Preventing proteostasis diseases by selective inhibition of a phosphatase regulatory subunit von Das, Indrajit, Krzyzosiak, Agnieszka, Schneider, Kim, Wrabetz, Lawrence, D'Antonio, Maurizio, Barry, Nicholas, Sigurdardottir, Anna, Bertolotti, Anne

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Sox2 expression in Schwann cells inhibits myelination in vivo and induces influx of macrophages to the nerve von Roberts, Sheridan L, Dun, Xin-Peng, Doddrell, Robin D S, Mindos, Thomas, Drake, Louisa K, Onaitis, Mark W, Florio, Francesca, Quattrini, Angelo, Lloyd, Alison C, D'Antonio, Maurizio, Parkinson, David B

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A new mouse model of Charcot-Marie-Tooth 2J neuropathy replicates human axonopathy and suggest alteration in axo-glia communication von Shackleford, Ghjuvan'Ghjacumu, Marziali, Leandro N, Sasaki, Yo, Claessens, Anke, Ferri, Cinzia, Weinstock, Nadav I, Rossor, Alexander M, Silvestri, Nicholas J, Wilson, Emma R, Hurley, Edward, Kidd, Grahame J, Manohar, Senthilvelan, Ding, Dalian, Salvi, Richard J, Feltri, M Laura, D'Antonio, Maurizio, Wrabetz, Lawrence

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Resetting translational homeostasis restores myelination in Charcot-Marie-Tooth disease type 1B mice von D'Antonio, Maurizio, Musner, Nicolò, Scapin, Cristina, Ungaro, Daniela, Del Carro, Ubaldo, Ron, David, Feltri, M Laura, Wrabetz, Lawrence

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Sustained Expression of Negative Regulators of Myelination Protects Schwann Cells from Dysmyelination in a Charcot-Marie-Tooth 1B Mouse Model von Florio, Francesca, Ferri, Cinzia, Scapin, Cristina, Feltri, M Laura, Wrabetz, Lawrence, D'Antonio, Maurizio

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Endoplasmic Reticulum Protein Quality Control Failure in Myelin Disorders von Volpi, Vera G, Touvier, Thierry, D'Antonio, Maurizio

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Electron Microscopy for the Analysis of Peripheral Nerve Myelin von Ferri, Cinzia, Quattrini, Angelo, D’Antonio, Maurizio

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Sustained OMA1-mediated integrated stress response is beneficial for spastic ataxia type 5 von Franchino, Camilla Aurora, Brughera, Martina, Baderna, Valentina, De Ritis, Daniele, Rocco, Alessandra, Seneca, Sara, Regal, Luc, Podini, Paola, D'Antonio, Maurizio, Toro, Camilo, Quattrini, Angelo, Scalais, Emmanuel, Maltecca, Francesca

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A novel mouse model of CMT1B identifies hyperglycosylation as a new pathogenetic mechanism von Veneri, Francesca A, Prada, Valeria, Mastrangelo, Rosa, Ferri, Cinzia, Nobbio, Lucilla, Passalacqua, Mario, Milanesi, Maria, Bianchi, Francesca, Del Carro, Ubaldo, Vallat, Jean-Michel, Duong, Phu, Svaren, John, Schenone, Angelo, Grandis, Marina, D'Antonio, Maurizio

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Treatment with IFB-088 Improves Neuropathy in CMT1A and CMT1B Mice von Bai, Yunhong, Treins, Caroline, Volpi, Vera G., Scapin, Cristina, Ferri, Cinzia, Mastrangelo, Rosa, Touvier, Thierry, Florio, Francesca, Bianchi, Francesca, Del Carro, Ubaldo, Baas, Frank F., Wang, David, Miniou, Pierre, Guedat, Philippe, Shy, Michael E., D’Antonio, Maurizio

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Neuregulin 1 type III improves peripheral nerve myelination in a mouse model of congenital hypomyelinating neuropathy von Belin, Sophie, Ornaghi, Francesca, Shackleford, Ghjuvan'Ghjacumu, Wang, Jie, Scapin, Cristina, Lopez-Anido, Camila, Silvestri, Nicholas, Robertson, Neil, Williamson, Courtney, Ishii, Akihiro, Taveggia, Carla, Svaren, John, Bansal, Rashmi, Schwab, Markus H, Nave, Klaus, Fratta, Pietro, D'Antonio, Maurizio, Poitelon, Yannick, Feltri, M Laura, Wrabetz, Lawrence

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Enhanced axonal neuregulin-1 type-III signaling ameliorates neurophysiology and hypomyelination in a Charcot–Marie–Tooth type 1B mouse model von Scapin, Cristina, Ferri, Cinzia, Pettinato, Emanuela, Zambroni, Desiree, Bianchi, Francesca, Del Carro, Ubaldo, Belin, Sophie, Caruso, Donatella, Mitro, Nico, Pellegatta, Marta, Taveggia, Carla, Schwab, Markus H, Nave, Klaus-Armin, Feltri, M Laura, Wrabetz, Lawrence, D’Antonio, Maurizio

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Calcineurin Activity Is Increased in Charcot-Marie-Tooth 1B Demyelinating Neuropathy von Sidoli, Mariapaola, Reed, Chelsey B., Scapin, Cristina, Paez, Pablo, Cavener, Douglas R., Kaufman, Randal J., D'Antonio, Maurizio, Feltri, M. Laura, Wrabetz, Lawrence

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Notch controls embryonic Schwann cell differentiation, postnatal myelination and adult plasticity von Parkinson, David B, Feltri, M Laura, Jessen, Kristján R, D'Antonio, Maurizio, Wilton, Daniel K, Mirsky, Rhona, Meijer, Dies, Woodhoo, Ashwin, Radtke, Freddy, Shen, Jie, Droggiti, Anna, Simons, Paul, Alonso, Maria B Duran, Guillemot, Francois, Wrabetz, Lawrence, Turmaine, Mark, Al-Shawi, Raya

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Schwann cells ER-associated degradation contributes to myelin maintenance in adult nerves and limits demyelination in CMT1B mice von Volpi, Vera G, Ferri, Cinzia, Fregno, Ilaria, Del Carro, Ubaldo, Bianchi, Francesca, Scapin, Cristina, Pettinato, Emanuela, Solda, Tatiana, Feltri, M Laura, Molinari, Maurizio, Wrabetz, Lawrence, D'Antonio, Maurizio

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Lack of Sterol Regulatory Element Binding Factor-1c Imposes Glial Fatty Acid Utilization Leading to Peripheral Neuropathy von Cermenati, Gaia, Audano, Matteo, Giatti, Silvia, Carozzi, Valentina, Porretta-Serapiglia, Carla, Pettinato, Emanuela, Ferri, Cinzia, D’Antonio, Maurizio, De Fabiani, Emma, Crestani, Maurizio, Scurati, Samuele, Saez, Enrique, Azcoitia, Iñigo, Cavaletti, Guido, Garcia-Segura, Luis-Miguel, Melcangi, Roberto C., Caruso, Donatella, Mitro, Nico

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Ablation of the UPR-Mediator CHOP Restores Motor Function and Reduces Demyelination in Charcot-Marie-Tooth 1B Mice von Pennuto, Maria, Tinelli, Elisa, Malaguti, MariaChiara, Del Carro, Ubaldo, D'Antonio, Maurizio, Ron, David, Quattrini, Angelo, Feltri, M. Laura, Wrabetz, Lawrence

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Ablation of Perk in Schwann Cells Improves Myelination in the S63del Charcot-Marie-Tooth 1B Mouse von Sidoli, Mariapaola, Musner, Nicolò, Silvestri, Nicholas, Ungaro, Daniela, D'Antonio, Maurizio, Cavener, Douglas R, Feltri, M Laura, Wrabetz, Lawrence

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HDAC1/2-Dependent P0 Expression Maintains Paranodal and Nodal Integrity Independently of Myelin Stability through Interactions with Neurofascins von Brügger, Valérie, Engler, Stefanie, Pereira, Jorge A, Ruff, Sophie, Horn, Michael, Welzl, Hans, Münger, Emmanuelle, Vaquié, Adrien, Sidiropoulos, Páris N M, Egger, Boris, Yotovski, Peter, Filgueira, Luis, Somandin, Christian, Lühmann, Tessa C, D'Antonio, Maurizio, Yamaguchi, Teppei, Matthias, Patrick, Suter, Ueli, Jacob, Claire

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Myelin under stress von D'Antonio, Maurizio, Feltri, M. Laura, Wrabetz, Lawrence

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