Glucosylceramide synthase inhibition protects against cardiac hypertrophy in chronic kidney disease von Baccam, Gabriel C., Xie, Jian, Jin, Xin, Park, Hyejung, Wang, Bing, Husson, Hervé, Ibraghimov-Beskrovnaya, Oxana, Huang, Chou-Long

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Inhibition of glucosylceramide accumulation results in effective blockade of polycystic kidney disease in mouse models von Leonard, John P, Natoli, Thomas A, Rogers, Kelly A, Russo, Ryan J, Ibraghimov-Beskrovnaya, Oxana, Husson, Hervé, Budman, Yeva, Wang, Bing, Bukanov, Nikolay O, Smith, Laurie A, Belenky, Alexei, Komarnitsky, Svetlana, Shayman, James A, Ledbetter, Steven R, Dackowski, William R

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CaMKII as a pathological mediator of ER stress, oxidative stress, and mitochondrial dysfunction in a murine model of nephronophthisis von Bracken, Christina, Beauverger, Philippe, Duclos, Olivier, Russo, Ryan J, Rogers, Kelly A, Husson, Hervé, Natoli, Thomas A, Ledbetter, Steven R, Janiak, Philip, Ibraghimov-Beskrovnaya, Oxana, Bukanov, Nikolay O

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Correction of cilia structure and function alleviates multi-organ pathology in Bardet–Biedl syndrome mice von Husson, Hervé, Bukanov, Nikolay O, Moreno, Sarah, Smith, Mandy M, Richards, Brenda, Zhu, Cheng, Picariello, Tyler, Park, Hyejung, Wang, Bing, Natoli, Thomas A, Smith, Laurie A, Zanotti, Stefano, Russo, Ryan J, Madden, Stephen L, Klinger, Katherine W, Modur, Vijay, Ibraghimov-Beskrovnaya, Oxana

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Anti-microRNA-21 Therapy on Top of ACE Inhibition Delays Renal Failure in Alport Syndrome Mouse Models von Rubel, Diana, Boulanger, Joseph, Craciun, Florin, Xu, Ethan Y, Zhang, Yanqin, Phillips, Lucy, Callahan, Michelle, Weber, William, Song, Wenping, Ngai, Nicholas, Bukanov, Nikolay O, Shi, Xingyi, Hariri, Ali, Husson, Hervé, Ibraghimov-Beskrovnaya, Oxana, Liu, Shiguang, Gross, Oliver

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Reduction of ciliary length through pharmacologic or genetic inhibition of CDK5 attenuates polycystic kidney disease in a model of nephronophthisis von Husson, Hervé, Moreno, Sarah, Smith, Laurie A, Smith, Mandy M, Russo, Ryan J, Pitstick, Rose, Sergeev, Mikhail, Ledbetter, Steven R, Bukanov, Nikolay O, Lane, Monica, Zhang, Kate, Billot, Katy, Carlson, George, Shah, Jagesh, Meijer, Laurent, Beier, David R, Ibraghimov-Beskrovnaya, Oxana

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Mechanical stimuli induce cleavage and nuclear translocation of the polycystin-1 C terminus von Chauvet, Veronique, Tian, Xin, Husson, Herve, Grimm, David H, Wang, Tong, Hiesberger, Thomas, Hieseberger, Thomas, Igarashi, Peter, Bennett, Anton M, Ibraghimov-Beskrovnaya, Oxana, Somlo, Stefan, Caplan, Michael J

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Mechanical stimuli induce cleavage and nuclear translocation of the polycystin-1 C terminus von Chauvet, Veronique, Tian, Xin, Husson, Herve, Grimm, David H., Wang, Tong, Hieseberger, Thomas, Igarashi, Peter, Bennett, Anton M., Ibraghimov-Beskrovnaya, Oxana, Somlo, Stefan, Caplan, Michael J.

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Glucosylceramide synthase modulation ameliorates murine renal pathologies and promotes macrophage effector function in vitro von Cheong, Agnes, Craciun, Florin, Husson, Hervé, Gans, Joseph, Escobedo, Javier, Chang, Yi-Chien, Guo, Lilu, Goncalves, Mariana, Kaplan, Nathan, Smith, Laurie A., Moreno, Sarah, Boulanger, Joseph, Liu, Shiguang, Saleh, Jacqueline, Zhang, Mindy, Blazier, Anna S., Qiu, Weiliang, Macklin, Andrew, Iyyanki, Tejaswi, Chatelain, Clément, Khader, Shameer, Natoli, Thomas A., Ibraghimov-Beskrovnaya, Oxana, Ofengeim, Dimitry, Proto, Jonathan D.

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Development of polycystic kidney disease in juvenile cystic kidney mice : Insights into pathogenesis, ciliary abnormalities, and common features with human disease von SMITH, Laurie A, BUKANOV, Nikolay O, HUSSON, Hervé, RUSSO, Ryan J, BARRY, Tiffany C, TAYLOR, Ava L, BEIER, David R, IBRAGHIMOV-BESKROVNAYA, Oxana

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Loss of GM3 synthase gene, but not sphingosine kinase 1, is protective against murine nephronophthisis-related polycystic kidney disease von NATOLI, Thomas A, HUSSON, Hervé, IBRAGHIMOV-BESKROVNAYA, Oxana, ROGERS, Kelly A, SMITH, Laurie A, BING WANG, BUDMAN, Yeva, BUKANOV, Nikolay O, LEDBETTER, Steven R, KLINGER, Katherine W, LEONARD, John P

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Pkd1 and Nek8 mutations affect cell-cell adhesion and cilia in cysts formed in kidney organ cultures von Natoli, Thomas A, Gareski, Tiffany C, Dackowski, William R, Smith, Laurie, Bukanov, Nikolay O, Russo, Ryan J, Husson, Herve, Matthews, Douglas, Piepenhagen, Peter, Ibraghimov-Beskrovnaya, Oxana

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Exome Capture Reveals ZNF423 and CEP164 Mutations, Linking Renal Ciliopathies to DNA Damage Response Signaling von Chaki, Moumita, Airik, Rannar, Ghosh, Amiya K., Giles, Rachel H., Chen, Rui, Slaats, Gisela G., Wang, Hui, Hurd, Toby W., Zhou, Weibin, Cluckey, Andrew, Gee, Heon Yung, Ramaswami, Gokul, Hong, Chen-Jei, Hamilton, Bruce A., Červenka, Igor, Ganji, Ranjani Sri, Bryja, Vitezslav, Arts, Heleen H., van Reeuwijk, Jeroen, Oud, Machteld M., Letteboer, Stef J.F., Roepman, Ronald, Husson, Hervé, Ibraghimov-Beskrovnaya, Oxana, Yasunaga, Takayuki, Walz, Gerd, Eley, Lorraine, Sayer, John A., Schermer, Bernhard, Liebau, Max C., Benzing, Thomas, Le Corre, Stephanie, Drummond, Iain, Janssen, Sabine, Allen, Susan J., Natarajan, Sivakumar, O’Toole, John F., Attanasio, Massimo, Saunier, Sophie, Antignac, Corinne, Koenekoop, Robert K., Ren, Huanan, Lopez, Irma, Nayir, Ahmet, Stoetzel, Corinne, Dollfus, Helene, Massoudi, Rustin, Gleeson, Joseph G., Andreoli, Sharon P., Doherty, Dan G., Lindstrad, Anna, Golzio, Christelle, Katsanis, Nicholas, Pape, Lars, Abboud, Emad B., Al-Rajhi, Ali A., Lewis, Richard A., Omran, Heymut, Lee, Eva Y.-H.P., Wang, Shaohui, Sekiguchi, JoAnn M., Saunders, Rudel, Johnson, Colin A., Garner, Elizabeth, Vanselow, Katja, Andersen, Jens S., Shlomai, Joseph, Nurnberg, Gudrun, Nurnberg, Peter, Levy, Shawn, Smogorzewska, Agata, Otto, Edgar A., Hildebrandt, Friedhelm

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Differences in the timing and magnitude of Pkd1 gene deletion determine the severity of polycystic kidney disease in an orthologous mouse model of ADPKD von Rogers, Kelly A., Moreno, Sarah E., Smith, Laurie A., Husson, Hervé, Bukanov, Nikolay O., Ledbetter, Steven R., Budman, Yeva, Lu, Yuefeng, Wang, Bing, Ibraghimov‐Beskrovnaya, Oxana, Natoli, Thomas A.

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Gene expression profiling of B cell chronic lymphocytic leukemia reveals a homogeneous phenotype related to memory B cells von Klein, U, Tu, Y, Stolovitzky, G A, Mattioli, M, Cattoretti, G, Husson, H, Freedman, A, Inghirami, G, Cro, L, Baldini, L, Neri, A, Califano, A, Dalla-Favera, R

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CXCL13 (BCA‐1) is produced by follicular lymphoma cells: role in the accumulation of malignant B cells von Husson, Hervé, S. Freedman, Arnold, A. Cardoso, Angelo, Schultze, Joachim, Munoz, Olivier, Strola, Giuliana, Kutok, Jeffery, G. Carideo, Elizabeth, De Beaumont, Rosalie, Caligaris‐Cappio, Federico, Ghia, Paolo

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Functional polycystin-1 expression is developmentally regulated during epithelial morphogenesis in vitro: downregulation and loss of membrane localization during cystogenesis von O. Bukanov, Nikolay, Husson, Hervé, Dackowski, William R., Lawrence, Brandon D., Clow, Patricia A., Roberts, Bruce L., Klinger, Katherine W., Ibraghimov-Beskrovnaya, Oxana

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MCP‐1 modulates chemotaxis by follicular lymphoma cells von Husson, Hervé, Carideo, Elizabeth G., Cardoso, Angelo A., Lugli, Serena M., Neuberg, Donna, Munoz, Olivier, De Leval, Laurence, Schultze, Joachim, Freedman, Arnold S.

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Differential expression and signaling of CBL and CBL-B in BCR/ABL transformed cells von SATTLER, Martin, PRIDE, Yuri B, QUINNAN, Laura R, VERMA, Shalini, MALOUF, Nicole A, HUSSON, Hervé, SALGIA, Ravi, LIPKOWITZ, Stanley, GRIFFIN, James D

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Gene expression profiling of follicular lymphoma and normal germinal center B cells using cDNA arrays von Husson, Hervé, Carideo, Elizabeth G., Neuberg, Donna, Schultze, Joachim, Munoz, Olivier, Marks, Peter W., Donovan, John W., Chillemi, Antoinette C., O'Connell, Peter, Freedman, Arnold S.

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