Pathogenesis of malnutrition in cystic fibrosis, and its treatment von PENCHARZ, P.B., DURIE, P.R.

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214: Retrospective Case Control Study Comparing Outcomes Post-Lung Transplantation in Cystic Fibrosis Patients with and without Cystic Fibrosis-Related Liver Cirrhosis von Nash, E.F, Coonar, A.S, Durie, P.R, Singer, L.G, Keshavjee, S, Chaparro, C

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A novel paradigm for attributing the diagnosis of CF disease von Ooi, C.Y, Tullis, E, Dupuis, A, Gonska, T, Ellis, L, Martin, S, Schibli, S, Jarvi, K, Zielenski, J, Durie, P.R

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CF diagnosis algorithms: challenging dogma von Ooi, C.Y, Durie, P.R, Gonska, T, Dupuis, A, Ellis, L, Martin, S, Jarvi, K, Schibli, S, Zielenski, J, Tullis, E

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Outcome in Cystic Fibrosis Liver Disease von Rowland, M, Gallagher, C, Canny, G, Greally, P, Slattery, D, Hayes, R, O'Laoide, R, Daly, L, Durie, P.R, Bourke, B

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Improvement in ion transport biomarkers and spirometry with the investigational CFTR potentiator VX-770 in subjects with cystic fibrosis and the G551D-CFTR mutation von Rowe, S.M, Accurso, F.J, Clancy, J.P, Boyle, M.P, Dunitz, J.M, Durie, P.R, Sagel, S.D, Hornick, D.B, Konstan, M.W, Donaldson, S.H, Moss, R.B, Pilewski, J.M, Rubenstein, R, Uluer, D.B, Aitken, M.L, Dong, Q, Ordonez, C.L, Campbell, P.W, Ashlock, M.A, Ramsey, B.W

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Final results of a 14- and 28-day study of VX-770 in subjects with CF von Accurso, F.J, Rowe, S.M, Durie, P.R, Konstan, M.W, Dunitz, J, Hornick, D.B, Sagel, S.D, Boyle, M.P, Uluer, A.Z, Moss, R.B, Ramsey, B.W, Freedman, S.D, Dong, Q, Zha, J, Stone, A.J, Olson, E.R, Ordonez, C.L, Clancy, J.P, Campbell, P.W, Ashlock, M.A

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Outcomes of patients with cystic fibrosis undergoing lung transplantation with and without cystic fibrosis-associated liver cirrhosis von Nash, E.F., Volling, C., Gutierrez, C.A., Tullis, E., Coonar, A., McRae, K., Keshavjee, S., Singer, L.G., Durie, P.R., Chaparro, C.

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Cystic fibrosis modifier genes related to Pseudomonas aeruginosa infection von Park, J E, Yung, R, Stefanowicz, D, Shumansky, K, Akhabir, L, Durie, P R, Corey, M, Zielenski, J, Dorfman, R, Daley, D, Sandford, A J

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Does the Macroduct ® collection system reliably define sweat chloride concentration in subjects with intermediate results? von Rose, J.B., Ellis, L., John, B., Martin, S., Gonska, T., Solomon, M., Tullis, E., Corey, M., Adeli, K., Durie, P.R.

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Segregation Analysis in Shwachman-Diamond Syndrome: Evidence for Recessive Inheritance von Ginzberg, H., Shin, J., Ellis, L., Goobie, S., Morrison, J., Corey, M., Durie, P.R., Rommens, J.M.

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Challenges in the dietary treatment of cystic fibrosis related diabetes mellitus von Wilson, D.C., Kalnins, D., Stewart, C., Hamilton, N., Hanna, A.K., Durie, P.R., Tullis, E., Pencharz, P.B.

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The assessment of nutritional status in children von Moore, D.J., Durie, P.R., Forstner, G.G., Pencharz, P.B.

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Acute pancreatitis in childhood von Weizman, Z., Durie, P.R.

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Longitudinal evaluation of serum trypsinogen measurement in pancreatic-insufficient and pancreatic-sufficient patients with cystic fibrosis von Couper, R.T.L., Corey, M., Durie, P.R., Forstner, G.G., Moore, D.J.

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Nutritional management of cystic fibrosis von Pencharz, P.B, Durie, P.R

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Malabsorption of medium-chain triglycerides in infants with cystic fibrosis: Correction with pancreatic enzyme supplements von Durie, P.R., Newth, C.J., Forstner, G.G., Gall, D.G.

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Dietary intakes of young children with cystic fibrosis: Is there a difference? von Bentur, L, Kalnins, D, Levison, H, Corey, M, Durie, P R

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Recommendations for management of liver and biliary tract disease in cystic fibrosis von Sokol, R.J. (The Children's Hospital, Denver, CO.), Durie, P.R

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Colipase and lipase secretion in childhood-onset pancreatic insufficiency: Delineation of patients with steatorrhea secondary to relative colipase deficiency von Gaskin, K.J., Durie, P.R., Lee, L., Hill, R., Forstner, G.G.

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