A biophysical basis for mucus solids concentration as a candidate biomarker for airways disease von Hill, David B, Vasquez, Paula A, Mellnik, John, McKinley, Scott A, Vose, Aaron, Mu, Frank, Henderson, Ashley G, Donaldson, Scott H, Alexis, Neil E, Boucher, Richard C, Forest, M Gregory

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Cystic fibrosis airway secretions exhibit mucin hyperconcentration and increased osmotic pressure von Henderson, Ashley G, Ehre, Camille, Button, Brian, Abdullah, Lubna H, Cai, Li-Heng, Leigh, Margaret W, DeMaria, Genevieve C, Matsui, Hiro, Donaldson, Scott H, Davis, C William, Sheehan, John K, Boucher, Richard C, Kesimer, Mehmet

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An Improved Inhaled Mucolytic to Treat Airway Muco-obstructive Diseases von Ehre, Camille, Rushton, Zachary L, Wang, Boya, Hothem, Lauren N, Morrison, Cameron B, Fontana, Nicholas C, Markovetz, Matthew R, Delion, Martial F, Kato, Takafumi, Villalon, Diane, Thelin, William R, Esther, Jr, Charles R, Hill, David B, Grubb, Barbara R, Livraghi-Butrico, Alessandra, Donaldson, Scott H, Boucher, Richard C

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Sodium Channels and Cystic Fibrosis von Donaldson, Scott H., Boucher, Richard C.

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Analysis of Depression and Anxiety Scores Following Initiation of Elexacaftor/Tezacaftor/Ivacaftor in Adults With Cystic Fibrosis von Pudukodu, Harish, Powell, Margret Z, Ceppe, Agathe, Donaldson, Scott H, Goralski, Jennifer L, Sowa, Nathaniel A

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SPLUNC1 Regulates Airway Surface Liquid Volume by Protecting ENaC from Proteolytic Cleavage von Garcia-Caballero, Agustin, Rasmussen, Julia E., Gaillard, Erol, Watson, Michael J., Olsen, John C., Donaldson, Scott H., Stutts, M. Jackson, Tarran, Robert, Agre, Peter C.

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Neutrophil serine proteases in cystic fibrosis: role in disease pathogenesis and rationale as a therapeutic target von Mall, Marcus A, Davies, Jane C, Donaldson, Scott H, Jain, Raksha, Chalmers, James D, Shteinberg, Michal

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Multicenter intestinal current measurements in rectal biopsies from CF and non-CF subjects to monitor CFTR function von Clancy, John P, Szczesniak, Rhonda D, Ashlock, Melissa A, Ernst, Sarah E, Fan, Lijuan, Hornick, Douglas B, Karp, Philip H, Khan, Umer, Lymp, James, Ostmann, Alicia J, Rezayat, Amir, Starner, Timothy D, Sugandha, Shajan P, Sun, Hongtao, Quinney, Nancy, Donaldson, Scott H, Rowe, Steven M, Gabriel, Sherif E

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Exercising our options: comparing effects of exercise and positive expiratory pressure on mucociliary clearance von Donaldson, Scott H

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Clinical Effectiveness of Elexacaftor/Tezacaftor/Ivacaftor in People with Cystic Fibrosis: A Clinical Trial von Nichols, David P, Paynter, Alex C, Heltshe, Sonya L, Donaldson, Scott H, Frederick, Carla A, Freedman, Steven D, Gelfond, Daniel, Hoffman, Lucas R, Kelly, Andrea, Narkewicz, Michael R, Pittman, Jessica E, Ratjen, Felix, Rosenfeld, Margaret, Sagel, Scott D, Schwarzenberg, Sarah Jane, Singh, Pradeep K, Solomon, George M, Stalvey, Michael S, Clancy, John P, Kirby, Shannon, Van Dalfsen, Jill M, Kloster, Margaret H, Rowe, Steven M

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Tezacaftor/Ivacaftor in Subjects with Cystic Fibrosis and F508del/F508del-CFTR or F508del/G551D-CFTR von Donaldson, Scott H, Pilewski, Joseph M, Griese, Matthias, Cooke, Jon, Viswanathan, Lakshmi, Tullis, Elizabeth, Davies, Jane C, Lekstrom-Himes, Julie A, Wang, Linda T

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Clinical mechanism of the cystic fibrosis transmembrane conductance regulator potentiator ivacaftor in G551D-mediated cystic fibrosis von Rowe, Steven M, Heltshe, Sonya L, Gonska, Tanja, Donaldson, Scott H, Borowitz, Drucy, Gelfond, Daniel, Sagel, Scott D, Khan, Umer, Mayer-Hamblett, Nicole, Van Dalfsen, Jill M, Joseloff, Elizabeth, Ramsey, Bonnie W

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Analysis of the Bacterial Communities Present in Lungs of Patients with Cystic Fibrosis from American and British Centers von Stressmann, Franziska A, Rogers, Geraint B, Klem, Erich R, Lilley, Andrew K, Donaldson, Scott H, Daniels, Thomas W, Carroll, Mary P, Patel, Nilesh, Forbes, Benjamin, Boucher, Richard C, Wolfgang, Matthew C, Bruce, Kenneth D

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Inhaled dry powder alginate oligosaccharide in cystic fibrosis: a randomised, double-blind, placebo-controlled, crossover phase 2b study von van Koningsbruggen-Rietschel, Silke, Davies, Jane C., Pressler, Tacjana, Fischer, Rainald, MacGregor, Gordon, Donaldson, Scott H., Smerud, Knut, Meland, Nils, Mortensen, Jann, Fosbol, Marie O., Downey, Damian G., Myrset, Astrid H., Flaten, Hugo, Rye, Philip D.

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Effect of hypertonic saline on mucociliary clearance and clinical outcomes in chronic bronchitis von Bennett, William D., Henderson, Ashley G., Ceppe, Agathe, Zeman, Kirby L., Wu, Jihong, Gladman, Christine, Fuller, Fred, Gazda, Stephen, Button, Brian, Boucher, Richard C., Donaldson, Scott H.

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Ivacaftor withdrawal syndrome in cystic fibrosis patients with the G551D mutation von Trimble, Aaron T., Donaldson, Scott H.

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Regulation of the Epithelial Sodium Channel by Serine Proteases in Human Airways von Donaldson, Scott H., Hirsh, Andrew, Li, Dong Chen, Holloway, Ginger, Chao, Julie, Boucher, Richard C., Gabriel, Sherif E.

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Current state of CFTR modulators for treatment of Cystic Fibrosis von Despotes, Katherine A., Donaldson, Scott H.

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Airway Mucus Hyperconcentration in Non-Cystic Fibrosis Bronchiectasis von Ramsey, Kathryn A, Chen, Alice C H, Radicioni, Giorgia, Lourie, Rohan, Martin, Megan, Broomfield, Amy, Sheng, Yong H, Hasnain, Sumaira Z, Radford-Smith, Graham, Simms, Lisa A, Burr, Lucy, Thornton, David J, Bowler, Simon D, Livengood, Stephanie, Ceppe, Agathe, Knowles, Michael R, Noone, Sr, Peadar G, Donaldson, Scott H, Hill, David B, Ehre, Camille, Button, Brian, Alexis, Neil E, Kesimer, Mehmet, Boucher, Richard C, McGuckin, Michael A

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Alterations in lipids after initiation of highly effective modulators in people with cystic fibrosis von Despotes, Katherine A., Ceppe, Agathe S., Donaldson, Scott H.

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