Sporadic human prion diseases: molecular insights and diagnosis von Puoti, Gianfranco, MD, Bizzi, Alberto, MD, Forloni, Gianluigi, PhD, Safar, Jiri G, MD, Tagliavini, Fabrizio, MD, Gambetti, Pierluigi, Prof

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Co-existence of PrPD types 1 and 2 in sporadic Creutzfeldt-Jakob disease of the VV subgroup: phenotypic and prion protein characteristics von Cali, Ignazio, Puoti, Gianfranco, Smucny, Jason, Curtiss, Paul Michael, Cracco, Laura, Kitamoto, Tetsuyuki, Occhipinti, Rossana, Cohen, Mark Lloyd, Appleby, Brian Stephen, Gambetti, Pierluigi

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A comparison of tau and 14-3-3 protein in the diagnosis of Creutzfeldt-Jakob disease von HAMLIN, Clive, PUOTI, Gianfranco, BERRI, Sally, STING, Elliott, HARRIS, Carrie, COHEN, Mark, SPEAR, Charles, BIZZI, Alberto, DEBANNE, Sara M, ROWLAND, Douglas Y

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Human prion diseases: surgical lessons learned from iatrogenic prion transmission von Bonda, David J, Manjila, Sunil, Mehndiratta, Prachi, Khan, Fahd, Miller, Benjamin R, Onwuzulike, Kaine, Puoti, Gianfranco, Cohen, Mark L, Schonberger, Lawrence B, Cali, Ignazio

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Variably protease-sensitive prionopathy: A new sporadic disease of the prion protein von Zou, Wen-Quan, Puoti, Gianfranco, Xiao, Xiangzhu, Yuan, Jue, Qing, Liuting, Cali, Ignazio, Shimoji, Miyuki, Langeveld, Jan P.M., Castellani, Rudy, Notari, Silvio, Crain, Barbara, Schmidt, Robert E., Geschwind, Michael, DeArmond, Stephen J., Cairns, Nigel J., Dickson, Dennis, Honig, Lawrence, Torres, Juan Maria, Mastrianni, James, Capellari, Sabina, Giaccone, Giorgio, Belay, Ermias D., Schonberger, Lawrence B., Cohen, Mark, Perry, George, Kong, Qingzhong, Parchi, Piero, Tagliavini, Fabrizio, Gambetti, Pierluigi

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Pathological 25 kDa C-Terminal Fragments of TDP-43 Are Present in Lymphoblastoid Cell Lines and Extracellular Vesicles from Patients Affected by Frontotemporal Lobar Degeneration a... von Cimini, Sara, Bellini, Sonia, Saraceno, Claudia, Benussi, Luisa, Ghidoni, Roberta, Giliani, Silvia Clara, Puoti, Gianfranco, Canafoglia, Laura, Giaccone, Giorgio, Rossi, Giacomina

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Plasma Small Extracellular Vesicle Cathepsin D Dysregulation in GRN/C9orf72 and Sporadic Frontotemporal Lobar Degeneration von Bellini, Sonia, Saraceno, Claudia, Benussi, Luisa, Geviti, Andrea, Longobardi, Antonio, Nicsanu, Roland, Cimini, Sara, Ricci, Martina, Canafoglia, Laura, Coppola, Cinzia, Puoti, Gianfranco, Binetti, Giuliano, Rossi, Giacomina, Ghidoni, Roberta

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Variably Protease-Sensitive Prionopathy: a Novel Disease of the Prion Protein von Gambetti, Pierluigi, Puoti, Gianfranco, Zou, Wen-Quan

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Case Report: Histopathology and Prion Protein Molecular Properties in Inherited Prion Disease With a De Novo Seven-Octapeptide Repeat Insertion von Cali, Ignazio, Cracco, Laura, Saracino, Dario, Occhipinti, Rossana, Coppola, Cinzia, Appleby, Brian Stephen, Puoti, Gianfranco

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Novel histotypes of sporadic Creutzfeldt-Jakob disease linked to 129MV genotype von Cracco, Laura, Puoti, Gianfranco, Cornacchia, Antonio, Glisic, Katie, Lee, Seong-Ki, Wang, Zerui, Cohen, Mark L, Appleby, Brian S, Cali, Ignazio

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Singular cases of Alzheimer’s disease disclose new and old genetic “acquaintances” von Coppola, Cinzia, Saracino, Dario, Oliva, Mariano, Cipriano, Lorenzo, Puoti, Gianfranco, Pappatà, Sabina, Di Fede, Giuseppe, Catania, Marcella, Ricci, Martina, Cimini, Sara, Giaccone, Giorgio, Bonavita, Simona, Rossi, Giacomina

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Large anterior temporal Virchow–Robin spaces: Evaluating MRI features over the years—Our experience and literature review von Capasso, Raffaella, Negro, Alberto, Cirillo, Sossio, Iovine, Silvia, Puoti, Gianfranco, Cirillo, Mario, Conforti, Renata

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Characterization of Prion Disease Associated with a Two-Octapeptide Repeat Insertion von Brennecke, Nicholas, Cali, Ignazio, Mok, Tze How, Speedy, Helen, Hosszu, Laszlo L. P., Stehmann, Christiane, Cracco, Laura, Puoti, Gianfranco, Prior, Thomas W., Cohen, Mark L., Collins, Steven J., Mead, Simon, Appleby, Brian S.

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Progressive multifocal leukoencephalopathy presenting with bilateral myoclonus: a case report von Andrea, Di Pietro, Gianmarco, Abbadessa, Giorgia, Bruno, Giuseppina, Miele, Giuseppe, Pontillo, Sirio, Cocozza, Maria, Spera Anna, Gianfranco, Puoti

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A novel mechanism of phenotypic heterogeneity in Creutzfeldt-Jakob disease von Nemani, Satish K., Xiao, Xiangzhu, Cali, Ignazio, Cracco, Laura, Puoti, Gianfranco, Nigro, Massimiliano, Lavrich, Jody, Bharara Singh, Anuradha, Appleby, Brian S., Sim, Valerie L., Notari, Silvio, Surewicz, Witold K., Gambetti, Pierluigi

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Plasma Small Extracellular Vesicles with Complement Alterations in GRN / C9orf72 and Sporadic Frontotemporal Lobar Degeneration von Bellini, Sonia, Saraceno, Claudia, Benussi, Luisa, Squitti, Rosanna, Cimini, Sara, Ricci, Martina, Canafoglia, Laura, Coppola, Cinzia, Puoti, Gianfranco, Ferrari, Clarissa, Longobardi, Antonio, Nicsanu, Roland, Lombardi, Marta, D'Arrigo, Giulia, Verderio, Claudia, Binetti, Giuliano, Rossi, Giacomina, Ghidoni, Roberta

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Unusual CLIPPERS presentation and role of MRI examination in the proper diagnostic assessment: a case report von Vola, Elena, Russo, Camilla, Macera, Antonio, Del Vecchio, Walter, Puoti, Gianfranco, Caranci, Ferdinando, Elefante, Andrea

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Delayed post‐hypoxic leukoencephalopathy with a peculiar autoantibody association von Coppola, Cinzia, Oliva, Mariano, Saracino, Dario, Cipriano, Lorenzo, Capaldo, Guglielmo, Puoti, Gianfranco, Fratta, Mario, Ugga, Lorenzo, D'Amico, Alessandra

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Variably Protease-sensitive Prionopathy in an Apparent Cognitively Normal 93-Year-Old von Ghoshal, Nupur, Perry, Arie, McKeel, Daniel, Schmidt, Robert E, Carter, Deborah, Norton, Joanne, Zou, Wen-Quan, Xiao, Xiangzhu, Puoti, Gianfranco, Notari, Silvio, Gambetti, Pierluigi, Morris, John C, Cairns, Nigel J

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New-Onset Refractory Status Epilepticus Mimicking Herpes Virus Encephalitis von Puoti, Gianfranco, Elefante, Andrea, Saracino, Dario, Capasso, Antonella, Cotrufo, Roberto, Belluomo Anello, Clara

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