Sex Genotyping of Archival Fixed and Immunolabeled Guinea Pig Cochleas von Depreux, Frédéric F., Czech, Lyubov, Whitlon, Donna S.

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Nesprin-1 mutations in human and murine cardiomyopathy von Puckelwartz, Megan J, Kessler, Eric J, Kim, Gene, DeWitt, Megan M, Zhang, Yuan, Earley, Judy U, Depreux, Frederic F.S, Holaska, James, Mewborn, Stephanie K, Pytel, Peter, McNally, Elizabeth M

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Fine-tuning of Notch signaling sets the boundary of the organ of Corti and establishes sensory cell fates von Basch, Martin L, Brown, 2nd, Rogers M, Jen, Hsin-I, Semerci, Fatih, Depreux, Frederic, Edlund, Renée K, Zhang, Hongyuan, Norton, Christine R, Gridley, Thomas, Cole, Susan E, Doetzlhofer, Angelika, Maletic-Savatic, Mirjana, Segil, Neil, Groves, Andrew K

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Lunatic fringe-mediated Notch signaling regulates adult hippocampal neural stem cell maintenance von Semerci, Fatih, Choi, William Tin-Shing, Bajic, Aleksandar, Thakkar, Aarohi, Encinas, Juan Manuel, Depreux, Frederic, Segil, Neil, Groves, Andrew K, Maletic-Savatic, Mirjana

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Hearing differences in Hartley guinea pig stocks from two breeders von Whitlon, Donna S., Young, Hunter, Barna, Mark, Depreux, Frédéric, Richter, Claus-Peter

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Statins protect mice from high-decibel noise-induced hearing loss von Dépreux, Frédéric, Czech, Lyubov, Young, Hunter, Richter, Claus-Peter, Zhou, Yingjie, Whitlon, Donna S.

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Eya4-deficient mice are a model for heritable otitis media von Depreux, Frederic F S, Darrow, Keith, Conner, David A, Eavey, Roland D, Liberman, M Charles, Seidman, Christine E, Seidman, J G

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Rescue of peripheral vestibular function in Usher syndrome mice using a splice-switching antisense oligonucleotide von Vijayakumar, Sarath, Depreux, Frederic F, Jodelka, Francine M, Lentz, Jennifer J, Rigo, Frank, Jones, Timothy A, Hastings, Michelle L

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Mutation in the transcriptional coactivator EYA4 causes dilated cardiomyopathy and sensorineural hearing loss von Seidman, Christine E, Schönberger, Jost, Wang, Libin, Shin, Jordan T, Kim, Sang Do, Depreux, Frederic F S, Zhu, Hao, Zon, Leonard, Pizard, Anne, Kim, Jae B, MacRae, Calum A, Mungall, Andy J, Seidman, J G

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Antisense oligonucleotides delivered to the amniotic cavity in utero modulate gene expression in the postnatal mouse von Depreux, Frederic F, Wang, Lingyan, Jiang, Han, Jodelka, Francine M, Rosencrans, Robert F, Rigo, Frank, Lentz, Jennifer J, Brigande, John V, Hastings, Michelle L

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Rescue of Outer Hair Cells with Antisense Oligonucleotides in Usher Mice Is Dependent on Age of Treatment von Ponnath, Abhilash, Depreux, Frederic F., Jodelka, Francine M., Rigo, Frank, Farris, Hamilton E., Hastings, Michelle L., Lentz, Jennifer J.

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Disruption of the lamin A and matrin-3 interaction by myopathic LMNA mutations von Depreux, Frederic F, Puckelwartz, Megan J, Augustynowicz, Aleksandra, Wolfgeher, Don, Labno, Christine M, Pierre-Louis, Dynora, Cicka, Danielle, Kron, Stephen J, Holaska, James, McNally, Elizabeth M

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Antisense oligonucleotide therapy rescues disruptions in organization of exploratory movements associated with Usher syndrome type 1C in mice von Donaldson, Tia N., Jennings, Kelsey T., Cherep, Lucia A., McNeela, Adam M., Depreux, Frederic F., Jodelka, Francine M., Hastings, Michelle L., Wallace, Douglas G.

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Gene expression, chromosome position and lamin A/C mutations von Puckelwartz, Megan J., Depreux, Frederic F.S., McNally, Elizabeth M.

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Ca²⁺ dysregulation in Ryr1I⁴⁸⁹⁵T/wt mice causes congenital myopathy with progressive formation of minicores, cores, and nemaline rods von Zvaritch, Elena, Kraeva, Natasha, Bombardier, Eric, McCloy, Robert A, Depreux, Frederic, Holmyard, Douglas, Kraev, Alexander, Seidman, Christine E, Seidman, J.G, Tupling, A. Russell, MacLennan, David H

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Ryr1I⁴⁸⁹⁵T mutation abolishes Ca²⁺ release channel function and delays development in homozygous offspring of a mutant mouse line von Zvaritch, Elena, Depreux, Frederic, Kraeva, Natasha, Loy, Ryan E, Goonasekera, Sanjeewa A, Boncompagi, Simona, Kraev, Alexander, Gramolini, Anthony O, Dirksen, Robert T, Franzini-Armstrong, Clara, Seidman, Christine E, Seidman, J.G, MacLennan, David H

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An$Ryr1^{I4895T}$Mutation Abolishes Ca²⁺ Release Channel Function and Delays Development in Homozygous Offspring of a Mutant Mouse Line von Zvaritch, Elena, Depreux, Frederic, Kraeva, Natasha, Loy, Ryan E., Goonasekera, Sanjeewa A., Boncompagi, Simona, Kraev, Alexander, Gramolini, Anthony O., Dirksen, Robert T., Franzini-Armstrong, Clara, Seidman, Christine E., Seidman, J. G., MacLennan, David H.

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Ca²⁺ dysregulation in$Ryr1^{14895T/wt} $Mice Causes Congenital Myopathy with Progressive Formation of Minicores, Cores, and Nemaline Rods von Zvaritch, Elena, Kraeva, Natasha, Bombardier, Eric, McCloy, Robert A., Depreux, Frederic, Holmyard, Douglas, Kraev, Alexander, Seidman, Christine E., Seidman, J. G., Tupling, A. Russell, MacLennan, David H.

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Ca^sup 2+^ dysregulation in Ryr1^sup I4895T/wt^ mice causes congenital myopathy with progressive formation of minicores, cores, and nemaline rods von Zvaritch, Elena, Kraeva, Natasha, Bombardier, Eric, McCloy, Robert A, Depreux, Frederic, Holmyard, Douglas, Kraev, Alexander, Seidman, Christine E, Seidman, J G, Tupling, A Russell, MacLennan, David H

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Ca 2+ dysregulation in Ryr1 I4895T/wt mice causes congenital myopathy with progressive formation of minicores, cores, and nemaline rods von Zvaritch, Elena, Kraeva, Natasha, Bombardier, Eric, McCloy, Robert A., Depreux, Frederic, Holmyard, Douglas, Kraev, Alexander, Seidman, Christine E., Seidman, J. G., Tupling, A. Russell, MacLennan, David H.

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