Hyperactive somatostatin interneurons contribute to excitotoxicity in neurodegenerative disorders von Zhang, Wen, Zhang, Lifeng, Liang, Bo, Schroeder, David, Zhang, Zhong-wei, Cox, Gregory A, Li, Yun, Lin, Da-Ting

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Convergence of mammalian RQC and C-end rule proteolytic pathways via alanine tailing von Thrun, Anna, Garzia, Aitor, Kigoshi-Tansho, Yu, Patil, Pratik R., Umbaugh, Charles S., Dallinger, Teresa, Liu, Jia, Kreger, Sylvia, Patrizi, Annarita, Cox, Gregory A., Tuschl, Thomas, Joazeiro, Claudio A.P.

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NEMF mutations that impair ribosome-associated quality control are associated with neuromuscular disease von Martin, Paige B., Kigoshi-Tansho, Yu, Sher, Roger B., Ravenscroft, Gianina, Stauffer, Jennifer E., Kumar, Rajesh, Yonashiro, Ryo, Müller, Tina, Griffith, Christopher, Allen, William, Pehlivan, Davut, Harel, Tamar, Zenker, Martin, Howting, Denise, Schanze, Denny, Faqeih, Eissa A., Almontashiri, Naif A. M., Maroofian, Reza, Houlden, Henry, Mazaheri, Neda, Galehdari, Hamid, Douglas, Ganka, Posey, Jennifer E., Ryan, Monique, Lupski, James R., Laing, Nigel G., Joazeiro, Claudio A. P., Cox, Gregory A.

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A microfluidic approach to rescue ALS motor neuron degeneration using rapamycin von Chennampally, Phaneendra, Sayed-Zahid, Ambreen, Soundararajan, Prabakaran, Sharp, Jocelyn, Cox, Gregory A., Collins, Scott D., Smith, Rosemary L.

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A Direct HDAC4-MAP Kinase Crosstalk Activates Muscle Atrophy Program von Choi, Moon-Chang, Cohen, Todd J., Barrientos, Tomasa, Wang, Bin, Li, Ming, Simmons, Bryan J., Yang, Jeong Soo, Cox, Gregory A., Zhao, Yingming, Yao, Tso-Pang

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Identification of quantitative trait loci for survival in the mutant dynactin p150Glued mouse model of motor neuron disease von Alexander, Guillermo M, Heiman-Patterson, Terry D, Bearoff, Frank, Sher, Roger B, Hennessy, Laura, Terek, Shannon, Caccavo, Nicole, Cox, Gregory A, Philip, Vivek M, Blankenhorn, Elizabeth A

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MARF1 Regulates Essential Oogenic Processes in Mice von Su, You-Qiang, Sugiura, Koji, Sun, Fengyun, Pendola, Janice K., Cox, Gregory A., Handel, Mary Ann, Schimenti, John C., Eppig, John J.

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A Congenital Muscular Dystrophy with Mitochondrial Structural Abnormalities Caused by Defective De Novo Phosphatidylcholine Biosynthesis von MITSUHASHI, Satomi, OHKUMA, Aya, GOTO, Kanako, KOKSAL, Burcu, KALE, Gulsev, IKEDA, Kazutaka, TAGUCHI, Ryo, NOGUCHI, Satoru, HAYASHI, Yukiko K, NONAKA, Ikuya, SHER, Roger B, SUGIMOTO, Hiroyuki, TALIM, Beril, NAKAGAWA, Yasuhito, COX, Gregory A, TOPALOGLU, Haluk, NISHINO, Ichizo, KARAHASHI, Minako, KOUMURA, Tomoko, AOYAMA, Chieko, KURIHARA, Mana, QUINLIVAN, Ros, SEWRY, Caroline, MITSUHASHI, Hiroaki

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An Active Dominant Mutation of Glycyl-tRNA Synthetase Causes Neuropathy in a Charcot-Marie-Tooth 2D Mouse Model von Seburn, Kevin L., Nangle, Leslie A., Cox, Gregory A., Schimmel, Paul, Burgess, Robert W.

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Author Correction: A microfluidic approach to rescue ALS motor neuron degeneration using rapamycin von Chennampally, Phaneendra, Sayed-Zahid, Ambreen, Soundararajan, Prabakaran, Sharp, Jocelyn, Cox, Gregory A., Collins, Scott D., Smith, Rosemary L.

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Unexpected similarities between C9ORF72 and sporadic forms of ALS/FTD suggest a common disease mechanism von Conlon, Erin G, Fagegaltier, Delphine, Agius, Phaedra, Davis-Porada, Julia, Gregory, James, Hubbard, Isabel, Kang, Kristy, Kim, Duyang, Phatnani, Hemali, Shneider, Neil A, Manley, James L

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The Histone Deacetylase HDAC4 Connects Neural Activity to Muscle Transcriptional Reprogramming von Cohen, Todd J., Waddell, David S., Barrientos, Tomasa, Lu, Zhonghua, Feng, Guoping, Cox, Gregory A., Bodine, Sue C., Yao, Tso-Pang

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Muscle choline kinase beta defect causes mitochondrial dysfunction and increased mitophagy von Mitsuhashi, Satomi, Hatakeyama, Hideyuki, Karahashi, Minako, Koumura, Tomoko, Nonaka, Ikuya, Hayashi, Yukiko K., Noguchi, Satoru, Sher, Roger B., Nakagawa, Yasuhito, Manfredi, Giovanni, Goto, Yu-ichi, Cox, Gregory A., Nishino, Ichizo

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Severity of Demyelinating and Axonal Neuropathy Mouse Models Is Modified by Genes Affecting Structure and Function of Peripheral Nodes von Morelli, Kathryn H., Seburn, Kevin L., Schroeder, David G., Spaulding, Emily L., Dionne, Loiuse A., Cox, Gregory A., Burgess, Robert W.

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Genetic background effects on disease onset and lifespan of the mutant dynactin p150Glued mouse model of motor neuron disease von Heiman-Patterson, Terry D, Blankenhorn, Elizabeth P, Sher, Roger B, Jiang, Juliann, Welsh, Priscilla, Dixon, Meredith C, Jeffrey, Jeremy I, Wong, Philip, Cox, Gregory A, Alexander, Guillermo M

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Author Correction: NEMF mutations that impair ribosome-associated quality control are associated with neuromuscular disease von Martin, Paige B., Kigoshi-Tansho, Yu, Sher, Roger B., Ravenscroft, Gianina, Stauffer, Jennifer E., Kumar, Rajesh, Yonashiro, Ryo, Müller, Tina, Griffith, Christopher, Allen, William, Pehlivan, Davut, Harel, Tamar, Zenker, Martin, Howting, Denise, Schanze, Denny, Faqeih, Eissa A., Almontashiri, Naif A. M., Maroofian, Reza, Houlden, Henry, Mazaheri, Neda, Galehdari, Hamid, Douglas, Ganka, Posey, Jennifer E., Ryan, Monique, Lupski, James R., Laing, Nigel G., Joazeiro, Claudio A. P., Cox, Gregory A.

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Ankyrin Repeat Domain Protein 2 and Inhibitor of DNA Binding 3 Cooperatively Inhibit Myoblast Differentiation by Physical Interaction von Mohamed, Junaith S., Lopez, Michael A., Cox, Gregory A., Boriek, Aladin M.

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Dysferlin Deficiency and the Development of Cardiomyopathy in a Mouse Model of Limb-Girdle Muscular Dystrophy 2B von Chase, Thomas H, Cox, Gregory A, Burzenski, Lisa, Foreman, Oded, Shultz, Leonard D

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Biochemical and genetic evidence for a role of IGHMBP2 in the translational machinery von de Planell-Saguer, Mariàngels, Schroeder, David G., Rodicio, Maria Celina, Cox, Gregory A., Mourelatos, Zissimos

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Alterations in Osteopontin Modify Muscle Size in Females in Both Humans and Mice von HOFFMAN, ERIC P, GORDISH-DRESSMAN, HEATHER, MCLANE, VIRGINIA D, DEVANEY, JOSEPH M, THOMPSON, PAUL D, VISICH, PAUL, GORDON, PAUL M, PESCATELLO, LINDA S, ZOELLER, ROBERT F, MOYNA, NIALL M, ANGELOPOULOS, THEODORE J, PEGORARO, ELENA, COX, GREGORY A, CLARKSON, PRISCILLA M

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