Enzyme replacement in a canine model of Hurler syndrome von Shull, R.M. (University of Tennessee, Knoxville, TN.), Kakkis, E.D, McEntee, M.F, Kania, S.A, Jonas, A.J, Neufeld, E.F

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Costello syndrome with pancreatic islet cell hyperplasia von Dickson, Patricia I., Briones, Norman Y., Baylen, Barry G., Jonas, Adam J., French, Samuel W., Lin, Henry J.

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Overexpression of the Human Lysosomal Enzyme α-L-Iduronidase in Chinese Hamster Ovary Cells von Kakkis, E.D., Matynia, A., Jonas, A.J., Neufeld, E.F.

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Cysteamine Therapy for Children with Nephropathic Cystinosis von Gahl, William A, Reed, George F, Thoene, Jess G, Schulman, Joseph D, Rizzo, William B, Jonas, Adam J, Denman, Daniel W, Schlesselman, James J, Corden, Brian J, Schneider, Jerry A

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Lysosomal sulphate transport is dependent upon sulphydryl groups von Chou, H F, Passage, M, Jonas, A J

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ATP stimulates lysosomal sulphate transport at neutral pH: evidence for phosphorylation of the lysosomal sulphate carrier von Chou, H F, Passage, M, Jonas, A J

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Sulfate transport by rat liver lysosomes von Jonas, A J, Jobe, H

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Vitamin B12 transport by rat liver lysosomal membrane vesicles von IDRISS, J.-M, JONAS, A. J

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Regulation of lysosomal sulfate transport by thyroid hormone von Chou, H F, Passage, M, Jonas, A J

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Cystine transport in purified rat liver lysosomes von Jonas, A J

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Circumvention of defective neutral amino acid transport in hartnup disease using tryptophan ethyl ester von JONAS, A. J, BUTLER, I. J

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ATP-dependent lysosomal cystine efflux is defective in cystinosis von Jonas, A J, Smith, M L, Schneider, J A

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Neutral-sugar transport by rat liver lysosomes von JONAS, A. J, CONRAD, P, JOBE, H

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N-acetyl-D-glucosamine countertransport in lysosomal membrane vesicles von Jonas, A J, Jobe, H

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Lysosomal sulfate transport: inhibitor studies von Koetters, Peter J., Chou, Hsu-Fang, Jonas, Adam J.

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Reconstitution of lysosomal sulfate transport in proteoliposomes von Koetters, Peter J., Chou, Hsu-Fang, Jonas, Adam J.

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Studies of lysosomal sialic acid metabolism: Retention of sialic acid by Salla disease lysosomes von Jonas, Adam J.

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Transport of N-acetyl-D-glucosamine and N-acetyl-D-galactosamine by Rat Liver Lysosomes von Jonas, A J, Speller, R J, Conrad, P B, Dubinsky, W P

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Low Breast Milk Phosphorus Concentration in Familial Hypophosphatemia von Jonas, Adam J, Dominguez, Barbara

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Nephropathic cystinosis with central nervous system involvement von Jonas, Adam J., Conley, Susan B., Marshall, Robert, Johnson, Rebecca A., Marks, Michael, Rosenberg, Harvey

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