Glibenclamide reverses cardiovascular abnormalities of Cantu syndrome driven by KATP channel overactivity von McClenaghan, Conor, Huang, Yan, Yan, Zihan, Harter, Theresa M, Halabi, Carmen M, Chalk, Rod, Kovacs, Attila, van Haaften, Gijs, Remedi, Maria S, Nichols, Colin G

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Pathophysiological Consequences of KATP Channel Overactivity and Pharmacological Response to Glibenclamide in Skeletal Muscle of a Murine Model of Cantù Syndrome von Scala, Rosa, Maqoud, Fatima, Zizzo, Nicola, Mele, Antonietta, Camerino, Giulia Maria, Zito, Francesco Alfredo, Ranieri, Girolamo, McClenaghan, Conor, Harter, Theresa M, Nichols, Colin G, Tricarico, Domenico

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Zoledronic Acid Blocks Overactive Kir6.1/SUR2-Dependent KATP Channels in Skeletal Muscle and Osteoblasts in a Murine Model of Cantú Syndrome von Scala, Rosa, Maqoud, Fatima, McClenaghan, Conor, Harter, Theresa M., Perrone, Maria Grazia, Scilimati, Antonio, Nichols, Colin G., Tricarico, Domenico

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Consequences of SUR2[A478V] Mutation in Skeletal Muscle of Murine Model of Cantu Syndrome von Scala, Rosa, Maqoud, Fatima, Zizzo, Nicola, Passantino, Giuseppe, Mele, Antonietta, Camerino, Giulia Maria, McClenaghan, Conor, Harter, Theresa M., Nichols, Colin G., Tricarico, Domenico

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Cardiovascular consequences of KATP overactivity in Cantu syndrome von Huang, Yan, McClenaghan, Conor, Harter, Theresa M, Hinman, Kristina, Halabi, Carmen M, Matkovich, Scot J, Zhang, Haixia, Brown, G Schuyler, Mecham, Robert P, England, Sarah K, Kovacs, Attila, Remedi, Maria S, Nichols, Colin G

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Hypotension Due to Kir6.1 Gain‐of‐Function in Vascular Smooth Muscle von Li, Anlong, Knutsen, Russell H., Zhang, Haixia, Osei‐Owusu, Patrick, Moreno‐Dominguez, Alex, Harter, Theresa M., Uchida, Keita, Remedi, Maria S., Dietrich, Hans H., Bernal‐Mizrachi, Carlos, Blumer, Kendall J., Mecham, Robert P., Koster, Joseph C., Nichols, Colin G.

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The Mechanism of High-Output Cardiac Hypertrophy Arising From Potassium Channel Gain-of-Function in Cantú Syndrome von McClenaghan, Conor, Huang, Yan, Matkovich, Scot J, Kovacs, Attila, Weinheimer, Carla J, Perez, Ron, Broekelmann, Thomas J, Harter, Theresa M, Lee, Jin-Moo, Remedi, Maria S, Nichols, Colin G

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Functional studies of aldo-keto reductases in Saccharomyces cerevisiae von Chang, Qing, Griest, Terry A., Harter, Theresa M., Mark Petrash, J.

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Complex consequences of Cantu syndrome SUR2 variant R1154Q in genetically modified mice von Zhang, Haixia, Hanson, Alex, de Almeida, Tobias Scherf, Emfinger, Christopher, McClenaghan, Conor, Harter, Theresa, Yan, Zihan, Cooper, Paige E, Brown, G Schuyler, Arakel, Eric C, Mecham, Robert P, Kovacs, Atilla, Halabi, Carmen M, Schwappach, Blanche, Remedi, Maria S, Nichols, Colin G

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Aldo-Keto Reductases in the Eye von Palla, Suryanarayana, Huang, Shun Ping, Ruzycki, Philip, Varma, Ross Arjun, Harter, Theresa, Reddy, Geereddy Bhanuprakash, Petrash, J. Mark

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Pharmacological Approaches for Targeting Cardiovascular and Skeletal Muscle KATP Channelopathies von McClenaghan, Conor, Huang, Yan, Yan, Zihan, Roeglin, Jacob, Harter, Theresa, Halabi, Carmen, Remedi, Maria S., Nichols, Colin G.

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The Mechanism of Cardiovascular Pathophysiology in Cantu Syndrome and Response to Glibenclamide in Novel KATP Channel Mutant Mouse Models von McClenaghan, Conor, Huang, Yan, Halabi, Carmen, Harter, Theresa, Mecham, Robert P., Remedi, Maria S., Nichols, Colin G.

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Glibenclamide reverses cardiovascular abnormalities of Cantu syndrome driven by [K.sub.ATP] channel overactivity von McClenaghan, Conor, Huang, Yan, Yan, Zihan, Harter, Theresa M, Halabi, Carmen M, Chalk, Rod, Kovacs, Attila, van Haaften, Gijs, Remedi, Maria S, Nichols, Colin G

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Kinetic Studies of FR-1, a Growth Factor-Inducible Aldo-Keto Reductase von Srivastava, Sanjay, Harter, Theresa M, Chandra, Animesh, Bhatnagar, Aruni, Srivastava, Satish K, Petrash, J. Mark

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ABCC9-related Intellectual disability Myopathy Syndrome is a KATP channelopathy with loss-of-function mutations in ABCC9 von Smeland, Marie F., McClenaghan, Conor, Roessler, Helen I., Savelberg, Sanne, Hansen, Geir Åsmund Myge, Hjellnes, Helene, Arntzen, Kjell Arne, Müller, Kai Ivar, Dybesland, Andreas Rosenberger, Harter, Theresa, Sala-Rabanal, Monica, Emfinger, Chris H., Huang, Yan, Singareddy, Soma S., Gunn, Jamie, Wozniak, David F., Kovacs, Attila, Massink, Maarten, Tessadori, Federico, Kamel, Sarah M., Bakkers, Jeroen, Remedi, Maria S., Van Ghelue, Marijke, Nichols, Colin G., van Haaften, Gijs

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Zoledronic Acid Blocks Overactive Kir6.1/SUR2-Dependent K[sub.ATP] Channels in Skeletal Muscle and Osteoblasts in a Murine Model of Cantú Syndrome von Scala, Rosa, Maqoud, Fatima, McClenaghan, Conor, Harter, Theresa M, Perrone, Maria Grazia, Scilimati, Antonio, Nichols, Colin G, Tricarico, Domenico

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Zoledronic Acid Blocks Overactive Kir6.1/SUR2-Dependent K ATP Channels in Skeletal Muscle and Osteoblasts in a Murine Model of Cantú Syndrome von Scala, Rosa, Maqoud, Fatima, McClenaghan, Conor, Harter, Theresa M, Perrone, Maria Grazia, Scilimati, Antonio, Nichols, Colin G, Tricarico, Domenico

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Aldo–keto reductases as modulators of stress response von Chang, Qing, Harter, Theresa M, Rikimaru, Loryn T, Petrash, J.Mark

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Abstract 011: Cardiovascular Consequences of Cantu Syndrome and Response to Glibenclamide Treatment in Two Novel KATP Channel Mutant Mouse Models von McClenaghan, Conor, Huang, Yan, Harter, Theresa, Brown, G. Schuyler, Hinman, Kristina, Halabi, Carmen, Matkovich, Scot, Mecham, Robert P, Weinheimer, Carla J, Kovacs, Attila, England, Sarah, Remedi, Maria S, Nichols, Colin G

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ABCC9-related Intellectual disability Myopathy Syndrome is a KATP channelopathy with loss-of-function mutations in ABCC9 von Smeland, Marie F, McClenaghan, Conor, Roessler, Helen I, Savelberg, Sanne, Hansen, Geir Åsmund Myge, Hjellnes, Helene, Arntzen, Kjell Arne, Müller, Kai Ivar, Dybesland, Andreas Rosenberger, Harter, Theresa, Sala-Rabanal, Monica, Emfinger, Chris H, Huang, Yan, Singareddy, Soma S, Gunn, Jamie, Wozniak, David F, Kovacs, Attila, Massink, Maarten, Tessadori, Federico, Kamel, Sarah M, Bakkers, Jeroen, Remedi, Maria S, Van Ghelue, Marijke, Nichols, Colin G, van Haaften, Gijs

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