Synapse alterations precede neuronal damage and storage pathology in a human cerebral organoid model of CLN3-juvenile neuronal ceroid lipofuscinosis von Gomez-Giro, Gemma, Arias-Fuenzalida, Jonathan, Jarazo, Javier, Zeuschner, Dagmar, Ali, Muhammad, Possemis, Nina, Bolognin, Silvia, Halder, Rashi, Jäger, Christian, Kuper, Willemijn F E, van Hasselt, Peter M, Zaehres, Holm, Del Sol, Antonio, van der Putten, Herman, Schöler, Hans R, Schwamborn, Jens C

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A Case of Unexpected Adult-Onset Neurologic Decline in CLN3-Associated Retinal Degeneration von Kuper, Willemijn F. E, van Alfen, Claudia, van Eck, Linda, van den Broek, Brigitte T. A, Huisman, Albert, van Genderen, Maria M, van Hasselt, Peter M

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Quantifying lymphocyte vacuolization serves as a measure of CLN3 disease severity von Kuper, Willemijn F. E., Oostendorp, Marlies, van den Broek, Brigitte T. A., van Veghel, Karin, Nonkes, Lourens J. P., Nieuwenhuis, Edward E. S., Fuchs, Sabine A., Veenendaal, Tineke, Klumperman, Judith, Huisman, Albert, Nierkens, Stefan, van Hasselt, Peter M.

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Automatic quantification of lymphocyte vacuolization in peripheral blood smears of patients with Batten's disease (CLN3 disease) von Nonkes, Lourens J. P., Kuper, Willemijn F. E., Berrens‐Hogenbirk, Karin, Musson, Ruben E. A., Hasselt, Peter M., Huisman, Albert

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Subchronic (13-week) oral toxicity study in rats with fungal chitin-glucan from Aspergillus niger von Jonker, D., Kuper, C.F., Maquet, V., Nollevaux, G., Gautier, S.

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Motor function impairment is an early sign of CLN3 disease von Kuper, Willemijn F.E, van Alfen, Claudia, van Eck, Linda, Huijgen, Barbara C.H, Nieuwenhuis, Edward E.S, van Brussel, Marco, van Hasselt, Peter M

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The c.1A > C start codon mutation in CLN3 is associated with a protracted disease course von Kuper, Willemijn F. E., Alfen, Claudia, Eck, Linda, Man, Stella A., Willemsen, Marjolein H., Gassen, Koen L. I., Losekoot, Monique, Hasselt, Peter M.

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The Serosal Immune System of the Thorax in Toxicology von Kuper, Christine F, van Bilsen, Jolanda, Wijnands, Marcel V W

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Extended Histopathology in Immunotoxicity Testing: Interlaboratory Validation Studies von Germolec, D. R., Nyska, A., Kashon, M., Kuper, C. F., Portier, C., Kommineni, C., Johnson, K. A., Luster, M. I.

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Recognizing differentiating clinical signs of CLN3 disease (Batten disease) at presentation von Kuper, Willemijn F. E., Talsma, Herman E., Schooneveld, Mary J., Pott, Jan Willem R., Huijgen, Barbara C. H., Wit, Gerard C., Hasselt, Peter M., Genderen, Maria M.

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Beyond nephronophthisis: Retinal dystrophy in the absence of kidney dysfunction in childhood expands the clinical spectrum of CEP83 deficiency von Veldman, Bram C. F., Kuper, Willemijn F. E., Lilien, Marc, Schuurs‐Hoeijmakers, Janneke H. M., Marcelis, Carlo, Phan, Milan, Hettinga, Ymkje, Talsma, Herman E., Hasselt, Peter M., Haijes, Hanneke A.

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Timing of cognitive decline in CLN3 disease von Kuper, Willemijn F. E., van Alfen, Claudia, Rigterink, Roeliene H., Fuchs, Sabine A., van Genderen, Maria M., van Hasselt, Peter M.

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Histopathologic Approaches to Detect Changes Indicative of Immunotoxicity von Kuper, C. Frieke, Harleman, Johannes H., Richter-Reichelm, Hans B., Vos, Joseph G.

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Towards Understanding Behaviour and Emotions of Children with CLN3 Disease (Batten Disease): Patterns, Problems and Support for Child and Family von Honingh, Aline K, Kruithof, Yvonne L, Kuper, Willemijn F E, van Hasselt, Peter M, Sterkenburg, Paula S

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Toxicological behaviour and characterisation of nanomaterials: A systematic approach von van Acker, F., Mulderij, M., Wouters, M., Reinders, S., Krul, C., Kuper, F.

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The Accuracy of Extended Histopathology to Detect Immunotoxic Chemicals von Germolec, D. R., Kashon, M., Nyska, A., Kuper, C. F., Portier, C., Kommineni, C., Johnson, K. A., Luster, M. I.

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Ninety-day oral toxicity study of lycopene from Blakeslea trispora in rats von Jonker, D., Kuper, C.F., Fraile, N., Estrella, A., Rodrı́guez Otero, C.

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Health Risks Associated with Inhaled Nasal Toxicants von Feron, V. J., Arts, J. H. E., Kuper, C. F., Slootweg, P. J., Woutersen, R. A.

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Molecular Signature of Asthma-Enhanced Sensitivity to CuO Nanoparticle Aerosols from 3D Cell Model von Kooter, Ingeborg, Ilves, Marit, Gröllers-Mulderij, Mariska, Duistermaat, Evert, Tromp, Peter C, Kuper, Frieke, Kinaret, Pia, Savolainen, Kai, Greco, Dario, Karisola, Piia, Ndika, Joseph, Alenius, Harri

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Mechanistic Similarities between 3D Human Bronchial Epithelium and Mice Lung, Exposed to Copper Oxide Nanoparticles, Support Non‐Animal Methods for Hazard Assessment von Ndika, Joseph, Ilves, Marit, Kooter, Ingeborg M., Gröllers‐Mulderij, Mariska, Duistermaat, Evert, Tromp, Peter C., Kuper, Frieke, Kinaret, Pia, Greco, Dario, Karisola, Piia, Alenius, Harri

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