The glutamate/cystine xCT antiporter antagonizes glutamine metabolism and reduces nutrient flexibility von Shin, Chun-Shik, Mishra, Prashant, Watrous, Jeramie D., Carelli, Valerio, D’Aurelio, Marilena, Jain, Mohit, Chan, David C.

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Rewiring of Glutamine Metabolism Is a Bioenergetic Adaptation of Human Cells with Mitochondrial DNA Mutations von Chen, Qiuying, Kirk, Kathryne, Shurubor, Yevgeniya I., Zhao, Dazhi, Arreguin, Andrea J., Shahi, Ifrah, Valsecchi, Federica, Primiano, Guido, Calder, Elizabeth L., Carelli, Valerio, Denton, Travis T., Beal, M. Flint, Gross, Steven S., Manfredi, Giovanni, D'Aurelio, Marilena

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High fat diet ameliorates mitochondrial cardiomyopathy in CHCHD10 mutant mice von Southwell, Nneka, Manzo, Onorina, Bacman, Sandra, Zhao, Dazhi, Sayles, Nicole M, Dash, Jalia, Fujita, Keigo, D’Aurelio, Marilena, Di Lorenzo, Annarita, Manfredi, Giovanni, Kawamata, Hibiki

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Determination of Coenzyme A and Acetyl-Coenzyme A in Biological Samples Using HPLC with UV Detection von Shurubor, Yevgeniya I, D'Aurelio, Marilena, Clark-Matott, Joanne, Isakova, Elena P, Deryabina, Yulia I, Beal, M Flint, Cooper, Arthur J L, Krasnikov, Boris F

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Barth syndrome: Cellular compensation of mitochondrial dysfunction and apoptosis inhibition due to changes in cardiolipin remodeling linked to tafazzin (TAZ) gene mutation von Gonzalvez, François, D'Aurelio, Marilena, Boutant, Marie, Moustapha, Aoula, Puech, Jean-Philippe, Landes, Thomas, Arnauné-Pelloquin, Laeticia, Vial, Guillaume, Taleux, Nellie, Slomianny, Christian, Wanders, Ronald J., Houtkooper, Riekelt H., Bellenguer, Pascale, Møller, Ian Max, Gottlieb, Eyal, Vaz, Frederic M., Manfredi, Giovanni, Petit, Patrice X.

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Prohibitin reduces mitochondrial free radical production and protects brain cells from different injury modalities von Zhou, Ping, Qian, Liping, D'Aurelio, Marilena, Cho, Sunghee, Wang, Gang, Manfredi, Giovanni, Pickel, Virginia, Iadecola, Costantino

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Distinct intracellular sAC-cAMP domains regulate ER Ca2+ signaling and OXPHOS function von Valsecchi, Federica, Konrad, Csaba, D'Aurelio, Marilena, Ramos-Espiritu, Lavoisier S., Stepanova, Anna, Burstein, Suzanne R., Galkin, Alexander, Magranè, Jordi, Starkov, Anatoly, Buck, Jochen, Levin, Lonny R., Manfredi, Giovanni

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A coordinated multiorgan metabolic response contributes to human mitochondrial myopathy von Southwell, Nneka, Primiano, Guido, Nadkarni, Viraj, Attarwala, Nabeel, Beattie, Emelie, Miller, Dawson, Alam, Sumaitaah, Liparulo, Irene, Shurubor, Yevgeniya I, Valentino, Maria Lucia, Carelli, Valerio, Servidei, Serenella, Gross, Steven S, Manfredi, Giovanni, Chen, Qiuying, D'Aurelio, Marilena

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A role of mitochondrial complex II defects in genetic models of Huntington's disease expressing N-terminal fragments of mutant huntingtin von Damiano, Maria, Diguet, Elsa, Malgorn, Carole, D'Aurelio, Marilena, Galvan, Laurie, Petit, Fanny, Benhaim, Lucile, Guillermier, Martine, Houitte, Diane, Dufour, Noelle, Hantraye, Philippe, Canals, Josep M, Alberch, Jordi, Delzescaux, Thierry, Déglon, Nicole, Beal, M Flint, Brouillet, Emmanuel

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Mutated Human SOD1 Causes Dysfunction of Oxidative Phosphorylation in Mitochondria of Transgenic Mice von Mattiazzi, Marina, D'Aurelio, Marilena, Gajewski, Carl D., Martushova, Katherine, Kiaei, Mahmoud, Beal, M. Flint, Manfredi, Giovanni

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Respiratory chain supercomplexes set the threshold for respiration defects in human mtDNA mutant cybrids von D'Aurelio, Marilena, Gajewski, Carl D., Lenaz, Giorgio, Manfredi, Giovanni

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An Assembled Complex IV Maintains the Stability and Activity of Complex I in Mammalian Mitochondria von Li, Youfen, D'Aurelio, Marilena, Deng, Jian-Hong, Park, Jeong-Soon, Manfredi, Giovanni, Hu, Peiqing, Lu, Jianxin, Bai, Yidong

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Role of Mitochondria in Oxidative Stress and Aging von LENAZ, GIORGIO, BOVINA, CARLA, D'AURELIO, MARILENA, FATO, ROMANA, FORMIGGINI, GABRIELLA, GENOVA, MARIA LUISA, GIULIANO, GIOVANNI, PICH, MILENA MERLO, PAOLUCCI, UGO, CASTELLI, GIOVANNA PARENTI, VENTURA, BARBARA

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Impaired amino acid metabolism in cells affected by the T8993G (NARP) mtDNA mutation: A potential novel therapeutic target von D'Aurelio⁎, Marilena, Yang, Lichuan, Chen, Qiuying, Beal, Flint, Gross, Steven, Manfredi, Giovanni

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In Vivo Regulation of Oxidative Phosphorylation in Cells Harboring a Stop-codon Mutation in Mitochondrial DNA-encoded Cytochrome c Oxidase Subunit I von D'Aurelio, Marilena, Pallotti, Francesco, Barrientos, Antoni, Gajewski, Carl D., Kwong, Jennifer Q., Bruno, Claudio, Beal, M. Flint, Manfredi, Giovanni

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BCL-2 Improves Oxidative Phosphorylation and Modulates Adenine Nucleotide Translocation in Mitochondria of Cells Harboring Mutant mtDNA von Manfredi, Giovanni, Kwong, Jennifer Q, Oca-Cossio, José A, Woischnik, Markus, Gajewski, Carl D, Martushova, Katherine, D'Aurelio, Marilena, Friedlich, Avi L, Moraes, Carlos T

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Bioenergetic markers in skin fibroblasts of sporadic amyotrophic lateral sclerosis and progressive lateral sclerosis patients von Kirk, Kathryne, Gennings, Chris, Hupf, Jonathan C., Tadesse, Saba, D'Aurelio, Marilena, Kawamata, Hibiki, Valsecchi, Federica, Mitsumoto, Hiroshi, Manfredi, Giovanni

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Enhanced Activity of the Plasma Membrane Oxidoreductase in Circulating Lymphocytes from Insulin-Dependent Diabetes Mellitus Patients von Lenaz, Giorgio, Paolucci, Ugo, Fato, Romana, D'Aurelio, Marilena, Parenti Castelli, Giovanna, Sgarbi, Gianluca, Biagini, Graziella, Ragni, Luca, Salardi, Silvana, Cacciari, Emanuele

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Bioenergetics of mitochondrial diseases associated with mtDNA mutations von Lenaz, Giorgio, Baracca, Alessandra, Carelli, Valerio, D'Aurelio, Marilena, Sgarbi, Gianluca, Solaini, Giancarlo

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Ubiquinol and a Coenzyme Q Reducing System Protect Platelet Mitochondrial Function of Transfusional Buffy Coats from Oxidative Stress von Pich, Milena Merlo, Castagnoli, Alida, Biondi, Annalisa, Bernacchia, Andrea, Tazzari, Pier Luigi, D'Aurelio, Marilena, Castelli, Giovanna Parenti, Formiggini, Gabriella, Conte, Roberto, Bovina, Carla, Lenaz, Giorgio

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