Compromised phagosome maturation underlies RPE pathology in cell culture and whole animal models of Smith-Lemli-Opitz Syndrome von Ramachandra Rao, Sriganesh, Pfeffer, Bruce A., Más Gómez, Néstor, Skelton, Lara A., Keiko, Ueda, Sparrow, Janet R., Rowsam, Aryn M., Mitchell, Claire H., Fliesler, Steven J.

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Formation of 7-dehydrocholesterol-containing membrane rafts in vitro and in vivo, with relevance to the Smith-Lemli-Opitz syndrome von Keller, R. Kennedy, Arnold, Thomas P., Fliesler, Steven J.

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Retention of function without normal disc morphogenesis occurs in cone but not rod photoreceptors von Farjo, Rafal, Skaggs, Jeff S, Nagel, Barbara A, Quiambao, Alexander B, Nash, Zack A, Fliesler, Steven J, Naash, Muna I

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The R172W mutation in peripherin/rds causes a cone–rod dystrophy in transgenic mice von Ding, Xi-Qin, Nour, May, Ritter, Linda M., Goldberg, Andrew F.X., Fliesler, Steven J., Naash, Muna I.

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Modulating Expression of Peripherin/rds in Transgenic Mice: Critical Levels and the Effect of Overexpression von Nour, May, Ding, Xi-Qin, Stricker, Heidi, Fliesler, Steven J, Naash, Muna I

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Development and characterization of a hypomorphic Smith–Lemli–Opitz syndrome mouse model and efficacy of simvastatin therapy von Correa-Cerro, Lina S., Wassif, Christopher A., Kratz, Lisa, Miller, Georgina F., Munasinghe, Jeeva P., Grinberg, Alexander, Fliesler, Steven J., Porter, Forbes D.

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The Relationship between Opsin Overexpression and Photoreceptor Degeneration von Tan, Elaine, Wang, Quan, Quiambao, Alexander B, Xu, Xiaoping, Qtaishat, Nasser M, Peachey, Neal S, Lem, Janis, Fliesler, Steven J, Pepperberg, David R, Naash, Muna I, Al-Ubaidi, Muayyad R

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Lipid hydroperoxide formation in the retina: correlation with retinal degeneration and light damage in a rat model of Smith–Lemli–Opitz syndrome von Richards, Michael J., Nagel, Barbara A., Fliesler, Steven J.

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Mechanism of Aminobisphosphonate Action: Characterization of Alendronate Inhibition of the Isoprenoid Pathway von Keller, R.Kennedy, Fliesler, Steven J.

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A comparison of the behavior of cholesterol and selected derivatives in mixed sterol–phospholipid Langmuir monolayers: a fluorescence microscopy study von Berring, Erin E., Borrenpohl, Kimberly, Fliesler, Steven J., Serfis, Alexa Barnoski

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Cholesterol-Dependent Association of Caveolin-1 with the Transducin α Subunit in Bovine Photoreceptor Rod Outer Segments:  Disruption by Cyclodextrin and Guanosine 5‘-O-(3-Thiotrip... von Elliott, Michael H, Fliesler, Steven J, Ghalayini, Abboud J

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Focus on Molecules von Fliesler, Steven J.

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Light-induced exacerbation of retinal degeneration in a rat model of Smith–Lemli–Opitz syndrome von Vaughan, Dana K., Peachey, Neal S., Richards, Michael J., Buchan, Blake, Fliesler, Steven J.

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Comparative behavior of sterols in phosphatidylcholine-sterol monolayer films von Serfis, A.B, Brancato, S, Fliesler, S.J

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Evidence for a Circadian Rhythm of Susceptibility to Retinal Light Damage von Vaughan, Dana K., Nemke, Jenny L., Fliesler, Steven J., Darrow, Ruth M., Organisciak, Daniel T.

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Retinal abnormalities associated with the G90D mutation in opsin von Naash, Muna I., Wu, Ting-Huai, Chakraborty, Dibyendu, Fliesler, Steven J., Ding, Xi-Qin, Nour, May, Peachey, Neal S., Lem, Janis, Qtaishat, Nasser, Al-Ubaidi, Muayyad R., Ripps, Harris

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Enzyme blockade: a nonradioactive method to determine the absolute rate of cholesterol synthesis in the brain von Keller, R. Kennedy, Small, Michael, Fliesler, Steven J.

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Alterations in retinal rod outer segment fatty acids and light-damage susceptibility in P23H rats von Bicknell, Ina Rea, Darrow, Ruth, Barsalou, Linda, Fliesler, Steven J, Organisciak, Daniel T

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Disturbed Cholesterol Homeostasis in a Peroxisome-Deficient PEX2 Knockout Mouse Model von Kovacs, Werner J., Shackelford, Janis E., Tape, Khanichi N., Richards, Michael J., Faust, Phyllis L., Fliesler, Steven J., Krisans, Skaidrite K.

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Marked Alteration of Sterol Metabolism and Composition without Compromising Retinal Development or Function von Fliesler, Steven J, Richards, Michael J, Miller, Chi-yen, Peachey, Neal S

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