Absence of the cystic fibrosis transmembrane regulator (Cftr) from myeloid-derived cells slows resolution of inflammation and infection von Bonfield, T. L., Hodges, C. A., Cotton, C. U., Drumm, M. L.

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A G542X cystic fibrosis mouse model for examining nonsense mutation directed therapies von McHugh, Daniel R, Steele, Miarasa S, Valerio, Dana M, Miron, Alexander, Mann, Rachel J, LePage, David F, Conlon, Ronald A, Cotton, Calvin U, Drumm, Mitchell L, Hodges, Craig A

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Neutrophil-mediated phagocytic host defense defect in myeloid Cftr-inactivated mice von Ng, Hang Pong, Zhou, Yun, Song, Kejing, Hodges, Craig A, Drumm, Mitchell L, Wang, Guoshun

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Genetic Modifiers of Lung Disease in Cystic Fibrosis von Drumm, Mitchell L, Konstan, Michael W, Schluchter, Mark D, Handler, Allison, Pace, Rhonda, Zou, Fei, Zariwala, Maimoona, Fargo, David, Xu, Airong, Dunn, John M, Darrah, Rebecca J, Dorfman, Ruslan, Sandford, Andrew J, Corey, Mary, Zielenski, Julian, Durie, Peter, Goddard, Katrina, Yankaskas, James R, Wright, Fred A, Knowles, Michael R

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Mining GWAS and eQTL data for CF lung disease modifiers by gene expression imputation von Dang, Hong, Polineni, Deepika, Pace, Rhonda G, Stonebraker, Jaclyn R, Corvol, Harriet, Cutting, Garry R, Drumm, Mitchell L, Strug, Lisa J, O'Neal, Wanda K, Knowles, Michael R

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Functional genomics analysis of human colon organoids identifies key transcription factors von Yin, Shiyi, Ray, Greeshma, Kerschner, Jenny L, Hao, Shuyu, Perez, Aura, Drumm, Mitchell L, Browne, James A, Leir, Shih-Hsing, Longworth, Michelle, Harris, Ann

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Growth deficits in cystic fibrosis mice begin in utero prior to IGF-1 reduction von Darrah, Rebecca, Bederman, Ilya, Vitko, Megan, Valerio, Dana M, Drumm, Mitchell L, Hodges, Craig A

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Linaclotide improves gastrointestinal transit in cystic fibrosis mice by inhibiting sodium/hydrogen exchanger 3 von McHugh, Daniel R, Cotton, Calvin U, Moss, Fraser J, Vitko, Megan, Valerio, Dana M, Kelley, Thomas J, Hao, Shuyu, Jafri, Anjum, Drumm, Mitchell L, Boron, Walter F, Stern, Robert C, McBennett, Kimberly, Hodges, Craig A

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Dual Contrast - Magnetic Resonance Fingerprinting (DC-MRF): A Platform for Simultaneous Quantification of Multiple MRI Contrast Agents von Anderson, Christian E., Donnola, Shannon B., Jiang, Yun, Batesole, Joshua, Darrah, Rebecca, Drumm, Mitchell L., Brady-Kalnay, Susann M., Steinmetz, Nicole F., Yu, Xin, Griswold, Mark A., Flask, Chris A.

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Genetic variation and clinical heterogeneity in cystic fibrosis von Drumm, Mitchell L, Ziady, Assem G, Davis, Pamela B

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Genetic influences on cystic fibrosis lung disease severity von Weiler, Colleen A, Drumm, Mitchell L

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Classifying molecular phenotypes of G6PC variants for pathogenic properties and to guide therapeutic development von Plona, Kathleen L., Eastman, Jean F., Drumm, Mitchell L.

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Early pulmonary disease manifestations in cystic fibrosis mice von Darrah, Rebecca J, Mitchell, Anna L, Campanaro, Cara K, Barbato, Eric S, Litman, Paul, Sattar, Abdus, Hodges, Craig A, Drumm, Mitchell L, Jacono, Frank J

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Variants in Solute Carrier SLC26A9 Modify Prenatal Exocrine Pancreatic Damage in Cystic Fibrosis von Miller, Melissa R., PhD, Soave, David, MS, Li, Weili, MS, Gong, Jiafen, PhD, Pace, Rhonda G., BS, Boëlle, Pierre-Yves, PhD, Cutting, Garry R., MD, Drumm, Mitchell L., PhD, Knowles, Michael R., MD, Sun, Lei, PhD, Rommens, Johanna M., PhD, Accurso, Frank, MD, Durie, Peter R., MD, FRCP(C), Corvol, Harriet, MD, PhD, Levy, Hara, MD, Sontag, Marci K., PhD, Strug, Lisa J., PhD

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Identification of IFRD1 as a modifier gene for cystic fibrosis lung disease von Wills-Karp, Marsha, Chen, Jing, Knowles, Michael R, Flick, Leah M, Gu, YuanYuan, Thio, Chloe L, Huber, Lukas A, Ewart, Susan L, Vietor, Ilja, Williams, Adrienne H, Drumm, Mitchell L, Karp, Christopher L, Harley, Isaac T. W, Arshad, S. Hasan, Grimes, H. Leighton, Henderson, Lindsay B, Harley, John B, Langefeld, Carl D, Kilpatrick, Jeffrey R, Filippi, Marie-Dominique, Cutting, Garry R, Aronow, Bruce J, Jegga, Anil G

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A susceptibility gene for type 2 diabetes confers substantial risk for diabetes complicating cystic fibrosis von Blackman, S. M., Hsu, S., Ritter, S. E., Naughton, K. M., Wright, F. A., Drumm, M. L., Knowles, M. R., Cutting, G. R.

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ADEMA: an algorithm to determine expected metabolite level alterations using mutual information von Cicek, A Ercument, Bederman, Ilya, Henderson, Leigh, Drumm, Mitchell L, Ozsoyoglu, Gultekin

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Mucin variable number tandem repeat polymorphisms and severity of cystic fibrosis lung disease: significant association with MUC5AC von Guo, Xueliang, Pace, Rhonda G, Stonebraker, Jaclyn R, Commander, Clayton W, Dang, Anthony T, Drumm, Mitchell L, Harris, Ann, Zou, Fei, Swallow, Dallas M, Wright, Fred A, O'Neal, Wanda K, Knowles, Michael R

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Gene Expression in Transformed Lymphocytes Reveals Variation in Endomembrane and HLA Pathways Modifying Cystic Fibrosis Pulmonary Phenotypes von O’Neal, Wanda K., Gallins, Paul, Pace, Rhonda G., Dang, Hong, Wolf, Whitney E., Jones, Lisa C., Guo, XueLiang, Zhou, Yi-Hui, Madar, Vered, Huang, Jinyan, Liang, Liming, Moffatt, Miriam F., Cutting, Garry R., Drumm, Mitchell L., Rommens, Johanna M., Strug, Lisa J., Sun, Wei, Stonebraker, Jaclyn R., Wright, Fred A., Knowles, Michael R.

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Generation of a conditional null allele for Cftr in mice von Hodges, Craig A., Cotton, Calvin U., Palmert, Mark R., Drumm, Mitchell L.

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