Pseudomonas aeruginosa LasB protease impairs innate immunity in mice and humans by targeting a lung epithelial cystic fibrosis transmembrane regulator–IL-6–antimicrobial–repair pat... von Saint-Criq, Vinciane, Villeret, Bérengère, Bastaert, Fabien, Kheir, Saadé, Hatton, Aurélie, Cazes, Aurélie, Xing, Zhou, Sermet-Gaudelus, Isabelle, Garcia-Verdugo, Ignacio, Edelman, Aleksander, Sallenave, Jean-Michel

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Correlating genotype with phenotype using CFTR‐mediated whole‐cell Cl− currents in human nasal epithelial cells von Noel, Sabrina, Servel, Nathalie, Hatton, Aurélie, Golec, Anita, Rodrat, Mayuree, Ng, Demi R. S., Li, Hongyu, Pranke, Iwona, Hinzpeter, Alexandre, Edelman, Aleksander, Sheppard, David N., Sermet‐Gaudelus, Isabelle

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Predictive factors for lumacaftor/ivacaftor clinical response von Masson, Alexandra, Schneider-Futschik, Elena K., Baatallah, Nesrine, Nguyen-Khoa, Thao, Girodon, Emmanuelle, Hatton, Aurélie, Flament, Thomas, Le Bourgeois, Muriel, Chedevergne, Frederique, Bailly, Céline, Kyrilli, Sylvia, Achimastos, Diane, Hinzpeter, Alexandre, Edelman, Aleksander, Sermet-Gaudelus, Isabelle

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Reclassifying inconclusive diagnosis for cystic fibrosis with new generation sweat test von Nguyen-Khoa, Thao, Hatton, Aurélie, Drummond, David, Aoust, Laura, Schlatter, Joël, Martin, Clémence, Ramel, Sophie, Kiefer, Sébastien, Gachelin, Elsa, Stremler, Nathalie, Cosson, Laure, Gabsi, Asma, Remus, Natascha, Benhamida, Myriam, Hadchouel, Alice, Fajac, Isabelle, Munck, Anne, Girodon, Emmanuelle, Sermet-Gaudelus, Isabelle

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Author Correction: New insights into structure and function of bis-phosphinic acid derivatives and implications for CFTR modulation von Bitam, Sara, Elbahnsi, Ahmad, Creste, Geordie, Pranke, Iwona, Chevalier, Benoit, Berhal, Farouk, Hoffmann, Brice, Servel, Nathalie, Baatalah, Nesrine, Tondelier, Danielle, Hatton, Aurelie, Moquereau, Christelle, Faria Da Cunha, Mélanie, Pastor, Alexandra, Lepissier, Agathe, Hinzpeter, Alexandre, Mornon, Jean‑Paul, Prestat, Guillaume, Edelman, Aleksander, Callebaut, Isabelle, Gravier‑Pelletier, Christine, Sermet‑Gaudelus, Isabelle

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Antisense oligonucleotide-based drug development for Cystic Fibrosis patients carrying the 3849+10 kb C-to-T splicing mutation von Oren, Yifat S., Irony-Tur Sinai, Michal, Golec, Anita, Barchad-Avitzur, Ofra, Mutyam, Venkateshwar, Li, Yao, Hong, Jeong, Ozeri-Galai, Efrat, Hatton, Aurélie, Leibson, Chen, Carmel, Liran, Reiter, Joel, Sorscher, Eric J., Wilton, Steve D., Kerem, Eitan, Rowe, Steven M., Sermet-Gaudelus, Isabelle, Kerem, Batsheva

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The U UGA C sequence provides a favorable context to ELX-02 induced CFTR readthrough von Pranke, Iwona M., Varilh, Jessica, Hatton, Aurélie, Faucon, Caroline, Girodon, Emmanuelle, Dreano, Elise, Chevalier, Benoit, Karri, Sabrina, Reix, Philippe, Durieu, Isabelle, Bidou, Laure, Namy, Olivier, Taulan, Magali, Hinzpeter, Alexandre, Sermet-Gaudelus, Isabelle

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Sweat Chloride Testing and Nasal Potential Difference (NPD) Are Primary Outcome Parameters in Treatment with Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Modulators von Sermet-Gaudelus, Isabelle, Nguyen-Khoa, Thao, Hatton, Aurelie, Hayes, Kate, Pranke, Iwona

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Resolvin D1 regulates epithelial ion transport and inflammation in cystic fibrosis airways von Ringholz, Fiona C., Higgins, Gerard, Hatton, Aurélie, Sassi, Ali, Moukachar, Ahmad, Fustero-Torre, Coral, Hollenhorst, Monika, Sermet-Gaudelus, Isabelle, Harvey, Brian J., McNally, Paul, Urbach, Valerie

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Author Correction: Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis von Simonin, Juliette, Bille, Emmanuelle, Crambert, Gilles, Noel, Sabrina, Dreano, Elise, Edwards, Aurélie, Hatton, Aurélie, Pranke, Iwona, Villeret, Bérengère, Cottart, Charles-Henry, Vrel, Jean-Patrick, Urbach, Valérie, Baatallah, Nesrine, Hinzpeter, Alexandre, Golec, Anita, Touqui, Lhousseine, Nassif, Xavier, Galietta, Luis J. V., Planelles, Gabrielle, Sallenave, Jean-Michel, Edelman, Aleksander, Sermet-Gaudelus, Isabelle

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Modulation of chromatin remodelling induced by the freshwater cyanotoxin cylindrospermopsin in human intestinal caco-2 cells von Huguet, Antoine, Hatton, Aurélie, Villot, Romain, Quenault, Hélène, Blanchard, Yannick, Fessard, Valérie

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Isolation, cultivation, and application of primary respiratory epithelial cells obtained by nasal brushing, polyp samples, or lung explants von Golec, Anita, Pranke, Iwona, Scudieri, Paolo, Hayes, Kate, Dreano, Elise, Dunlevy, Fiona, Hatton, Aurelie, Downey, Damian G., Galietta, Luis, Sermet, Isabelle

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Analysis of nasal potential in murine cystic fibrosis models von da Cunha, Mélanie Faria, Simonin, Juliette, Sassi, Ali, Freund, Romain, Hatton, Aurélie, Cottart, Charles-Henry, Elganfoud, Nadia, Zoubairi, Rachid, Dragu, Corina, Jais, Jean Philippe, Hinzpeter, Alexandre, Edelman, Aleksander, Sermet-Gaudelus, Isabelle

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Correction of CFTR function in nasal epithelial cells from cystic fibrosis patients predicts improvement of respiratory function by CFTR modulators von Pranke, Iwona M., Hatton, Aurélie, Simonin, Juliette, Jais, Jean Philippe, Le Pimpec-Barthes, Françoise, Carsin, Ania, Bonnette, Pierre, Fayon, Michael, Stremler-Le Bel, Nathalie, Grenet, Dominique, Thumerel, Matthieu, Mazenq, Julie, Urbach, Valerie, Mesbahi, Myriam, Girodon-Boulandet, Emanuelle, Hinzpeter, Alexandre, Edelman, Aleksander, Sermet-Gaudelus, Isabelle

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Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis von Simonin, Juliette, Bille, Emmanuelle, Crambert, Gilles, Noel, Sabrina, Dreano, Elise, Edwards, Aurélie, Hatton, Aurélie, Pranke, Iwona, Villeret, Bérengère, Cottart, Charles-Henry, Vrel, Jean-Patrick, Urbach, Valérie, Baatallah, Nesrine, Hinzpeter, Alexandre, Golec, Anita, Touqui, Lhousseine, Nassif, Xavier, Galietta, Luis J. V, Planelles, Gabrielle, Sallenave, Jean-Michel, Edelman, Aleksander, Sermet-Gaudelus, Isabelle

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New insights into structure and function of bis-phosphinic acid derivatives and implications for CFTR modulation von Bitam, Sara, Elbahnsi, Ahmad, Creste, Geordie, Pranke, Iwona, Chevalier, Benoit, Berhal, Farouk, Hoffmann, Brice, Servel, Nathalie, Baatalah, Nesrine, Tondelier, Danielle, Hatton, Aurelie, Moquereau, Christelle, Faria Da Cunha, Mélanie, Pastor, Alexandra, Lepissier, Agathe, Hinzpeter, Alexandre, Mornon, Jean-Paul, Prestat, Guillaume, Edelman, Aleksander, Callebaut, Isabelle, Gravier-Pelletier, Christine, Sermet-Gaudelus, Isabelle

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Systemic bis-phosphinic acid derivative restores chloride transport in Cystic Fibrosis mice von da Cunha, Mélanie Faria, Pranke, Iwona, Sassi, Ali, Schreiweis, Christiane, Moriceau, Stéphanie, Vidovic, Dragana, Hatton, Aurélie, Carlon, Mariane Sylvia, Creste, Geordie, Berhal, Farouk, Prestat, Guillaume, Freund, Romain, Odolczyk, Norbert, Jais, Jean Philippe, Gravier-Pelletier, Christine, Zielenkiewicz, Piotr, Jullien, Vincent, Hinzpeter, Alexandre, Oury, Franck, Edelman, Aleksander, Sermet-Gaudelus, Isabelle

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Putting bicarbonate on the spot: pharmacological insights for CFTR correction in the airway epithelium von Zajac, Miroslaw, Lepissier, Agathe, Dréano, Elise, Chevalier, Benoit, Hatton, Aurélie, Kelly-Aubert, Mairead, Guidone, Daniela, Planelles, Gabrielle, Edelman, Aleksander, Girodon, Emmanuelle, Hinzpeter, Alexandre, Crambert, Gilles, Pranke, Iwona, Galietta, Luis J V, Sermet-Gaudelus, Isabelle

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Might Brushed Nasal Cells Be a Surrogate for CFTR Modulator Clinical Response? von Pranke, Iwona, Hatton, Aurelie, Masson, Alexandra, Flament, Thomas, Le Bourgeois, Muriel, Chedevergne, Frederique, Bailly, Celine, Urbach, Valerie, Hinzpeter, Alexandre, Edelman, Aleksander, Sermet-Gaudelus, Isabelle

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Genetic deletion of keratin 8 corrects the altered bone formation and osteopenia in a mouse model of cystic fibrosis von Le Henaff, Carole, Faria Da Cunha, Mélanie, Hatton, Aurélie, Tondelier, Danielle, Marty, Caroline, Collet, Corinne, Zarka, Mylène, Geoffroy, Valérie, Zatloukal, Kurt, Laplantine, Emmanuel, Edelman, Aleksander, Sermet-Gaudelus, Isabelle, Marie, Pierre J

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