The Extended Clinical Phenotype of 26 Patients with Chronic Mucocutaneous Candidiasis due to Gain-of-Function Mutations in STAT1 von Depner, Mark, Fuchs, Sebastian, Raabe, Jan, Frede, Natalie, Glocker, Cristina, Doffinger, Rainer, Gkrania-Klotsas, Effrossyni, Kumararatne, Dinakantha, Atkinson, T. Prescott, Schroeder, Harry W., Niehues, Tim, Dückers, Gregor, Stray-Pedersen, Asbjørg, Baumann, Ulrich, Schmidt, Reinhold, Franco, Jose L., Orrego, Julio, Ben-Shoshan, Moshe, McCusker, Christine, Jacob, Cristina Miuki Abe, Carneiro-Sampaio, Magda, Devlin, Lisa A., Edgar, J. David M., Henderson, Paul, Russell, Richard K., Skytte, Anne-Bine, Seneviratne, Suranjith L., Wanders, Jennifer, Stauss, Hans, Meyts, Isabelle, Moens, Leen, Jesenak, Milos, Kobbe, Robin, Borte, Stephan, Borte, Michael, Wright, Dowain A., Hagin, David, Torgerson, Troy R., Grimbacher, Bodo

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Simple Measurement of IgA Predicts Immunity and Mortality in Ataxia-Telangiectasia von Zielen, Stefan, Duecker, Ruth Pia, Woelke, Sandra, Donath, Helena, Bakhtiar, Sharhzad, Buecker, Aileen, Kreyenberg, Hermann, Huenecke, Sabine, Bader, Peter, Mahlaoui, Nizar, Ehl, Stephan, El-Helou, Sabine M., Pietrucha, Barbara, Plebani, Alessandro, van der Flier, Michiel, van Aerde, Koen, Kilic, Sara S., Reda, Shereen M., Kostyuchenko, Larysa, McDermott, Elizabeth, Galal, Nermeen, Pignata, Claudio, Pérez, Juan Luis Santos, Laws, Hans-Juergen, Niehues, Tim, Kutukculer, Necil, Seidel, Markus G., Marques, Laura, Ciznar, Peter, Edgar, John David M., Soler-Palacín, Pere, von Bernuth, Horst, Krueger, Renate, Meyts, Isabelle, Baumann, Ulrich, Kanariou, Maria, Grimbacher, Bodo, Hauck, Fabian, Graf, Dagmar, Granado, Luis Ignacio Gonzalez, Prader, Seraina, Reisli, Ismail, Slatter, Mary, Rodríguez-Gallego, Carlos, Arkwright, Peter D., Bethune, Claire, Deripapa, Elena, Sharapova, Svetlana O., Lehmberg, Kai, Davies, E. Graham, Schuetz, Catharina, Kindle, Gerhard, Schubert, Ralf

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Occurrence of B-cell lymphomas in patients with activated phosphoinositide 3-kinase δ syndrome von Kracker, Sven, PhD, Curtis, James, BSc, Ibrahim, Mohammad A.A., MBBCh, MSc, PhD, FRCPath, FRCP, Sediva, Anna, MD, PhD, Salisbury, Jon, BSc, MD, FRCPath, Campr, Vit, MD, Debré, Marianne, MD, Edgar, J. David M., BSc, FRCP, FRCPath, Imai, Kohsuke, MD, PhD, Picard, Capucine, MD, PhD, Casanova, Jean-Laurent, MD, PhD, Fischer, Alain, MD, PhD, Nejentsev, Sergey, MD, PhD, Durandy, Anne, MD, PhD

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Inborn Errors of Immunity on the Island of Ireland — a Cross-Jurisdictional UKPID/ESID Registry Report von Ryan, Paul, Redenbaugh, Vyanka, McGucken, Jayne, Kindle, Gerhard, Devlin, Lisa A., Coulter, Tanya, Buckland, Matthew S., Seppänen, Mikko R. J., Conlon, Niall P., Feighery, Conleth, Edgar, J. David M.

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Correction to: Inborn Errors of Immunity on the Island of Ireland — a Cross‑Jurisdictional UKPID/ESID Registry Report von Ryan, Paul, Redenbaugh, Vyanka, McGucken, Jayne, Kindle, Gerhard, Devlin, Lisa A., Coulter, Tanya, Buckland, Matthew S., Seppänen, Mikko R. J., Conlon, Niall P., Feighery, Conleth, Edgar, J. David M.

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Adherence to best practice guidelines in chronic spontaneous urticaria (CSU) improves patient outcome von Conlon, Niall P, Edgar, J David M

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Clinical spectrum and features of activated phosphoinositide 3-kinase δ syndrome: A large patient cohort study von Coulter, Tanya I., MRCPI, Chandra, Anita, PhD, FRCPath, Bacon, Chris M., PhD, FRCPath, Babar, Judith, MRCP, FRCR, Curtis, James, PhD, Screaton, Nick, FRCP, FRCR, Goodlad, John R., MD, FRCPath, Farmer, George, MD, Steele, Cathal Laurence, MB, Leahy, Timothy Ronan, MRCPI, Doffinger, Rainer, PhD, FRCPath, Baxendale, Helen, PhD, FRCPath, Bernatoniene, Jolanta, PhD, Edgar, J. David M., FRCP, FRCPath, Longhurst, Hilary J., PhD, FRCPath, Ehl, Stephan, MD, PhD, Speckmann, Carsten, MD, Grimbacher, Bodo, MD, PhD, Sediva, Anna, MD, PhD, Milota, Tomas, MD, Faust, Saul N., PhD, FRCPCH, Williams, Anthony P., PhD, FRCPath, Hayman, Grant, FRCP, FRCPath, Kucuk, Zeynep Yesim, MD, Hague, Rosie, MRCP, FRCPH, French, Paul, MD, MRCS, DipFMS, FRCPath, Brooker, Richard, FRCPCH, Forsyth, Peter, FRCPath, Herriot, Richard, FRCP, FRCPath, Cancrini, Caterina, MD, PhD, Palma, Paolo, MD, PhD, Ariganello, Paola, MD, Conlon, Niall, PhD, FRCPath, Feighery, Conleth, PhD, FRCPath, Gavin, Patrick J., MD, Jones, Alison, PhD, FRCPCH, Imai, Kohsuke, MD, PhD, Ibrahim, Mohammad A.A., PhD, FRCP, FRCPath, Markelj, Gašper, MD, Abinun, Mario, MD, PhD, Rieux-Laucat, Frédéric, PhD, Latour, Sylvain, PhD, Pellier, Isabelle, MD, PhD, Fischer, Alain, MD, PhD, Touzot, Fabien, MD, PhD, Casanova, Jean-Laurent, MD, PhD, Durandy, Anne, MD, PhD, Burns, Siobhan O., MD, PhD, Savic, Sinisa, PhD, FRCPath, Kumararatne, D.S., FRCPath, DPhil (Oxon), Moshous, Despina, MD, PhD, Kracker, Sven, PhD, Vanhaesebroeck, Bart, PhD, FMedSci, Okkenhaug, Klaus, PhD, Picard, Capucine, MD, PhD, Nejentsev, Sergey, MD, PhD, Condliffe, Alison M., PhD, FRCP, Cant, Andrew James, MD, FRCP, FRCPH

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A prospective study of the sensitivity, specificity and diagnostic performance of soluble intercellular adhesion molecule 1, highly sensitive C-reactive protein, soluble E-selectin... von Edgar, J David M, Gabriel, Vanessa, Gallimore, J Ruth, McMillan, Stanley A, Grant, Judith

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Long-term outcomes of 176 patients with X-linked hyper-IgM syndrome treated with or without hematopoietic cell transplantation von de la Morena, M. Teresa, MD, Leonard, David, PhD, Torgerson, Troy R., MD, PhD, Cabral-Marques, Otavio, PhD, Slatter, Mary, MD, Aghamohammadi, Asghar, MD, Chandra, Sharat, MD, Murguia-Favela, Luis, MD, Bonilla, Francisco A., MD, PhD, Kanariou, Maria, MD, Damrongwatanasuk, Rongras, MD, Kuo, Caroline Y., MD, Dvorak, Christopher C., MD, Meyts, Isabelle, MD, Chen, Karin, MD, Kobrynski, Lisa, MD, MPH, Kapoor, Neena, MD, Richter, Darko, MD, DiGiovanni, Daniela, MD, Dhalla, Fatima, MD, Farmaki, Evangelia, MD, Speckmann, Carsten, MD, Español, Teresa, MD, Shcherbina, Anna, MD, Hanson, Imelda Celine, MD, Litzman, Jiri, MD, Routes, John M., MD, Wong, Melanie, MD, PhD, Fuleihan, Ramsay, MD, Seneviratne, Suranjith L., MD, Small, Trudy N., MD, Janda, Ales, MD, Bezrodnik, Liliana, MD, Seger, Reinhard, MD, Raccio, Andrea Gomez, MD, Edgar, J. David M., MD, Chou, Janet, MD, Abbott, Jordan K., MD, van Montfrans, Joris, MD, González-Granado, Luis Ignacio, MD, Bunin, Nancy, MD, Kutukculer, Necil, MD, Gray, Paul, MD, Seminario, Gisela, MD, Pasic, Srdjan, MD, Aquino, Victor, MD, Wysocki, Christian, MD, PhD, Abolhassani, Hassan, MD, Dorsey, Morna, MD, Cunningham-Rundles, Charlotte, MD, PhD, Knutsen, Alan P., MD, Sleasman, John, MD, Costa Carvalho, Beatriz Tavares, MD, Condino-Neto, Antonio, MD, Grunebaum, Eyal, MD, Chapel, Helen, MD, Ochs, Hans D., MD, PhD, Filipovich, Alexandra, MD, Cowan, Mort, MD, Gennery, Andrew, MD, Cant, Andrew, MD, Notarangelo, Luigi D., MD, Roifman, Chaim M., MD

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Identification of Diagnostic Biomarkers for Infection in Premature Neonates von Kingsmore, Stephen F., Kennedy, Neil, Halliday, Henry L., Van Velkinburgh, Jennifer C., Zhong, Shengiang, Gabriel, Vanessa, Grant, Judith, Beavis, William D., Tchernev, Velizar T., Perlee, Lorah, Lejnine, Serguei, Grimwade, Brian, Sorette, Martin, Edgar, J. David M.

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Current clinical practice and challenges in the management of secondary immunodeficiency in hematological malignancies von Na, Il‐Kang, Buckland, Matthew, Agostini, Carlo, Edgar, John David M., Friman, Vanda, Michallet, Mauricette, Sánchez‐Ramón, Silvia, Scheibenbogen, Carmen, Quinti, Isabella

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Overview of antibody‐mediated immunity to S. pneumoniae: pneumococcal infections, pneumococcal immunity assessment, and recommendations for IG product evaluation von Sorensen, Ricardo U., Edgar, J. David M.

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X-linked Inhibitor of Apoptosis Complicated by Granulomatous Lymphocytic Interstitial Lung Disease (GLILD) and Granulomatous Hepatitis von Steele, Cathal L., Doré, Matthew, Ammann, Sandra, Loughrey, Maurice, Montero, Angeles, Burns, Siobhan O., Morris, Emma C., Gaspar, Bobby, Gilmour, Kimberly, Bibi, Shahnaz, Shendi, Hiba, Devlin, Lisa, Speckmann, Carsten, Edgar, David M.

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Etanercept and anakinra can prolong febrile episodes in patients with hyperimmunoglobulin D and periodic fever syndrome von Shendi, Hiba M., Walsh, Deirdre, Edgar, J. David M.

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Risk stratification through allergy history: single-centre experience of specialized COVID-19 vaccine clinic von Lyons, Daniel, Murray, Cliodhna, Hannigan, Siobhan, Sui, Jacklyn, Alamin, Salma, Conlon, Niall, Keogan, Mary, Khalib, Khairin, Fitzpatrick, Chris, O’B Hourihane, Jonathan, Carey, Michael, Edgar, J David M

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Liver disease predicts mortality in patients with X-linked immunodeficiency with hyper-IgM but can be prevented by early hematopoietic stem cell transplantation von Azzu, Vian, Kennard, Lucinda, Morillo-Gutierrez, Beatriz, Slatter, Mary, Edgar, J. David M., Kumararatne, Dinakantha S., Griffiths, William J.H.

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Prescribing Immunoglobulin Replacement Therapy for Patients with Non-classical and Secondary Antibody Deficiency: an Analysis of the Practice of Clinical Immunologists in the UK an... von Edgar, John David M., Richter, Alex G., Huissoon, Aarnoud P., Kumararatne, Dinakantha S., Baxendale, Helen E., Bethune, Claire A., Garcez, Tomaz, Misbah, Siraj A., Sorensen, Ricardo U.

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Combined liver and hematopoietic stem cell transplantation in patients with X-linked hyper-IgM syndrome von Bucciol, Giorgia, Nicholas, Sarah K., Calvo, Pier Luigi, Cant, Andrew, Edgar, J. David M., Español, Teresa, Ferrua, Francesca, Galicchio, Miguel, Gennery, Andrew R., Hadzic, Nedim, Hanson, I. Celine, Kusminsky, Gustavo, Lange, Andrzej, Lanternier, Fanny, Mahlaoui, Nizar, Moshous, Despina, Nademi, Zohreh, Neven, Benedicte, Oleastro, Matias, Porta, Fulvio, Quarello, Paola, Silva, Marcelo, Slatter, Mary A., Soncini, Elena, Stefanowicz, Marek, Tandoi, Francesco, Teisseyre, Mikołaj, Torgerson, Troy R., Veys, Paul, Weinacht, Katja G., Wolska-Kuśnierz, Beata, Pirenne, Jacques, de la Morena, M. Teresa, Meyts, Isabelle

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Fatal Anaphylaxis to Intravenous Co-Amoxiclav: A Case Series von Conlon, Niall P, Edgar, J David M

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Whole-genome sequencing of a sporadic primary immunodeficiency cohort von Thaventhiran, James E. D., Lango Allen, Hana, Burren, Oliver S., Rae, William, Greene, Daniel, Staples, Emily, Zhang, Zinan, Farmery, James H. R., Simeoni, Ilenia, Rivers, Elizabeth, Maimaris, Jesmeen, Penkett, Christopher J., Stephens, Jonathan, Deevi, Sri V. V., Sanchis-Juan, Alba, Gleadall, Nicholas S., Thomas, Moira J., Sargur, Ravishankar B., Gordins, Pavels, Baxendale, Helen E., Brown, Matthew, Tuijnenburg, Paul, Worth, Austen, Hanson, Steven, Linger, Rachel J., Buckland, Matthew S., Rayner-Matthews, Paula J., Gilmour, Kimberly C., Samarghitean, Crina, Seneviratne, Suranjith L., Sansom, David M., Lynch, Andy G., Megy, Karyn, Ellinghaus, Eva, Ellinghaus, David, Jorgensen, Silje F., Karlsen, Tom H., Stirrups, Kathleen E., Cutler, Antony J., Kumararatne, Dinakantha S., Chandra, Anita, Edgar, J. David M., Herwadkar, Archana, Cooper, Nichola, Grigoriadou, Sofia, Huissoon, Aarnoud P., Goddard, Sarah, Jolles, Stephen, Schuetz, Catharina, Boschann, Felix, Lyons, Paul A., Hurles, Matthew E., Savic, Sinisa, Burns, Siobhan O., Kuijpers, Taco W., Turro, Ernest, Ouwehand, Willem H., Thrasher, Adrian J., Smith, Kenneth G. C.

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