo, Yiyi, Vlagea, Alexandru, Deyà-Martínez, Ángela, Yagüe, Jordi, Plaza-Martín, Ana María, Juan, Manel, Alsina, Laia

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Changes in Treg and Breg cells in a healthy pediatric population von Luo, Yiyi, Acevedo, Daniel, Vlagea, Alexandru, Codina, Anna, García-García, Ana, Deyà-Martínez, Angela, Martí-Castellote, Celia, Esteve-Solé, Ana, Alsina, Laia

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Association between soluble angiotensin-converting enzyme 2 in saliva and SARS-CoV-2 infection: a cross-sectional study von Bru, Samuel, Brotons, Pedro, Jordan, Iolanda, Alsina, Laia, Henares, Desiree, Carballar, Reyes, de Sevilla, Mariona Fernandez, Barrabeig, Irene, Fumado, Victoria, Baro, Bàrbara, Martínez-Láinez, Joan Marc, Garcia-Garcia, Juan J., Bassat, Quique, Balaguer, Albert, Clotet, Josep, Launes, Cristian, Muñoz-Almagro, Carmen

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Immunological Changes in Blood of Newborns Exposed to Anti-TNF-α during Pregnancy von Esteve-Solé, Ana, Deyà-Martínez, Àngela, Teixidó, Irene, Ricart, Elena, Gompertz, Macarena, Torradeflot, Maria, de Moner, Noemí, Gonzalez, Europa Azucena, Plaza-Martin, Ana Maria, Yagüe, Jordi, Juan, Manel, Alsina, Laia

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Molecular analysis of the novel L243R mutation in STXBP2 reveals impairment of degranulation activity von Viñas-Giménez, Laura, Donadeu, Laura, Alsina, Laia, Rincón, Rafael, de la Campa, Elena Álvarez, Esteve-Sole, Ana, Català, Albert, Colobran, Roger, de la Cruz, Xavier, Sayós, Joan, Martínez-Gallo, Mónica

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Cost-minimization analysis of immunoglobulin treatment of primary immunodeficiency diseases in Spain von Alsina, Laia, Montoro, J. Bruno, Moral, Pedro Moral, Neth, Olaf, Pica, Marta Ortiz, Sánchez-Ramón, Silvia, Presa, María, Oyagüez, Itziar, Casado, Miguel Ángel, González-Granado, Luis Ignacio

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A Multi‑Center, Open‑Label, Single‑Arm Trial to Evaluate the Efficacy, Pharmacokinetics, and Safety and Tolerability of IGSC 20% in Subjects with Primary Immunodeficiency von Santamaria, Manuel, Neth, Olaf, Douglass, Jo A., Krivan, Gergely, Kobbe, Robin, Bernatowska, Ewa, Grigoriadou, Sofia, Bethune, Claire, Chandra, Anita, Horneff, Gerd, Borte, Michael, Sonnenschein, Anja, Kralickova, Pavlina, Ramón, Silvia Sánchez, Langguth, Daman, Gonzalez-Granado, Luis Ignacio, Alsina, Laia, Querolt, Montse, Griffin, Rhonda, Hames, Carrie, Mondou, Elsa, Price, Jeffrey, Sanz, Ana, Lin, Jiang

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Case report: Challenges in immune reconstitution following hematopoietic stem cell transplantation for CTLA-4 insufficiency-like primary immune regulatory disorders von Margarit-Soler, Adriana, Deyà-Martínez, Àngela, Canizales, Juan Torres, Vlagea, Alexandru, García-García, Ana, Marsal, Júlia, Del Castillo, Maria Trabazo, Planas, Sílvia, Simó, Sílvia, Esteve-Sole, Ana, Grande, María Suárez-Lledó, Badell, Isabel, Tarrats, Montserrat Rovira, Fernández-Avilés, Francesc, Alsina, Laia

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Case Report: Characterizing the Role of the STXBP2-R190C Monoallelic Mutation Found in a Patient With Hemophagocytic Syndrome and Langerhans Cell Histiocytosis von Viñas-Giménez, Laura, Rincón, Rafael, Colobran, Roger, de la Cruz, Xavier, Celis, Verónica Paola, Dapena, José Luis, Alsina, Laia, Sayós, Joan, Martínez-Gallo, Mónica

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Acute and long-term immune responses to SARS-CoV-2 infection in unvaccinated children and young adults with inborn errors of immunity von García-García, Ana, Fortuny, Claudia, Fumadó, Victoria, Jordan, Iolanda, Ruiz-López, Laura, González-Navarro, Europa Azucena, Egri, Natalia, Esteve-Solé, Ana, Luo, Yiyi, Vlagea, Alexandru, Cabedo, Manel Monsonís, Launes, Cristian, Soler, Aleix, Codina, Anna, Juan, Manel, Pascal, Mariona, Deyà-Martínez, Angela, Alsina, Laia

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Detrimental NFKB1 missense variants affecting the Rel-homology domain of p105/p50 von Fliegauf, Manfred, Kinnunen, Matias, Posadas-Cantera, Sara, Camacho-Ordonez, Nadezhda, Abolhassani, Hassan, Alsina, Laia, Atschekzei, Faranaz, Bogaert, Delfien J., Burns, Siobhan O., Church, Joseph A., Dückers, Gregor, Freeman, Alexandra F., Hammarström, Lennart, Hanitsch, Leif Gunnar, Kerre, Tessa, Kobbe, Robin, Sharapova, Svetlana O., Siepermann, Kathrin, Speckmann, Carsten, Steiner, Sophie, Verma, Nisha, Walter, Jolan E., Westermann-Clark, Emma, Goldacker, Sigune, Warnatz, Klaus, Varjosalo, Markku, Grimbacher, Bodo

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Correction to: A Multi-center, Open-Label, Single-Arm Trial to Evaluate the Efficacy, Pharmacokinetics, and Safety and Tolerability of IGSC 20% in Subjects with Primary Immunodefic... von Santamaria, Manuel, Neth, Olaf, Douglass, Jo A., Krivan, Gergely, Kobbe, Robin, Bernatowska, Ewa, Grigoriadou, Sofia, Bethune, Claire, Chandra, Anita, Horneff, Gerd, Borte, Michael, Sonnenschein, Anja, Kralickova, Pavlina, Ramón, Silvia Sánchez, Langguth, Daman D., Gonzalez‑Granado, Luis Ignacio, Alsina, Laia, Querolt, Montse, Griffin, Rhonda, Hames, Carrie, Mondou, Elsa, Price, Jeffrey, Sanz, Ana, Lin, Jiang

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The ABACHAI clinical trial protocol: Safety and efficacy of abatacept (s.c.) in patients with CTLA-4 insufficiency or LRBA deficiency: A non controlled phase 2 clinical trial von Krausz, Máté, Uhlmann, Annette, Rump, Ina Caroline, Ihorst, Gabriele, Goldacker, Sigune, Sogkas, Georgios, Posadas-Cantera, Sara, Schmidt, Reinhold, Feißt, Manuel, Alsina, Laia, Dybedal, Ingunn, Recher, Mike, Warnatz, Klaus, Grimbacher, Bodo

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Mycophenolate mofetil for autoimmune cytopenias in children: high rates of response in inborn errors of immunity von Berrueco, Rubén, González-Forster, Elisa, Deya-Martinez, Angela, Solsona, María, García-García, Ana, Calzada-Hernández, Joan, Yiyi, Luo, Vlagea, Alexandru, Ruiz-Llobet, Anna, Alsina, Laia

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