Excess Serum Interleukin‐18 Distinguishes Patients With Pathogenic Mutations in PSTPIP1 von Stone, Deborah L., Ombrello, Amanda, Arostegui, Juan I., Schneider, Corinne, Dang, Vinh, Jesus, Adriana, Girard‐Guyonvarc'h, Charlotte, Gabay, Cem, Lee, Wonyong, Chae, Jae Jin, Aksentijevich, Ivona, Goldbach‐Mansky, Raphaela T., Kastner, Daniel L., Canna, Scott W.

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Pharmacokinetics, Pharmacodynamics, and Proposed Dosing of the Oral JAK1 and JAK2 Inhibitor Baricitinib in Pediatric and Young Adult CANDLE and SAVI Patients von Kim, Hanna, Brooks, Kristina M., Tang, Cheng Cai, Wakim, Paul, Blake, Mary, Brooks, Stephen R., Montealegre Sanchez, Gina A., de Jesus, Adriana A., Huang, Yan, Tsai, Wanxia Li, Gadina, Massimo, Prakash, Apurva, Janes, Jonathan Marcus, Zhang, Xin, Macias, William L., Kumar, Parag, Goldbach‐Mansky, Raphaela

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Identification of Distinct Inflammatory Programs and Biomarkers in Systemic Juvenile Idiopathic Arthritis and Related Lung Disease by Serum Proteome Analysis von Chen, Guangbo, Deutsch, Gail H., Schulert, Grant S., Zheng, Hong, Jang, SoRi, Trapnell, Bruce, Lee, Pui Y., Macaubas, Claudia, Ho, Katherine, Schneider, Corinne, Saper, Vivian E., Jesus, Adriana Almeida, Krasnow, Mark A., Grom, Alexei, Goldbach‐Mansky, Raphaela, Khatri, Purvesh, Mellins, Elizabeth D., Canna, Scott W.

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Regression Approaches to Assess Effect of Treatments That Arrest Progression of Symptoms von Ortega-Villa, Ana M, Nason, Martha C, Fay, Michael P, Alehashemi, Sara, Goldbach-Mansky, Raphaela, Follmann, Dean A

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Anakinra‐Associated Systemic Amyloidosis von Alehashemi, Sara, Dasari, Surendra, Metpally, Anvitha, Uss, Kat, Castelo‐Soccio, Leslie A., Heller, Theo, Kellman, Peter, Chen, Marcus Y., Ahlman, Mark, Kim, Jeff, Wargo, Susannah, Kuhns, Douglas B., Fink, Danielle, Jesus, Adriana, Martin, Paul S., Chang, Richard, Bolanos, Jonathan, Lee, Chyi‐Chia Richard, Nasr, Samih H., Goldbach‐Mansky, Raphaela, McPhail, Ellen

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The 2022 EULAR/ACR Points to Consider at the Early Stages of Diagnosis and Management of Suspected Haemophagocytic Lymphohistiocytosis/Macrophage Activation Syndrome (HLH/MAS) von Shakoory, Bita, Geerlinks, Ashley, Wilejto, Marta, Kernan, Kate, Hines, Melissa, Romano, Micol, Piskin, David, Ravelli, Angelo, Sinha, Rashmi, Aletaha, Daniel, Allen, Carl, Bassiri, Hamid, Behrens, Edward M, Carcillo, Joseph, Carl, Linda, Chatham, Winn, Cohen, Jeffrey I, Cron, Randy Q, Drewniak, Erik, Grom, Alexei A, Henderson, Lauren A, Horne, Annacarin, Jordan, Michael B, Nichols, Kim E, Schulert, Grant, Vastert, Sebastiaan, Demirkaya, Erkan, Goldbach-Mansky, Raphaela, de Benedetti, Fabrizio, Marsh, Rebecca A, Canna, Scott W

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Human Autoinflammatory Diseases Mediated by NLRP3-, Pyrin-, NLRP1-, and NLRC4-Inflammasome Dysregulation Updates on Diagnosis, Treatment, and the Respective Roles of IL-1 and IL-18 von Alehashemi, Sara, Goldbach-Mansky, Raphaela

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The 2021 EULAR/American College of Rheumatology Points to Consider for Diagnosis, Management and Monitoring of the Interleukin‐1 Mediated Autoinflammatory Diseases: Cryopyrin‐Assoc... von Romano, Micol, Arici, Z. Serap, Piskin, David, Alehashemi, Sara, Aletaha, Daniel, Barron, Karyl, Benseler, Susanne, Berard, Roberta A., Broderick, Lori, Dedeoglu, Fatma, Diebold, Michelle, Durrant, Karen, Ferguson, Polly, Foell, Dirk, Hausmann, Jonathan S., Jones, Olcay Y., Kastner, Daniel, Lachmann, Helen J., Laxer, Ronald M., Rivera, Dorelia, Ruperto, Nicola, Simon, Anna, Twilt, Marinka, Frenkel, Joost, Hoffman, Hal M., Jesus, Adriana A., Kuemmerle‐Deschner, Jasmin B., Ozen, Seza, Gattorno, Marco, Goldbach‐Mansky, Raphaela, Demirkaya, Erkan

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Autoinflammation: The prominent role of IL-1 in monogenic autoinflammatory diseases and implications for common illnesses von Goldbach-Mansky, Raphaela, MD, MHS, Kastner, Daniel L., MD, PhD

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Brief Report: Anakinra Use During Pregnancy in Patients With Cryopyrin‐Associated Periodic Syndromes von Chang, Zenas, Spong, Catherine Y., Jesus, Adriana A., Davis, Michael A., Plass, Nicole, Stone, Deborah L., Chapelle, Dawn, Hoffmann, Patrycja, Kastner, Daniel L., Barron, Karyl, Goldbach‐Mansky, Raphaela T., Stratton, Pamela

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Novel Majeed Syndrome–Causing LPIN2 Mutations Link Bone Inflammation to Inflammatory M2 Macrophages and Accelerated Osteoclastogenesis von Bhuyan, Farzana, Jesus, Adriana A., Mitchell, Jacob, Leikina, Evgenia, VanTries, Rachel, Herzog, Ronit, Onel, Karen B., Oler, Andrew, Montealegre Sanchez, Gina A., Johnson, Kim A., Bichell, Lena, Marrero, Bernadette, De Castro, Luis Fernandez, Huang, Yan, Calvo, Katherine R., Collins, Michael T., Ganesan, Sundar, Chernomordik, Leonid V., Ferguson, Polly J., Goldbach‐Mansky, Raphaela

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IL-1 blockade in autoinflammatory syndromes von Jesus, Adriana A, Goldbach-Mansky, Raphaela

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Neonatal detection of Aicardi Goutières Syndrome by increased C26:0 lysophosphatidylcholine and interferon signature on newborn screening blood spots von Armangue, Thais, Orsini, Joseph J., Takanohashi, Asako, Gavazzi, Francesco, Conant, Alex, Ulrick, Nicole, Morrissey, Mark A., Nahhas, Norah, Helman, Guy, Gordish-Dressman, Heather, Orcesi, Simona, Tonduti, Davide, Stutterd, Chloe, van Haren, Keith, Toro, Camilo, Iglesias, Alejandro D., van der Knaap, Marjo S., Goldbach Mansky, Raphaela, Moser, Anne B., Jones, Richard O., Vanderver, Adeline

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Rash, Fever, and Pulmonary Hypertension in a 6‐Year‐Old Female von Buchbinder, David, Montealegre Sanchez, Gina A., Goldbach‐Mansky, Raphaela, Brunner, Hermine, Shulman, Andrew I.

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Molecular Mechanisms in Genetically Defined Autoinflammatory Diseases: Disorders of Amplified Danger Signaling von de Jesus, Adriana Almeida, Canna, Scott W, Liu, Yin, Goldbach-Mansky, Raphaela

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Autoinflammatory Disease Reloaded: A Clinical Perspective von Kastner, Daniel L., Aksentijevich, Ivona, Goldbach-Mansky, Raphaela

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A novel mutation of IL1RN in the deficiency of interleukin‐1 receptor antagonist syndrome: Description of two unrelated cases from Brazil von Jesus, Adriana A., Osman, Mazen, Silva, Clovis A., Kim, Peter W., Pham, Tuyet‐Hang, Gadina, Massimo, Yang, Barbara, Bertola, Débora R., Carneiro‐Sampaio, Magda, Ferguson, Polly J., Renshaw, Blair R., Schooley, Ken, Brown, Michael, Al‐Dosari, Asma, Al‐Alami, Jamil, Sims, John E., Goldbach‐Mansky, Raphaela, El‐Shanti, Hatem

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Blocking Interleukin‐1 in Rheumatic Diseases: Its Initial Disappointments and Recent Successes in the Treatment of Autoinflammatory Diseases von Goldbach‐Mansky, Raphaela

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Editorial: Insights in autoimmune and autoinflammatory disorders: 2021 von Goldbach-Mansky, Raphaela, Diamond, Betty

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Deficiency of Interleukin-1 Receptor Antagonist Responsive to Anakinra von Schnellbacher, Charlotte, Ciocca, Giovanna, Menendez, Roxanna, Aksentijevich, Ivona, Goldbach-Mansky, Raphaela, Duarte, Ana M., Rivas-Chacon, Rafael

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