Towards sustainability assessment of machining processes von Hegab, H.A., Darras, B., Kishawy, H.A.

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Sustainability Assessment of Machining with Nano-Cutting Fluids von Hegab, H., Darras, B., Kishawy, H.A.

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Six-Minute Walk Test demonstrates motor fatigue in spinal muscular atrophy von MONTES, J, MCDERMOTT, M. P, CHUNG, W. K, DARRAS, B. T, DE VIVO, D. C, KAUFMANN, P, FINKEL, R. S, MARTENS, W. B, DUNAWAY, S, GLANZMAN, A. M, RILEY, S, QUIGLEY, J, MONTGOMERY, M. J, SPROULE, D, TAWIL, R

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Friction stir processing of commercial AZ31 magnesium alloy von Darras, B.M., Khraisheh, M.K., Abu-Farha, F.K., Omar, M.A.

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Sustainable Cooling and Lubrication Strategies in Machining Processes: A Comparative Study von Hegab, H., Kishawy, H.A., Darras, B.

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RAPID-ONSET DYSTONIA-PARKINSONISM IN A CHILD WITH A NOVEL ATP1A3 GENE MUTATION von ANSELM, I. A, SWEADNER, K. J, GOLLAMUDI, S, OZELIUS, L. J, DARRAS, B. T

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Progression of spinal deformity in wheelchair-dependent patients with Duchenne muscular dystrophy who are not treated with steroids: coronal plane (scoliosis) and sagittal plane (k... von Shapiro, F, Zurakowski, D, Bui, T, Darras, B T

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Electrical impedance myography for the assessment of children with muscular dystrophy: a preliminary study von Rutkove, S B, Darras, B T

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Pediatric sciatic neuropathies: A 30-year prospective study von SRINIVASAN, J, RYAN, M. M, ESCOLAR, D. M, DARRAS, B, JONES, H. R

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S12 Onasemnogene abeparvovec gene therapy for spinal muscular atrophy type 1: phase 3 study (STR1VE-US) von Finkel, RS, Connolly, AM, Darras, BT, Iannaccone, ST, Kuntz, NL, Peña, LDM, Smith, EC, Chiriboga, CA, Crawford, TO, Shieh, PB, Kwon, JM, Zaidman, CM, Schultz, M, Kausar, I, Chand, D, Tauscher-Wisniewski, S, Ouyang, H, Macek, TA, Mendell, JR

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S61 Onasemnogene abeparvovec gene-replacement therapy (GRT) for spinal muscular atrophy type 1 (SMA1): preliminary pulmonary and ventilatory findings from the phase 3 study (STR1VE... von Shell, R, Day, JW, Chiriboga, CA, Crawford, TO, Darras, BT, Finkel, RS, Connolly, AM, Iannaccone, ST, Kuntz, NL, Peña, LDM, Shieh, PB, Smith, EC, Kausar, I, Schultz, M, Feltner, DE, Ogrinc, FG, Macek, TA, Kernbauer, E, L’Italien, J, Sproule, DM, Kaspar, BK, Mendell, JR

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Electrical impedance myography in Duchenne muscular dystrophy detects disease progression in boys younger than 7 years of age von Darras, B, Wu, J, Zaidman, C, Kapur, K, Yim, S, Pasternak, A, Madabusi, L, Szelag, H, Harrington, T, Li, J, Pacheck, A, Rutkove, S

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Should motor function determine the timing of scoliosis surgery in spinal muscular atrophy? von Dunaway Young, S, Montes, J, Salazar, R, Glanzman, A, Pasternak, A, Quigley, J, Ciurylo, E, Riley, S, Martens, W, Gee, R, Duong, T, Civitello, M, Chiriboga, C, Tennekoon, G, Day, J, Finkel, R, Darras, B, De Vivo, D

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Revised Hammersmith scale for spinal muscular atrophy: Longitudinal changes over six and twelve months in a large international cohort von Ramsey, D, Scoto, M, Mayhew, A, Main, M, Mazzone, E, Montes, J, Dunaway, S, Salazar, R, Glanzman, A, Pasternak, A, Duong, T, Gee, R, Civitello, M, Bushby, K, Day, J, Darras, B, De Vivo, D, Finkel, R, Mercuri, E, Muntoni, F

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Efficacy and safety of nusinersen in infants with spinal muscular atrophy (SMA): Final results from the phase 3 ENDEAR study von Finkel, R, Kuntz, N, Mercuri, E, Chiriboga, C.A, Darras, B, Topaloglu, H, Montes, J, Su, J, Zhong, Z.J, Gheuens, S, Bennett, C.F, Schneider, E, Farwell, W

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Steroid-responsive neurologic relapses in a child with a proteolipid protein-1 mutation von GORMAN, M. P, GOLOMB, M. R, WALSH, L. E, HOBSON, G. M, GARBERN, J. Y, KINKEL, R. P, DARRAS, B. T, URION, D. K, EKSIOGLU, Y. Z

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Interim analysis of the phase 3 CHERISH study evaluating nusinersen in patients with later-onset spinal muscular atrophy (SMA): Primary and descriptive secondary endpoints von Mercuri, E, Finkel, R, Kirschner, J, Chiriboga, C.A, Kuntz, N, Darras, B, Shieh, P.B, Saito, K, De Vivo, D.C, Mazzone, E.S, Montes, J, Yang, Q, Zhong, Z.J, Gheuens, S, Bennett, C.F, Schneider, E, Farwell, W

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Patterns of disease progression in type 2 and 3 SMA: Implications for clinical trials von Mercuri, E, Finkel, R, Montes, J, Mazzone, E, Main, M, Ramsey, D, Mayhew, A, Glanzman, A, Pasternak, A, Pane, M, Pera, M, Scoto, M, Messina, S, Vita, G, D'Amico, A, Darras, B, Bertini, E, Muntoni, F, De Vivo, D

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Safety and Efficacy of Carvedilol Therapy for Patients with Dilated Cardiomyopathy Secondary to Muscular Dystrophy von Rhodes, J., Margossian, R., Darras, B. T., Colan, S. D., Jenkins, K. J., Geva, T., Powell, A. J.

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Prospective cohort study of spinal muscular atrophy types 2 and 3 von KAUFMANN, Petra, MCDERMOTT, Michael P, YANG, Michele L, TAWIL, Rabi, CHUNG, Wendy K, MARTENS, William B, MONTES, Jacqueline, BATTISTA, Vanessa, O'HAGEN, Jessica, DUNAWAY, Sally, FLICKINGER, Jean, QUIGLEY, Janet, DARRAS, Basil T, RILEY, Susan, GLANZMAN, Allan M, BENTON, Maryjane, RYAN, Patricia A, PUNYANITYA, Mark, MONTGOMERY, Megan J, MARRA, Jonathan, KOO, Benjamin, DE VIVO, Darryl C, FINKEL, Richard S, SPROULE, Douglas M, KANG, Peter B, OSKOUI, Maryam, CONSTANTINESCU, Andrei, GOOCH, Clifton L, REGHAN FOLEY, A

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