DNAJC19, a Mitochondrial Cochaperone Associated with Cardiomyopathy, Forms a Complex with Prohibitins to Regulate Cardiolipin Remodeling von Richter-Dennerlein, Ricarda, Korwitz, Anne, Haag, Mathias, Tatsuta, Takashi, Dargazanli, Sascha, Baker, Michael, Decker, Thorsten, Lamkemeyer, Tobias, Rugarli, Elena I., Langer, Thomas

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Tissue-Specific Loss of DARS2 Activates Stress Responses Independently of Respiratory Chain Deficiency in the Heart von Dogan, Sukru Anil, Pujol, Claire, Maiti, Priyanka, Kukat, Alexandra, Wang, Shuaiyu, Hermans, Steffen, Senft, Katharina, Wibom, Rolf, Rugarli, Elena I., Trifunovic, Aleksandra

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Loss of prohibitin membrane scaffolds impairs mitochondrial architecture and leads to tau hyperphosphorylation and neurodegeneration von Merkwirth, Carsten, Martinelli, Paola, Korwitz, Anne, Morbin, Michela, Brönneke, Hella S, Jordan, Sabine D, Rugarli, Elena I, Langer, Thomas

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The m-AAA Protease Associated with Neurodegeneration Limits MCU Activity in Mitochondria von König, Tim, Tröder, Simon E., Bakka, Kavya, Korwitz, Anne, Richter-Dennerlein, Ricarda, Lampe, Philipp A., Patron, Maria, Mühlmeister, Mareike, Guerrero-Castillo, Sergio, Brandt, Ulrich, Decker, Thorsten, Lauria, Ines, Paggio, Angela, Rizzuto, Rosario, Rugarli, Elena I., De Stefani, Diego, Langer, Thomas

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Spastin binds to lipid droplets and affects lipid metabolism von Papadopoulos, Chrisovalantis, Orso, Genny, Mancuso, Giuseppe, Herholz, Marija, Gumeni, Sentiljana, Tadepalle, Nimesha, Jüngst, Christian, Tzschichholz, Anne, Schauss, Astrid, Höning, Stefan, Trifunovic, Aleksandra, Daga, Andrea, Rugarli, Elena I

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The class 3 PI3K coordinates autophagy and mitochondrial lipid catabolism by controlling nuclear receptor PPARα von Iershov, Anton, Nemazanyy, Ivan, Alkhoury, Chantal, Girard, Muriel, Barth, Esther, Cagnard, Nicolas, Montagner, Alexandra, Chretien, Dominique, Rugarli, Elena I., Guillou, Herve, Pende, Mario, Panasyuk, Ganna

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Regulation of OPA1 processing and mitochondrial fusion by m-AAA protease isoenzymes and OMA1 von Ehses, Sarah, Raschke, Ines, Mancuso, Giuseppe, Bernacchia, Andrea, Geimer, Stefan, Tondera, Daniel, Martinou, Jean-Claude, Westermann, Benedikt, Rugarli, Elena I, Langer, Thomas

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Loss of OMA1 delays neurodegeneration by preventing stress-induced OPA1 processing in mitochondria von Korwitz, Anne, Merkwirth, Carsten, Richter-Dennerlein, Ricarda, Tröder, Simon E, Sprenger, Hans-Georg, Quirós, Pedro M, López-Otín, Carlos, Rugarli, Elena I, Langer, Thomas

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Emerging roles of mitochondrial proteases in neurodegeneration von Martinelli, Paola, Rugarli, Elena I.

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Lipid Droplets in the Pathogenesis of Hereditary Spastic Paraplegia von Tadepalle, Nimesha, Rugarli, Elena I.

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CLUH regulates mitochondrial biogenesis by binding mRNAs of nuclear-encoded mitochondrial proteins von Gao, Jie, Schatton, Désirée, Martinelli, Paola, Hansen, Henriette, Pla-Martin, David, Barth, Esther, Becker, Christian, Altmueller, Janine, Frommolt, Peter, Sardiello, Marco, Rugarli, Elena I

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CLUH regulates mitochondrial metabolism by controlling translation and decay of target mRNAs von Schatton, Désirée, Pla-Martin, David, Marx, Marie-Charlotte, Hansen, Henriette, Mourier, Arnaud, Nemazanyy, Ivan, Pessia, Alberto, Zentis, Peter, Corona, Teresa, Kondylis, Vangelis, Barth, Esther, Schauss, Astrid C, Velagapudi, Vidya, Rugarli, Elena I

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Whole-exome sequencing identifies homozygous AFG3L2 mutations in a spastic ataxia-neuropathy syndrome linked to mitochondrial m-AAA proteases von Pierson, Tyler Mark, Adams, David, Bonn, Florian, Martinelli, Paola, Cherukuri, Praveen F, Teer, Jamie K, Hansen, Nancy F, Cruz, Pedro, Mullikin For The Nisc Comparative Sequencing Program, James C, Blakesley, Robert W, Golas, Gretchen, Kwan, Justin, Sandler, Anthony, Fuentes Fajardo, Karin, Markello, Thomas, Tifft, Cynthia, Blackstone, Craig, Rugarli, Elena I, Langer, Thomas, Gahl, William A, Toro, Camilo

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Loss of the mitochondrial i‐AAA protease YME1L leads to ocular dysfunction and spinal axonopathy von Sprenger, Hans‐Georg, Wani, Gulzar, Hesseling, Annika, König, Tim, Patron, Maria, MacVicar, Thomas, Ahola, Sofia, Wai, Timothy, Barth, Esther, Rugarli, Elena I, Bergami, Matteo, Langer, Thomas

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Mitochondrial quality control: a matter of life and death for neurons von Rugarli, Elena I, Langer, Thomas

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The m-AAA Protease Defective in Hereditary Spastic Paraplegia Controls Ribosome Assembly in Mitochondria von Nolden, Mark, Ehses, Sarah, Koppen, Mirko, Bernacchia, Andrea, Rugarli, Elena I., Langer, Thomas

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The Mitochondrial m-AAA Protease Prevents Demyelination and Hair Greying von Wang, Shuaiyu, Jacquemyn, Julie, Murru, Sara, Martinelli, Paola, Barth, Esther, Langer, Thomas, Niessen, Carien M, Rugarli, Elena I

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CLUH controls astrin-1 expression to couple mitochondrial metabolism to cell cycle progression von Schatton, Désirée, Di Pietro, Giada, Szczepanowska, Karolina, Veronese, Matteo, Marx, Marie-Charlotte, Braunöhler, Kristina, Barth, Esther, Müller, Stefan, Giavalisco, Patrick, Langer, Thomas, Trifunovic, Aleksandra, Rugarli, Elena I

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Variable and Tissue-Specific Subunit Composition of Mitochondrial m-AAA Protease Complexes Linked to Hereditary Spastic Paraplegia von Koppen, Mirko, Metodiev, Metodi D., Casari, Giorgio, Rugarli, Elena I., Langer, Thomas

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Pleiotropic effects of spastin on neurite growth depending on expression levels von Riano, Elena, Martignoni, Monica, Mancuso, Giuseppe, Cartelli, Daniele, Crippa, Francesca, Toldo, Irene, Siciliano, Gabriele, Di Bella, Daniela, Taroni, Franco, Bassi, Maria Teresa, Cappelletti, Graziella, Rugarli, Elena I

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