Aligning with the 3Rs: alternative models for research into muscle development and inherited myopathies von Mehmood, Hashir, Kasher, Paul R, Barrett-Jolley, Richard, Walmsley, Gemma L

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Dirty Fish Versus Squeaky Clean Mice: Dissecting Interspecies Differences Between Animal Models of Interferonopathy von Rutherford, Holly A, Kasher, Paul R, Hamilton, Noémie

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Editorial: Innovative models of stroke pathology von Crilly, Siobhan, Zille, Marietta, Kasher, Paul R, Modo, Michel

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Zebrafish drug screening identifies candidate therapies for neuroprotection after spontaneous intracerebral haemorrhage von Crilly, Siobhan, Parry-Jones, Adrian, Wang, Xia, Selley, Julian N, Cook, James, Tapia, Victor S, Anderson, Craig S, Allan, Stuart M, Kasher, Paul R

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Direct evidence for axonal transport defects in a novel mouse model of mutant spastin-induced hereditary spastic paraplegia (HSP) and human HSP patients von Kasher, Paul R, De Vos, Kurt J, Wharton, Stephen B, Manser, Catherine, Bennett, Ellen J, Bingley, Megan, Wood, Jonathan D, Milner, Roy, McDermott, Christopher J, Miller, Christopher C.J, Shaw, Pamela J, Grierson, Andrew J

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Characterization of samhd1 morphant zebrafish recapitulates features of the human type I interferonopathy Aicardi-Goutières syndrome von Kasher, Paul R, Jenkinson, Emma M, Briolat, Valérie, Gent, David, Morrissey, Catherine, Zeef, Leo A H, Rice, Gillian I, Levraud, Jean-Pierre, Crow, Yanick J

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Characterization of a mutant samhd1 zebrafish model implicates dysregulation of cholesterol biosynthesis in Aicardi-Goutières syndrome von Withers, Sarah E, Rowlands, Charlie F, Tapia, Victor S, Hedley, Frances, Mosneag, Ioana-Emilia, Crilly, Siobhan, Rice, Gillian I, Badrock, Andrew P, Hayes, Andrew, Allan, Stuart M, Briggs, Tracy A, Kasher, Paul R

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CLP1 Founder Mutation Links tRNA Splicing and Maturation to Cerebellar Development and Neurodegeneration von Schaffer, Ashleigh E., Eggens, Veerle R.C., Caglayan, Ahmet Okay, Reuter, Miriam S., Scott, Eric, Coufal, Nicole G., Silhavy, Jennifer L., Xue, Yuanchao, Kayserili, Hulya, Yasuno, Katsuhito, Rosti, Rasim Ozgur, Abdellateef, Mostafa, Caglar, Caner, Kasher, Paul R., Cazemier, J. Leonie, Weterman, Marian A., Cantagrel, Vincent, Cai, Na, Zweier, Christiane, Altunoglu, Umut, Satkin, N. Bilge, Aktar, Fesih, Tuysuz, Beyhan, Yalcinkaya, Cengiz, Caksen, Huseyin, Bilguvar, Kaya, Fu, Xiang-Dong, Trotta, Christopher R., Gabriel, Stacey, Reis, André, Gunel, Murat, Baas, Frank, Gleeson, Joseph G.

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Impairment of the tRNA-splicing endonuclease subunit 54 (tsen54) gene causes neurological abnormalities and larval death in zebrafish models of pontocerebellar hypoplasia von KASHER, Paul R, NAMAVAR, Yasmin, VAN TIJN, Paula, FLUITER, Kees, SIZAROV, Aleksander, KAMERMANS, Maarten, GRIERSON, Andrew J, ZIVKOVIC, Danica, BAAS, Frank

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Small 6q16.1 Deletions Encompassing POU3F2 Cause Susceptibility to Obesity and Variable Developmental Delay with Intellectual Disability von Kasher, Paul R., Schertz, Katherine E., Thomas, Megan, Jackson, Adam, Annunziata, Silvia, Ballesta-Martinez, María J., Campeau, Philippe M., Clayton, Peter E., Eaton, Jennifer L., Granata, Tiziana, Guillén-Navarro, Encarna, Hernando, Cristina, Laverriere, Caroline E., Liedén, Agne, Villa-Marcos, Olaya, McEntagart, Meriel, Nordgren, Ann, Pantaleoni, Chiara, Pebrel-Richard, Céline, Sarret, Catherine, Sciacca, Francesca L., Wright, Ronnie, Kerr, Bronwyn, Glasgow, Eric, Banka, Siddharth

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Brazilin is a natural product inhibitor of the NLRP3 inflammasome von McMahon, Emily, El-Sayed, Sherihan, Green, Jack, Hoyle, Christopher, FitzPatrick, Lorna, Jones, Emma V., Corrie, Eve, Kelly, Rebecca L., Challinor, Mairi, Freeman, Sally, Bryce, Richard A., Lawrence, Catherine B., Brough, David, Kasher, Paul R.

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Small-angle neutron scattering studies of alginate as biomineralizing agent and scale initiator von Dahdal, Y.N., Pipich, V., Rapaport, H., Oren, Y., Kasher, R., Schwahn, D.

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Small-Angle Neutron Scattering Studies of Mineralization on BSA Coated Citrate Capped Gold Nanoparticles Used as a Model Surface for Membrane Scaling in RO Wastewater Desalination von Dahdal, Y. N, Pipich, V, Rapaport, H, Oren, Y, Kasher, R, Schwahn, D

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Accumulation of GdCl3 in the feed of a reverse osmosis system during desalination as determined by neutron absorption von Schwahn, D., Pipich, V., Kasher, R., Oren, Y.

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Using zebrafish larval models to study brain injury, locomotor and neuroinflammatory outcomes following intracerebral haemorrhage [version 2; peer review: 2 approved] von Crilly, Siobhan, Njegic, Alexandra, Laurie, Sarah E, Fotiou, Elisavet, Hudson, Georgina, Barrington, Jack, Webb, Kirsty, Young, Helen L, Badrock, Andrew P, Hurlstone, Adam, Rivers-Auty, Jack, Parry-Jones, Adrian R, Allan, Stuart M, Kasher, Paul R

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FLT4 causes developmental disorders of the cardiovascular and lymphovascular systems via pleiotropic molecular mechanisms von Monaghan, Richard M, Naylor, Richard W, Flatman, Daisy, Kasher, Paul R, Williams, Simon G, Keavney, Bernard D

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Virtual screening-led design of inhibitor scaffolds for the NLRP3 inflammasome von El-Sayed, Sherihan, McMahon, Emily, Musleh, Sondos, Freeman, Sally, Brough, David, Kasher, Paul R., Bryce, Richard A.

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Impaired eIF5A function causes a Mendelian disorder that is partially rescued in model systems by spermidine von Faundes, Víctor, Jennings, Martin D., Crilly, Siobhan, Legraie, Sarah, Withers, Sarah E., Cuvertino, Sara, Davies, Sally J., Douglas, Andrew G. L., Fry, Andrew E., Harrison, Victoria, Amiel, Jeanne, Lehalle, Daphné, Newman, William G., Newkirk, Patricia, Ranells, Judith, Splitt, Miranda, Cross, Laura A., Saunders, Carol J., Sullivan, Bonnie R., Granadillo, Jorge L., Gordon, Christopher T., Kasher, Paul R., Pavitt, Graham D., Banka, Siddharth

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A type I interferon signature identifies bilateral striatal necrosis due to mutations in ADAR1 von Livingston, John H, Lin, Jean-Pierre, Dale, Russell C, Gill, Deepak, Brogan, Paul, Munnich, Arnold, Kurian, Manju A, Gonzalez-Martinez, Victoria, De Goede, Christian G E L, Falconer, Alastair, Forte, Gabriella, Jenkinson, Emma M, Kasher, Paul R, Szynkiewicz, Marcin, Rice, Gillian I, Crow, Yanick J

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RNA-Seq Dataset From Isolated Leukocytes Following Spontaneous Intracerebral Hemorrhage in Zebrafish Larvae von Crilly, Siobhan, Cooper, James, Bradford, Lauren, Prise, Ian E, Krishnan, Siddharth, Kasher, Paul R

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