Recommendations for the classification of diseases as CFTR-related disorders von Bombieri, C, Claustres, M, De Boeck, K, Derichs, N, Dodge, J, Girodon, E, Sermet, I, Schwarz, M, Tzetis, M, Wilschanski, M, Bareil, C, Bilton, D, Castellani, C, Cuppens, H, Cutting, G.R, Drevínek, P, Farrell, P, Elborn, J.S, Jarvi, K, Kerem, B, Kerem, E, Knowles, M, Macek, M, Munck, A, Radojkovic, D, Seia, M, Sheppard, D.N, Southern, K.W, Stuhrmann, M, Tullis, E, Zielenski, J, Pignatti, P.F, Ferec, C

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Cystic Fibrosis Screen Positive, Inconclusive Diagnosis (CFSPID): A new designation and management recommendations for infants with an inconclusive diagnosis following newborn scre... von Munck, A, Mayell, S.J, Winters, V, Shawcross, A, Derichs, N, Parad, R, Barben, J, Southern, K.W

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CFTR biomarkers: time for promotion to surrogate end-point? von DE BOECK, K, KENT, L, MELOTTI, P, DANNER-BOUCHER, I, BOERNER, S, FAJAC, I, SOUTHERN, K, DE NOOIJER, R. A, BOT, A, DE RIJKE, Y, DE WACHTER, E, LEAL, T, DAVIES, J, VERMEULEN, F, HUG, M. J, RAULT, G, NGUYEN-KHOA, T, BARRETO, C, PROESMANS, M, DERICHS, N, AMARAL, M, ROWE, S. M, MIDDLETON, P, DE JONGE, H, BRONSVELD, I, WILSCHANSKI, M

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Real life practice of sweat testing in Europe von Cirilli, N., Southern, K.W., Buzzetti, R., Barben, J., Nährlich, L., Munck, A., Wilschanski, M., De Boeck, K., Derichs, N.

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New clinical diagnostic procedures for cystic fibrosis in Europe von De Boeck, K, Derichs, N, Fajac, I, de Jonge, H.R, Bronsveld, I, Sermet, I, Vermeulen, F, Sheppard, D.N, Cuppens, H, Hug, M, Melotti, P, Middleton, P.G, Wilschanski, M

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Phenotypic characterisation of patients with intermediate sweat chloride values: towards validation of the European diagnostic algorithm for cystic fibrosis von Goubau, C, Wilschanski, M, Skalická, V, Lebecque, P, Southern, K W, Sermet, I, Munck, A, Derichs, N, Middleton, P G, Hjelte, L, Padoan, R, Vasar, M, De Boeck, K

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Evaluation of portal venous gas detected by ultrasound examination for diagnosis of necrotising enterocolitis von Dördelmann, M, Rau, G A, Bartels, D, Linke, M, Derichs, N, Behrens, C, Bohnhorst, B

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WS11.4 Real life practice of sweat testing in Europe: results from an ECFS-wide survey von Cirilli, N, Buzzetti, R, Southern, K.W, Barben, J, Nährlich, L, Munck, A, Wilschanski, M, De Boeck, K, Derichs, N

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WS7.2 Ex vivo effect of CFTR modulators VX770, VX809 and PTC124 on CFTR-mediated chloride secretion in rectal biopsies from CF patients von Scheinert, S, Pinders-Kessel, L, Derichs, N

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WS18.4 Intestinal current measurement as outcome marker for clinical trials: the ECFS CTN certification process and central reading core facility von Scheinert, S, de Jonge, H, Bronsveld, I, Nahrlich, L, Melotti, P, van Koningsbruggen-Rietschel, S, Sermet-Gaudelus, I, Hayes, K, Derichs, N

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55 Reliability of intestinal current measurement as CFTR biomarker and responsiveness to oral ivacaftor treatment von Scheinert, S, Pinders-Kessel, L, Klosinski, M, Derichs, N

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EPS1.3 Safety, tolerability and early signs of efficacy with riociguat for the treatment of adult Phe508del homozygous cystic fibrosis patients: study design and rationale for the... von Derichs, N, Taylor-Cousar, J, Tullis, E, Davies, J, Nazareth, D, Downey, D.G, Rosenbluth, D, Fajac, I, Malfroot, A, Bakker, M, Clancy, J.P, Uluer, A, Castellani, C, Sermet-Gaudelus, I, Ahrens, R.C, Sutharsan, S, Welte, T, Gust, T, Kaiser, A, Hoffmann, A, Ratjen, F, Rowe, S

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WS11.6 Current status of early CF diagnosis in Latin America: results from the 1st LANES meeting von Derichs, N, Pirs, A. Kotnik, Jung, A, Aponte, G.B, Boza, M.L, Castanos, C, Chaustre, I, Chong, E, Onate, L. Cordero, Hoepker, A, Lezana, J.L, Maestre, M, Palomo, L. Rosal, Pinchak, C, Filho, L.V. Ferreira da Silva, Vasquez-Mobile, C, Mastoridis, P

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WS10.6 Organ-specific CFTR dysfunction: Comparison of biomarkers for CF diagnosis and CFTR modulator effects von Pinders-Kessel, L, Scheinert, S, Klosinski, M, Staab, D, Derichs, N

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Diversity of the basic defect of homozygous CFTR mutation genotypes in humans von Stanke, F, Ballmann, M, Bronsveld, I, Dörk, T, Gallati, S, Laabs, U, Derichs, N, Ritzka, M, Posselt, H-G, Harms, H K, Griese, M, Blau, H, Mastella, G, Bijman, J, Veeze, H, Tümmler, B

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24 ENaC-related disorder as a new CF-like clinical entity von Norek, A, Scheinert, S, Kusmierek, E, Chrzescijanska, E, Nowakowska, A, Sapiejka, E, Swierczynska, B, Sands, D, Derichs, N

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Intestinal current measurement for diagnostic classification of patients with questionable cystic fibrosis: validation and reference data von Derichs, Nico, Sanz, Javier, Von Kanel, Thomas, Stolpe, Cornelia, Zapf, Antonia, Tümmler, Burkhard, Gallati, Sabina, Ballmann, Manfred

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64 Correction o ΔF508-CFTR in human airway epithelia and ex vivo rectal biopsies by s-cis -locked bithiazole corrector-29 von Derichs, N, Tran, D, Namkung, W, Finkbeiner, W.E, Kurth, M.J, Nielson, D.W, Verkman, A.S

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Intestinal current measurement for difficult CF diagnosis: reference values and reproducibility von Derichs, N, Stolpe, C, Tümmler, B, Ballmann, M

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52 Protein analysis of mutant CFTR in human tissues von van Barneveld, A, Zander, I, Hyde, R, Länger, F, Simon, A, Junge, S, Ballmann, M, Derichs, N, Tümmler, B

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