Mice transgenic for the human myotonic dystrophy region with expanded CTG repeats display muscular and brain abnormalities von SEZNEC, Hervé, AGBULUT, Onnik, FOUQUET, Coralie, BUTLER-BROWNE, Gillian, DELACOURTE, André, JUNIEN, Claudine, GOURDON, Geneviève, SERGEANT, Nicolas, SAVOURET, Cédric, GHESTEM, Antoine, TABTI, Nacira, WILLER, Jean-Claude, OURTH, Lucie, DUROS, Chantal, BRISSON, Edith

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Transgenic mice carrying large human genomic sequences with expanded CTG repeat mimic closely the DM CTG repeat intergenerational and somatic instability von SEZNEC, H, LIA-BALDINI, A.-S, DUROS, C, FOUQUET, C, LACROIX, C, HOFMANN-RADVANYI, H, JUNIEN, C, GOURDON, G

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Somatic Instability of the CTG Repeat in Mice Transgenic for the Myotonic Dystrophy Region is Age Dependent But Not Correlated to the Relative Intertissue Transcription Levels and... von Lia, Anne-Sophie, Seznec, Hervé, Hofmann-Radvanyi, Hélène, Radvanyi, François, Duros, Chantal, Saquet, Céline, Blanche, Martine, Junien, Claudine, Gourdon, Geneviève

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Myotonic dystrophy : size- and sex-dependent dynamics of CTG meiotic instability, and somatic mosaicism von LAVEDAN, C, HOFMANN-RADVANYI, H, SHELBOURNE, P, RABES, J.-P, DUROS, C, SAVOY, D, DEHAUPAS, I, LUCE, S, JOHNSON, K, JUNIEN, C

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Moderate intergenerational and somatic instability of a 55-CTG repeat in transgenic mice von Junien, Claudine, Gourdon, Geneviève, Blanche, Martine, Duros, Chantal, Abitbol, Marc, Hofmann-Radvanyi, Hlène, Radvanyi, François, Lia, Anne-Sophie

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Myotonic dystrophy: absence of CTG enlarged transcript in congenital forms, and low expression of the normal allele von Hofmann-Radvanyi, Hélène, Lavedan, Christian, Rabès, Jean-Pierre, Savoy, Daniel, Duros, Chantal, Johnson, Keith, Junien, Claudine

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