Oxidative stress in SEPN1-related myopathy: From pathophysiology to treatment von Arbogast, Sandrine, Beuvin, Maud, Fraysse, Bodvaël, Zhou, Haïyan, Muntoni, Francesco, Ferreiro, Ana

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Increased myofilament Ca2+ sensitivity and diastolic dysfunction as early consequences of Mybpc3 mutation in heterozygous knock-in mice von Fraysse, Bodvaël, Weinberger, Florian, Bardswell, Sonya C, Cuello, Friederike, Vignier, Nicolas, Geertz, Birgit, Starbatty, Jutta, Krämer, Elisabeth, Coirault, Catherine, Eschenhagen, Thomas, Kentish, Jonathan C, Avkiran, Metin, Carrier, Lucie

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TRPC3, but not TRPC1, as a good therapeutic target for standalone or complementary treatment of DMD von Creismeas, Anna, Gazaille, Claire, Bourdon, Audrey, Lallemand, Marc-Antoine, Francois, Virginie, Allais, Marine, Ledevin, Mireille, Larcher, Thibaut, Toumaniantz, Gilles, Lafoux, Aude, Huchet, Corinne, Anegon, Ignacio, Adjali, Oumeya, Le Guiner, Caroline, Fraysse, Bodvael

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A centronuclear myopathy-dynamin 2 mutation impairs skeletal muscle structure and function in mice von Durieux, Anne-Cécile, Vignaud, Alban, Prudhon, Bernard, Viou, Mai Thao, Beuvin, Maud, Vassilopoulos, Stéphane, Fraysse, Bodvaël, Ferry, Arnaud, Lainé, Jeanne, Romero, Norma B., Guicheney, Pascale, Bitoun, Marc

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Calcium homeostasis alterations in a mouse model of the Dynamin 2-related centronuclear myopathy von Fraysse, Bodvaël, Guicheney, Pascale, Bitoun, Marc

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A Centronuclear Myopathy – Dynamin 2 Mutation Impairs Autophagy in Mice von Durieux, Anne‐Cécile, Vassilopoulos, Stéphane, Lainé, Jeanne, Fraysse, Bodvaël, Briñas, Laura, Prudhon, Bernard, Castells, Josiane, Freyssenet, Damien, Bonne, Gisèle, Guicheney, Pascale, Bitoun, Marc

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Gait characterization in golden retriever muscular dystrophy dogs using linear discriminant analysis von Fraysse, Bodvaël, Barthélémy, Inès, Qannari, El Mostafa, Rouger, Karl, Thorin, Chantal, Blot, Stéphane, Le Guiner, Caroline, Chérel, Yan, Hogrel, Jean-Yves

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Long-term microdystrophin gene therapy is effective in a canine model of Duchenne muscular dystrophy von Le Guiner, Caroline, Servais, Laurent, Montus, Marie, Larcher, Thibaut, Fraysse, Bodvaël, Moullec, Sophie, Allais, Marine, François, Virginie, Dutilleul, Maeva, Malerba, Alberto, Koo, Taeyoung, Thibaut, Jean-Laurent, Matot, Béatrice, Devaux, Marie, Le Duff, Johanne, Deschamps, Jack-Yves, Barthelemy, Inès, Blot, Stéphane, Testault, Isabelle, Wahbi, Karim, Ederhy, Stéphane, Martin, Samia, Veron, Philippe, Georger, Christophe, Athanasopoulos, Takis, Masurier, Carole, Mingozzi, Federico, Carlier, Pierre, Gjata, Bernard, Hogrel, Jean-Yves, Adjali, Oumeya, Mavilio, Fulvio, Voit, Thomas, Moullier, Philippe, Dickson, George

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Novel chemical tyrosine functionalization of adeno-associated virus improves gene transfer efficiency in liver and retina von Leray, Aurélien, Lalys, Pierre-Alban, Varin, Juliette, Bouzelha, Mohammed, Bourdon, Audrey, Alvarez-Dorta, Dimitri, Pavageau, Karine, Depienne, Sébastien, Marchand, Maia, Mellet, Anthony, Demilly, Joanna, Ducloyer, Jean-Baptiste, Girard, Tiphaine, Fraysse, Bodvaël, Ledevin, Mireille, Guilbaud, Mickaël, Gouin, Sébastien G., Ayuso, Eduard, Adjali, Oumeya, Larcher, Thibaut, Cronin, Thérèse, Le Guiner, Caroline, Deniaud, David, Mével, Mathieu

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Multiple pathological events in exercised dystrophic mdx mice are targeted by pentoxifylline: outcome of a large array of in vivo and ex vivo tests von Burdi, Rosa, Rolland, Jean-Francois, Fraysse, Bodvael, Litvinova, Karina, Cozzoli, Anna, Giannuzzi, Viviana, Liantonio, Antonella, Camerino, Giulia Maria, Sblendorio, Valeriana, Capogrosso, Roberta Francesca, Palmieri, Beniamino, Andreetta, Francesca, Confalonieri, Paolo, De Benedictis, Leonarda, Montagnani, Monica, De Luca, Annamaria

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Nonsense-Mediated mRNA Decay and Ubiquitin–Proteasome System Regulate Cardiac Myosin-Binding Protein C Mutant Levels in Cardiomyopathic Mice von Vignier, Nicolas, Schlossarek, Saskia, Fraysse, Bodvael, Mearini, Giulia, Krämer, Elisabeth, Pointu, Hervé, Mougenot, Nathalie, Guiard, Josiane, Reimer, Rudolph, Hohenberg, Heinrich, Schwartz, Ketty, Vernet, Muriel, Eschenhagen, Thomas, Carrier, Lucie

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Growth Hormone Secretagogues Exert Differential Effects on Skeletal Muscle Calcium Homeostasis in Male Rats Depending on the Peptidyl/Nonpeptidyl Structure von Liantonio, Antonella, Gramegna, Gianluca, Carbonara, Giuseppe, Sblendorio, Valeriana Teresa, Pierno, Sabata, Fraysse, Bodvaël, Giannuzzi, Viviana, Rizzi, Laura, Torsello, Antonio, Camerino, Diana Conte

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Novel chemical tyrosine functionalization of adeno-associated virus improves gene transfer efficiency in liver and retina von Leray, Aurélien, Lalys, Pierre-Alban, Varin, Juliette, Bouzelha, Mohammed, Bourdon, Audrey, Alvarez-Dorta, Dimitri, Pavageau, Karine, Depienne, Sébastien, Marchand, Maia, Mellet, Anthony, Demilly, Joanna, Ducloyer, Jean-Baptiste, Girard, Tiphaine, Fraysse, Bodvaël, Ledevin, Mireille, Guilbaud, Mickaël, Gouin, Sébastien G, Ayuso, Eduard, Adjali, Oumeya, Larcher, Thibaut, Cronin, Thérèse, Le Guiner, Caroline, Deniaud, David, Mével, Mathieu

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Ca2+ overload and mitochondrial permeability transition pore activation in living delta-sarcoglycan-deficient cardiomyocytes von Fraysse, Bodvaël, Nagi, Sadia M, Boher, Belinda, Ragot, Hélène, Lainé, Jeanne, Salmon, André, Fiszman, Marc Y, Toussaint, Marcel, Fromes, Yves

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Expression of the Na+/Ca2+ exchanger in skeletal muscle von Fraysse, Bodvael, Rouaud, Thierry, Millour, Marie, Fontaine-Perus, Josiane, Gardahaut, Marie-France, Levitsky, Dmitri O

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Acute effect of androgens on maximal force-generating capacity and electrically evoked calcium transient in mouse skeletal muscles von Fraysse, Bodvael, Vignaud, Alban, Fane, Bourama, Schuh, Mélanie, Butler-Browne, Gillian, Metzger, Daniel, Ferry, Arnaud

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A Multidisciplinary Evaluation of the Effectiveness of Cyclosporine A in Dystrophic Mdx Mice von De Luca, Annamaria, Nico, Beatrice, Liantonio, Antonella, Didonna, Maria Paola, Fraysse, Bodvael, Pierno, Sabata, Burdi, Rosa, Mangieri, Domenica, Rolland, Jean-François, Camerino, Claudia, Zallone, Alberta, Confalonieri, Paolo, Andreetta, Francesca, Arnoldi, Elisa, Courdier-Fruh, Isabelle, Magyar, Josef P., Frigeri, Antonio, Pisoni, Michela, Svelto, Maria, Conte Camerino, Diana

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The alteration of calcium homeostasis in adult dystrophic mdx muscle fibers is worsened by a chronic exercise in vivo von Fraysse, Bodvael, Liantonio, Antonella, Cetrone, Michela, Burdi, Rosa, Pierno, Sabata, Frigeri, Antonio, Pisoni, Michela, Camerino, Claudia, De Luca, Annamaria

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Expression of the Na+/Ca2+ exchanger in skeletal muscle von FRAYSSE, Bodvaël, ROUAUD, Thierry, MILLOUR, Marie, FONTAINE-PERUS, Josiane, GARDAHAUT, Marie-France, LEVITSKY, Dmitri O

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Development of a zebrafish 4-day embryo-larval bioassay to assess toxicity of chemicals von Fraysse, Benoit, Mons, Raphael, Garric, Jeanne

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