Structural Requirements for Efficient Processing and Activation of Recombinant Human UDP-N-acetylglucosamine:Lysosomal-enzyme-N-acetylglucosamine-1-phosphotransferase von Kudo, Mariko, Canfield, William M.

Volltext

Structural basis for recognition of phosphodiester-containing lysosomal enzymes by the cation-independent mannose 6-phosphate receptor von Olson, Linda J., Peterson, Francis C., Castonguay, Alicia, Bohnsack, Richard N., Kudo, Mariko, Gotschall, Russell R., Canfield, William M., Volkman, Brian F., Dahms, Nancy M.

Volltext

Effect of a Liver X Receptor Agonist on Deposition and Lymphatic Absorption of Plant Sterols in Stroke-Prone Spontaneously Hypertensive Rats Having a Mutation in ATP-Binding Casset... von HAMADA, Tadateru, KUDO, Mariko, SATO, Masao, INOUE, Nao, NAGAO, Koji, IMAIZUMI, Katsumi, IKEDA, Ikuo

Volltext

Dietary soy protein isolate and its undigested high molecular fraction upregulate hepatic ATP-binding cassette transporter G5 and ATP-binding cassette transporter G8 mRNA and incre... von Ikeda, I.(Tohoku Univ., Sendai (Japan)), Kudo, M, Hamada, T, Nagao, K, Oshiro, Y, Kato, M, Sugawara, T, Yamahira, T, Ito, H, Tamaru, S, Sato, M, Imaizumi, K, Nagaoka, S, Yanagita, T

Volltext

Cation-independent Mannose 6-Phosphate Receptor von Bohnsack, Richard N., Song, Xuezheng, Olson, Linda J., Kudo, Mariko, Gotschall, Russell R., Canfield, William M., Cummings, Richard D., Smith, David F., Dahms, Nancy M.

Volltext

Phenotype and genotype in mucolipidoses II and III alpha/beta: a study of 61 probands von Cathey, S S, Leroy, J G, Wood, T, Eaves, K, Simensen, R J, Kudo, M, Stevenson, R E, Friez, M J

Volltext

Mucolipidosis II (I-Cell Disease) and Mucolipidosis IIIA (Classical Pseudo-Hurler Polydystrophy) Are Caused by Mutations in the GlcNAc-Phosphotransferase α/β–Subunits Precursor Gen... von Kudo, Mariko, Brem, Michael S., Canfield, William M.

Volltext

Glycoengineered Acid α-Glucosidase With Improved Efficacy at Correcting the Metabolic Aberrations and Motor Function Deficits in a Mouse Model of Pompe Disease von Zhu, Yunxiang, Jiang, Ji-Lei, Gumlaw, Nathan K, Zhang, Jinhua, Bercury, Scott D, Ziegler, Robin J, Lee, Karen, Kudo, Mariko, Canfield, William M, Edmunds, Timothy, Jiang, Canwen, Mattaliano, Robert J, Cheng, Seng H

Volltext

Functions of the α, β, and γ Subunits of UDP-GlcNAc:Lysosomal Enzyme N-Acetylglucosamine-1-phosphotransferase von Qian, Yi, Lee, Intaek, Lee, Wang-Sik, Qian, Meiqian, Kudo, Mariko, Canfield, William M., Lobel, Peter, Kornfeld, Stuart

Volltext

Characterization of the Major Core Structures of the α2→8-linked Polysialic Acid-containing Glycan Chains Present in Neural Cell Adhesion Molecule in Embryonic Chick Brains von Kudo, Mariko, Kitajima, Ken, Inoue, Sadako, Shiokawa, Koichiro, Morris, Howard R., Dell, Anne, Inoue, Yasuo

Volltext

Cation-independent mannose 6-phosphate receptor: a composite of distinct phosphomannosyl binding sites von Bohnsack, Richard N, Song, Xuezheng, Olson, Linda J, Kudo, Mariko, Gotschall, Russell R, Canfield, William M, Cummings, Richard D, Smith, David F, Dahms, Nancy M

Volltext

The α- and β-subunits of the Human UDP-N-acetylglucosamine:Lysosomal Enzyme Phosphotransferase Are Encoded by a Single cDNA von Kudo, Mariko, Bao, Ming, D'Souza, Anil, Ying, Fu, Pan, Huaqin, Roe, Bruce A., Canfield, William M.

Volltext

Domain 5 of the Cation-Independent Mannose 6-Phosphate Receptor Preferentially Binds Phosphodiesters (Mannose 6-Phosphate N-Acetylglucosamine Ester) von Chavez, Carrie A, Bohnsack, Richard N, Kudo, Mariko, Gotschall, Russell R, Canfield, William M, Dahms, Nancy M

Volltext

Clinical diagnosis using electrophoretic analysis von Sato, Hirohisa, Kudo, Mariko

Volltext

Clinical diagnosis using electrophoretic analysis von Sato, Hirohisa, Kudo, Mariko

Volltext

Rapid Identification of Digitalis purpurea Using Near-Infrared Reflectance Spectroscopy von KUDO, MARIKO, WATT, ROBERT A., MOFFAT, ANTHONY C.

Volltext

Man‐6‐P‐GlcNAc recognition by domain 5 of the cation‐independent mannose 6‐phosphate receptor von Castonguay, Alicia, Olson, Linda, Bohnsack, Richard, Kudo, Mariko, Gotschall, Russell, Canfield, William, Dahms, Nancy

Volltext

Species-specific differences in the processing of acid α-glucosidase are due to the amino acid identity at position 201 von Moreland, Rodney J., Higgins, Sheri, Zhou, AnQiang, VanStraten, Peter, Cauthron, Robert D., Brem, Michael, McLarty, Beverly J., Kudo, Mariko, Canfield, William M.

Volltext

Functions of the α, β, and γ Subunits of UDP-GlcNAc:Lysosomal Enzyme N-Acetylglucosamine-1-phosphotransferase von Yi Qian, Intaek Lee, Wang-Sik Lee, Meiqian Qian, Mariko Kudo, William M. Canfield, Peter Lobel, Stuart Kornfeld

Volltext

Molecular order in mucolipidosis II and III nomenclature von Cathey, Sara S., Kudo, Mariko, Tiede, Stephan, Raas-Rothschild, Annick, Braulke, Thomas, Beck, Michael, Taylor, Harold A., Canfield, William M., Leroy, Jules G., Neufeld, Elizabeth F., McKusick, Victor A.

Volltext